Hypertrophic olivary degeneration (HOD) is a rare neurological condition, which is defined as a secondary degenerative process associated with focal lesions to the Guillain–Mollaret triangle of the dentato-rubro-olivary pathway. The etiologies of HOD include hemorrhage, ischemia, tumors, and demyelination [
1,
2]. Classically, patients with HOD show characteristic palatal tremors combined with a variable degree of other neurological signs. Herein, we describe a middle-aged man with HOD that developed 6 months after dorsal pontine hemorrhage, who presented with cerebellar ataxia and pendular nystagmus but not palatal tremor. …