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Acta Neuropathologica

Ausgabe 2/2018

Inhalt (10 Artikel)

Review

The function of the cellular prion protein in health and disease

Joel C. Watts, Matthew E. C. Bourkas, Hamza Arshad

Original Paper

Cofactors influence the biological properties of infectious recombinant prions

Natalia Fernández-Borges, Michele A. Di Bari, Hasier Eraña, Manuel Sánchez-Martín, Laura Pirisinu, Beatriz Parra, Saioa R. Elezgarai, Ilaria Vanni, Rafael López-Moreno, Gabriele Vaccari, Vanessa Venegas, Jorge M. Charco, David Gil, Chafik Harrathi, Claudia D’Agostino, Umberto Agrimi, Tomás Mayoral, Jesús R. Requena, Romolo Nonno, Joaquín Castilla

Original Paper

Neuropathology of iatrogenic Creutzfeldt–Jakob disease and immunoassay of French cadaver-sourced growth hormone batches suggest possible transmission of tauopathy and long incubation periods for the transmission of Abeta pathology

Charles Duyckaerts, Véronique Sazdovitch, Kunie Ando, Danielle Seilhean, Nicolas Privat, Zehra Yilmaz, Laurène Peckeu, Elodie Amar, Emmanuel Comoy, Aleksandra Maceski, Sylvain Lehmann, Jean-Pierre Brion, Jean-Philippe Brandel, Stéphane Haïk

Open Access Original Paper

Synapse loss in the prefrontal cortex is associated with cognitive decline in amyotrophic lateral sclerosis

Christopher M. Henstridge, Dimitrios I. Sideris, Emily Carroll, Sanziana Rotariu, Sally Salomonsson, Makis Tzioras, Chris-Anne McKenzie, Colin Smith, Christine A. F. von Arnim, Albert C. Ludolph, Dorothée Lulé, Danielle Leighton, Jon Warner, Elaine Cleary, Judith Newton, Robert Swingler, Siddharthan Chandran, Thomas H. Gillingwater, Sharon Abrahams, Tara L. Spires-Jones

Open Access Original Paper

Artificial intelligence in neurodegenerative disease research: use of IBM Watson to identify additional RNA-binding proteins altered in amyotrophic lateral sclerosis

Nadine Bakkar, Tina Kovalik, Ileana Lorenzini, Scott Spangler, Alix Lacoste, Kyle Sponaugle, Philip Ferrante, Elenee Argentinis, Rita Sattler, Robert Bowser

Original Paper

Co-occurrence of mixed proteinopathies in late-stage Huntington’s disease

Isabelle St-Amour, Andréanne Turgeon, Claudia Goupil, Emmanuel Planel, Sébastien S. Hébert

Open Access Original Paper

Changes in chromatin state reveal ARNT2 at a node of a tumorigenic transcription factor signature driving glioblastoma cell aggressiveness

Alexandra Bogeas, Ghislaine Morvan-Dubois, Elias A. El-Habr, François-Xavier Lejeune, Matthieu Defrance, Ashwin Narayanan, Klaudia Kuranda, Fanny Burel-Vandenbos, Salwa Sayd, Virgile Delaunay, Luiz G. Dubois, Hugues Parrinello, Stéphanie Rialle, Sylvie Fabrega, Ahmed Idbaih, Jacques Haiech, Ivan Bièche, Thierry Virolle, Michele Goodhardt, Hervé Chneiweiss, Marie-Pierre Junier

Original Paper

Functional requirement of a wild-type allele for mutant IDH1 to suppress anchorage-independent growth through redox homeostasis

Patricia D. B. Tiburcio, Bing Xiao, Shauna Berg, Sydney Asper, Sean Lyne, Yan Zhang, Xingen Zhu, Hai Yan, L. Eric Huang

Correspondence

Circumscribed/non-diffuse histology confers a better prognosis in H3K27M-mutant gliomas

Drew Pratt, Siva Kumar Natarajan, Adam Banda, Caterina Giannini, Pankaj Vats, Carl Koschmann, Rajen Mody, Arul Chinnaiyan, Sriram Venneti

Open Access Correspondence

First confirmed case of chronic traumatic encephalopathy in a professional bull rider

C. Dirk Keene, Caitlin S. Latimer, Lisa M. Steele, Christine L. Mac Donald

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