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Erschienen in: Journal of Anesthesia 3/2015

01.06.2015 | Clinical Report

Anesthetic management of pediatric patients with Emanuel syndrome

verfasst von: Reiko Nishinarita, Takahiro Mihara, Nobuhito Nakamura, Yoshihisa Miyamoto, Koui Ka

Erschienen in: Journal of Anesthesia | Ausgabe 3/2015

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Abstract

Emanuel syndrome is a rare anomaly associated with multiple systemic malformations. We present two cases involving pediatric patients with Emanuel syndrome. The first patient presented with micrognathia and had patent ductus arteriosus and a single kidney. The patient was difficult to intubate with McGRATH® but was successfully intubated with an Airtraq® device. The second patient did not present with micrognathia and was not difficult to intubate. A thorough examination of the heart, kidney, and spinal cord is important when planning the anesthetic management of patients with Emanuel syndrome. Moreover, adequate preparation for a difficult airway is essential, and the Airtraq® device may be useful for intubating patients with Emanuel syndrome with micrognathia.
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Metadaten
Titel
Anesthetic management of pediatric patients with Emanuel syndrome
verfasst von
Reiko Nishinarita
Takahiro Mihara
Nobuhito Nakamura
Yoshihisa Miyamoto
Koui Ka
Publikationsdatum
01.06.2015
Verlag
Springer Japan
Erschienen in
Journal of Anesthesia / Ausgabe 3/2015
Print ISSN: 0913-8668
Elektronische ISSN: 1438-8359
DOI
https://doi.org/10.1007/s00540-014-1955-y

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