We describe the first angiographic demonstration of spontaneous occlusion of the arterial supply of a right lower lobe pulmonary sequestration. Intralobar pulmonary sequestration was first diagnosed by cardiac catheterization and aortography in a 1-year-old female. Systemic arterial supply was from a branch of the infra-diaphragmatic aorta and venous drainage was to the left atrium. Conservative management was elected, and the patient was followed up with annual exams. Repeat catheterization and aortography, performed to evaluate complaints of chest pain at age 13 years, showed no flow through the previously demonstrated systemic arterial supply from the aorta.