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Erschienen in: Rheumatology International 12/2010

01.11.2010 | Case Report

Acute adrenal crisis mimicking familial Mediterranean fever attack in a renal transplant FMF patient with amyloid goiter

verfasst von: Hamdi Emeksiz, Sevcan Bakkaloglu, Orhun Camurdan, Mehmet Boyraz, Oguz Soylemezoglu, Enver Hasanoglu, Necla Buyan

Erschienen in: Rheumatology International | Ausgabe 12/2010

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Abstract

The most devastating complication of familial Mediterranean fever (FMF) is amyloidosis which is capable of resulting in chronic renal failure. Although amyloid deposits are frequent in adrenal glands based on the autopsies of FMF patients however; to our knowledge, symptomatic adrenal insufficiency has not been reported yet. We describe a 21-year-old-FMF amyloidosis case with a well-functioning allograft who presented to the emergency clinic with the complaints of abdominal pain, vomiting and diarrhea mimicking FMF attack. adrenocorticotrophic hormone stimulation test was performed due to resistant hyponatremia and disclosed Addison disease. In countries with a high prevalence of FMF, adrenal crisis should be borne in mind in long standing FMF patients.
Literatur
1.
Zurück zum Zitat Danovitch GM, Le Roith D, Sikuler SE, Straus R (1979) Amyloid goitre in familial Mediterranean fever. Clin Endocrinol (Oxf) 11:595–601CrossRef Danovitch GM, Le Roith D, Sikuler SE, Straus R (1979) Amyloid goitre in familial Mediterranean fever. Clin Endocrinol (Oxf) 11:595–601CrossRef
2.
Zurück zum Zitat Levy M, Yaffe C (1978) Testicular function in patients with familial Mediterranean fever on long-term colchicine treatment. Fertil Steril 29:667–668PubMed Levy M, Yaffe C (1978) Testicular function in patients with familial Mediterranean fever on long-term colchicine treatment. Fertil Steril 29:667–668PubMed
3.
Zurück zum Zitat Kadayifci A, Uygun A, Dagalp K, Kepekci Y (2000) The coexistence of familial Mediterranean fever and Addison disease. J Clin Gastroenterol 30:98–99CrossRefPubMed Kadayifci A, Uygun A, Dagalp K, Kepekci Y (2000) The coexistence of familial Mediterranean fever and Addison disease. J Clin Gastroenterol 30:98–99CrossRefPubMed
5.
Zurück zum Zitat Arean VM, Klein RE (1961) Amyloid goitre: review of the literature and report of a case. Am J Clin Pathol 36:341–355PubMed Arean VM, Klein RE (1961) Amyloid goitre: review of the literature and report of a case. Am J Clin Pathol 36:341–355PubMed
6.
Zurück zum Zitat Ozdemir BH, Akman B, Ozdemir FN (2001) Amyloid goiter in Familial Mediterranean fever (FMF): a clinicopathologic study of 10 cases. Ren Fail 23:659–667CrossRefPubMed Ozdemir BH, Akman B, Ozdemir FN (2001) Amyloid goiter in Familial Mediterranean fever (FMF): a clinicopathologic study of 10 cases. Ren Fail 23:659–667CrossRefPubMed
7.
Zurück zum Zitat Grateau G (2000) The relationship between familial Mediterranean fever and amyloidosis. Curr Opin Rheumatol 12:61–64CrossRefPubMed Grateau G (2000) The relationship between familial Mediterranean fever and amyloidosis. Curr Opin Rheumatol 12:61–64CrossRefPubMed
9.
Zurück zum Zitat Nomura K, Demura H, Saruta T (1994) Addison’s disease in Japan: characteristics and changes revealed in a nationwide survey. Intern Med 33:602–606CrossRefPubMed Nomura K, Demura H, Saruta T (1994) Addison’s disease in Japan: characteristics and changes revealed in a nationwide survey. Intern Med 33:602–606CrossRefPubMed
10.
Zurück zum Zitat Sav T, Ozbakir O, Kelestimur F, Gursoy S, Baskol M, Kula M, Dundar M (2006) Adrenal axis functions in patients with familial Mediterranean fever. Clin Rheumatol 25:458–461CrossRefPubMed Sav T, Ozbakir O, Kelestimur F, Gursoy S, Baskol M, Kula M, Dundar M (2006) Adrenal axis functions in patients with familial Mediterranean fever. Clin Rheumatol 25:458–461CrossRefPubMed
Metadaten
Titel
Acute adrenal crisis mimicking familial Mediterranean fever attack in a renal transplant FMF patient with amyloid goiter
verfasst von
Hamdi Emeksiz
Sevcan Bakkaloglu
Orhun Camurdan
Mehmet Boyraz
Oguz Soylemezoglu
Enver Hasanoglu
Necla Buyan
Publikationsdatum
01.11.2010
Verlag
Springer-Verlag
Erschienen in
Rheumatology International / Ausgabe 12/2010
Print ISSN: 0172-8172
Elektronische ISSN: 1437-160X
DOI
https://doi.org/10.1007/s00296-009-1115-0

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