Erschienen in:
01.06.2015 | e-Herz: Case study
Cor triatriatum dexter in a patient with pectus excavatum
A rare cause of right heart failure
verfasst von:
C. Kilit, M. Oylumlu, A. Doğan, B. Amasyalı
Erschienen in:
Herz
|
Ausgabe 4/2015
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Excerpt
Cor triatriatum dexter (CTD) is an extremely rare congenital anomaly in which the right atrium is divided into two chambers by a membrane caused by persistence of the right valve of the sinus venosus [
1]. The persistence of the right leaflet of the venous sinus valve causes a wide range of defects including a prominent Eustachian valve, the Chiari network, and CTD [
2]. It has an estimated incidence of around 0.025 % of all congenital heart diseases and is frequently associated with right-sided defects caused by abnormal fetal circulation. Among these, the most frequent are stenosis or atresia of the pulmonary valve, tricuspid valve abnormalities, and atrial septal defects [
3]. A patent foramen ovale (PFO) has been shown previously in neonatal and adult patients with CTD [
4,
5]. However, CTD and PFO together in a patient with pectus excavatum (PE), which is the most common chest wall deformity affecting 1–300/1,000 individuals, has not been reported in the literature [
6]. …