The online version of this article (doi:10.1007/s12325-015-0197-1) contains supplementary material, which is available to authorized users.
The lifespan of patients with sickle-cell disease (SCD) continues to increase, and most affected individuals in high-resource countries now live into adulthood. This necessitates a successful transition from pediatric to adult health care. Care for transitioning patients with SCD often falls to primary care providers who may not be fully aware of the many challenges and issues faced by patients and the current management strategies for SCD. In this review, we aim to close the knowledge gap between primary care providers and specialists who treat transitioning patients with SCD. We describe the challenges and issues encountered by these patients, and we propose a biopsychosocial multidisciplinary approach to the management of the identified issues. Examples of this approach, such as transition-focused integrated care models and quality improvement collaboratives, with the potential to improve health outcomes in adulthood are also described.
Supplementary material 1 (PDF 191 kb)12325_2015_197_MOESM1_ESM.pdf
Vichinsky EP. Comprehensive care in sickle cell disease: its impact on morbidity and mortality. Semin Hematol. 1991;28:220–6. PubMed
Brown RT, editor. Comprehensive handbook of childhood cancer and sickle cell disease: a biopsychosocial approach. New York: Oxford University Press; 2006.
Nash KB, Telfair J. Sickle cell disease: a biopsychosocial model. In: Livingston I, editor. Handbook of Black American health: the mosaic of conditions, issues, policies, and prospects. Westport: Greenwood Press; 1994. p. 123–39.
Rogers ZR. Priapism in sickle cell disease. Hematol Oncol Clin N Am. 2005;19:917–28 (viii). CrossRef
NIH ends transcranial doppler (TCD) with transfusions changing to hydroxyurea (TWiTCH) clinical trial due to early results. National Institutes of Health website. http://www.nih.gov/news/health/nov2014/nhlbi-19.htm. Accessed Dec 2, 2014.
Howard J, Woodhead T, Musumadi L, Martell A, Inusa BP. Moving young people with sickle cell disease from paediatric to adult services. Br J Hosp Med (Lond). 2010;71:310–4. CrossRef
Ohene-Frempong K, Weiner SJ, Sleeper LA, et al. Cerebrovascular accidents in sickle cell disease: rates and risk factors. Blood. 1998;91:288–94. PubMed
Wilkie DJ, Johnson B, Mack AK, Labotka R, Molokie RE. Sickle cell disease: an opportunity for palliative care across the life span. Nurs Clin N Am. 2010;45:375–97. CrossRef
Hauser ES, Dorn L. Transitioning adolescents with sickle cell disease to adult-centered care. Pediatr Nurs. 1999;25:479–88. PubMed
Bediako SM. Predictors of employment status among African Americans with sickle cell disease. J Health Care Poor Underserved. 2010;21:1124–37. PubMed
Key features of the Affordable Care Act by year. U.S. Department of Health & Human Services Web site. http://www.hhs.gov/healthcare/facts/timeline/timeline-text.html. Accessed Sept 18, 2014.
American Academy of Pediatrics. Health supervision for children with sickle cell disease. Pediatrics. 2002;109:526–35. CrossRef
Registry and surveillance system for hemoglobinopathies (RuSH). Centers for Disease Control and Prevention Web site. http://www.cdc.gov/ncbddd/hemoglobinopathies/documents/rushfactsheet2010.pdf. Accessed Oct 30, 2014.
National Institutes of Health, National Heart, Lung, and Blood Institute. The management of sickle cell disease. NIH Publication No. 02-2117; 2002.
Jordan L. Day hospital reduces inpatient length of stay and emergency department visits for patients with sickle cell anemia. https://innovations.ahrq.gov/profiles/day-hospital-reduces-inpatient-length-stay-and-emergency-department-visits-patients-sickle.
American Academy of Pediatrics, American Academy of Family Physicians, and American College of Physicians, Transitions Clinical Report Authoring Group. Supporting the health care transition from adolescence to adulthood in the medical home. Pediatrics. 2011;128:182–200. CrossRef
Topic: sickle cell disease. National Institute for Children’s Health Quality Web site. http://www.nichq.org/sitecore/content/sickle-cell-disease/sickle-cell-disease. Accessed 24 Mar 2015.
- A Biopsychosocial Model for the Management of Patients With Sickle-Cell Disease Transitioning to Adult Medical Care
Lori E. Crosby
Charles T. Quinn
Karen A. Kalinyak
- Springer Healthcare
Neu im Fachgebiet Innere Medizin
Meistgelesene Bücher aus der Inneren Medizin
e.Med Kampagnen-Visual, Mail Icon II