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Annals of Hematology

Ausgabe 10/2025

Inhalt (68 Artikel)

Diffuse large B-cell lymphoma in the new era: prognostic tools for mapping risk

  • Open Access
  • Review

Andrea Duminuco, Salvatore Scarso, Vittorio Del Fabro, Laura Anastasia Caruso, Gaia Stanzione, Francesco Di Raimondo, Giuseppe Alberto Palumbo, Calogero Vetro

Early-life clinical and hematological profiles: a comparative study of children with and without sickle cell disease in the first three years of life

  • Open Access
  • Research

Siana Nkya, Isihaka Mahawi, Rehema Shungu, Collin Nzunda, Frida Kaywanga, David Solomon, Theogloria Kerrety, Emmanuel Josephat, Heavenlight Christopher, Doreen Ngowi, Julieth Johansen, Florence Urio, Josephine Mgaya, Upendo Masamu, Clara Chamba, Raphael Sangeda, Fadya Hashim, Emmanuela Ambroise, Lulu Chirande, Agnes Jonathan, Emmanuel Balandya, Solomon Ofori Acquah, Julie Makani

Establishment of reference interval (RI) for G6PD/6PGD ratio in adults from Yangjiang, China

  • Open Access
  • Research

Zhen Wang, Xiao-Hua Yu, Jian-Lian Liang, Bai-Ru Lai, Yan-Bin Cao, Yu-Chan Huang, Jin-Ling Chen, Jin-Xiu Yao, Li-Ye Yang

Prognostic scoring model incorporating clinical characteristics for pediatric hemophagocytic lymphohistiocytosis: a multicenter retrospective study

  • Open Access
  • Research

Shu-yi Guo, Ru Tang, Shi-lin Liu, Li-hua Yang, Yun-yan He, Liu-hua Liao, Hong Wen, Sen-lin Luo, Xiang Lan, Ya-wei Zou, Hui-qin Chen, Xing-jiang Long, Qi-wen Chen, Hai-xia Guo, Cong Liang, Hao-yan Ren, Si-xi Liu, Dun-hua Zhou

Management and outcomes of refractory immune thrombocytopenia in pediatric patients: A retrospective analysis from Ospedale Pediatrico Bambino Gesù

  • Open Access
  • Research

Gabriele Canciani, Anna Cascone, Antonio Musolino, Antonio Torelli, Emanuela Monteferrario, Giuseppe Palumbo, Giulia Ceglie

Codanin-1, defective in congenital dyserythropoietic anemia I (CDA-I), regulates erythroid differentiation

  • Open Access
  • Research

Linette Bosques, Susree Modepalli, Arvindhan Nagarajan, Caroline Tang, Sandra Martínez-Morilla, Nur-Taz Rahman, Sameet S. Mehta, Diane S. Krause, Hannah Tamary, Patrick G. Gallagher, Shilpa M. Hattangadi, Gary M. Kupfer

Outcome and response to different management regimens in pediatric patients with immune thrombocytopenia (ITP)

  • Open Access
  • Research

Rasha AbdelRaouf AbdelAziz, Dalia El-Sayed, Fatma El Zahraa Ahmed, Mohammed Al Komy

Revisiting hepatitis B vaccination in children with transfusion-dependent thalassemia

  • Open Access
  • Research

Angga Wirahmadi, Ludi Dhyani Rahmartani, Pustika Amalia Wahidiyat

Morbidity and mortality of sickle cell disease in Côte d’Ivoire

  • Open Access
  • Research

Jacques Fabrice Konan Koffi, Renée-Paule Botti, Roméo Ayemou, Aya Annick Charlene N’dri, Awa Ouattara, Eudoxie-Emmanuelle Gneblo, Kouassi Gustave Koffi

Multicenter, real-world observational study of AVA therapy following ELT/HET switching in Chinese children with persistent/chronic primary ITP

  • Open Access
  • Research

Jingjing Liu, Zhifa Wang, Nan Wang, Jingyao Ma, Lijuan Wang, Yan Liu, Jinxi Meng, Shuyue Dong, Yu Hu, Juntao Ouyang, Zhenping Chen, Xiaoling Cheng, Runhui Wu

Epidemiological study of thalassemia in the Buyi population of Qiannan Prefecture, Guizhou Province, China based on third-generation sequencing

  • Open Access
  • Research

Jiangfen Wu, Lei Wang, Zhenju Jin, Lingyan Ren, Yinghong Shi, Ying Zhou, Guohui Meng, Aiping Mao, Di cui, Bangquan An, Shengwen Huang

EC2-mutant Mycoplasma pneumoniae in pediatric ITP: severe hemorrhage with accelerated platelet recovery

  • Open Access
  • Research

Jiaqian Wan, Xi Lin, Jingyao Ma, Yu Hu, Yaguang Peng, Runhui Wu

Haemoglobin variants in nigeria: real-world data from a point-of-care device

  • Open Access
  • Research

Taiwo Kotila, Oladapo Aworanti, Chima Akunwata, Peter Ogundeji, Samuel Oresanya, Adetunji Adewale, Raphael Alabi, Foluke Fasola, John Olaniyi

Results from a US modified Delphi consensus to define disease progression and disease modification in polycythemia Vera

  • Open Access
  • Research

Prithviraj Bose, Emily Nagler, Muhammad Sarfraz Nawaz, Raajit K. Rampal, Tsewang Tashi, Swapna Thota, John O. Mascarenhas

Identification of a novel PML exon 6 splice variant in atypical PML::RARα transcripts in acute promyelocytic leukemia

  • Open Access
  • Research

Haimin Chen, Meihong Chen, Zhongjie Yang, Shuzhen Liao, Yun Lin, Linlin Yan

Von Willebrand factor and JAK2V617F variant allele frequency predict thrombosis and bleeding in patients with myeloproliferative neoplasms

  • Open Access
  • Research

Ayala Gat, Romi Kazoom, Inbal Shapira, Ela Shai, Batia Roth Jelinek, Noa Buchman, Yosef Kalish, Ariela Arad, Eran Zimran

Post-cytotoxic myeloid neoplasms: a comprehensive analysis of clinicopathologic, genetic profile, latency determinants, and potential prognostic predictors- a single centre study

  • Open Access
  • Research

Dina Sameh Soliman, Shehab Fareed, Prem Chandra, Susanna Akiki, Halima El-Omri, Feryal Ibrahim, Mohamed Yassin, Sarah A. El Kourashy, Ahmad Al-Sabbagh, Einas Al-Kuwari

Impact of inflammatory cytokine polymorphisms on the progression of myelodysplastic syndromes

  • Open Access
  • Research

Nanami Gotoh, Tsatsralgerel Munkh-Erdene, Ai Hayashi, Tetsuhiro Kasamatsu, Miri Kitamura, Asumi Kojima, Takafumi Okawa, Tsukasa Oda, Eiji Miyauchi, Nobuo Sasaki, Ikuko Matsumura, Akira Matsumoto, Hisashi Takei, Nobuhiko Kobayashi, Yuri Miyazawa, Yoshiyuki Ogawa, Hiroshi Handa, Takayuki Saitoh

NIPA1 depletion in tumor-associated macrophages via IGFBP2/EGFR attenuates acute myeloid leukemia progression and chemoresistance

  • Open Access
  • Research

Shanhao Tang, Lixia Sheng, Qitian Mu, Yi Wang, Lieguang Chen, Kaihong Xu, Miao Zhou, Zhijuan Xu, An Wu, Guifang Ouyang

DGKα inhibition enhances the antitumor effect of chiauranib on transformed follicular lymphoma

  • Open Access
  • Research

Jiewen Huang, Mengya Zhong, Jingwei Yao, Guangchao Pan, Qinwei Chen, Yating Liu, Yuelong Jiang, Yiming Luo, Jie Zha, Bing Xu

Polatuzumab vedotin, rituximab, cyclophosphamide, doxorubicin, and prednisone (Pola-R-CHP) therapy in diffuse large B-cell lymphoma in patients aged 80 years or older: a real-world study

  • Open Access
  • Research

Toshiki Yamada, Nobuhiko Nakamura, Hideko Goto, Takeshi Hara, Senji Kasahara, Kenji Fukuno, Michio Sawada, Hiroshi Nakamura, Naoki Hayase, Takayuki Goto, Tomomi Suzaki, Kei Fujita, Shin Lee, Nobuhiro Kanemura, Masahito Shimizu, Hisashi Tsurumi

Continous or fixedcarfilzomib, lenalidomide and dexamethasone (krd) for relapsed-refractory multiple myeloma: long-term follow-up from a multicenter, retrospective real-life surveyfrom European myeloma network (emn) Italy

  • Open Access
  • Research

Concetta Conticello, Vittorio Del Fabro, Alessandra Romano, Anna Mele, Roberto Mina, Sara Bringhen, Alessandra Orofino, Elisabetta Antonioli, Stefano Pulini, Lorenzo De Paoli, Tommaso Za, Emilia Cotzia, Federica Elia, Andrea Casson, Eleonora Prete, Stefania Citiso, Carmine Liberatore, Gloria Margiotta-Casaluci, Francesca Fazio, Sonia Morè, Irene Attucci, Fabrizio Accardi, Velia Bongarzoni, Silvia Mangiacavalli, Elena Rossi, Donato Mannina, Bruno Garibaldi, Rita Rizzi, Monica Di Cecca, Bernardino Rossini, Giuseppina Uccello, Cirino Botta, Dario Leotta, Donatella Vincelli, Massimo Gentile, Alfonso Piciocchi, Giovanni Marsili, Francesca Patriarca, Renato Zambello, Pellegrino Musto, Mario Boccadoro, Massimo Offidani, Maria Teresa Petrucci, Francesco Di Raimondo

Epidemiology of chronic lymphocytic leukaemia in Germany: A retrospective analysis of administrative claims data

  • Open Access
  • Research

Phillen Nozibuyiso Maqhuzu, Derya Bocuk, Sebastian Boelz, Sabrina Khageh Hosseini, Christian Leeb, Francois Renevey, Antje Mevius, Katja Greth, Konstantinos Christofyllakis

Clinical features and prognosis analysis of patients with follicular lymphoma: a real-world study in China

  • Open Access
  • Research

Yang Su, Qi Hu, Weili Zhao, Chi Liu, Li Wang, Shu Cheng, Pengpeng Xu, Linlin Liu, Wenzhong Yang

USP7 mutations are associated with adverse outcomes in pediatric T cell acute lymphoblastic leukemia and lymphoma

  • Open Access
  • Research

Jun Li, Yuan Yuan, Feng-Feng Niu, Ying Wang, Wei Lin, Rui-Dong Zhang, Ling Jin, Yan-Long Duan, Chao Gao

Frequent TCR rearrangements in pediatric B-cell lymphoblastic acute leukemia: genomic and phenotypic features

  • Open Access
  • Research

Jiajia Zheng, Yiting Wang, Zhiheng Li, Peifang Xiao, Jun Lu, Hu Liu, Yixin Hu, Shuiyan Wu, Bohan Li, Li Gao, Qi Ji, Hailong He, Yi Wang, Jie Li, Nan Chen, Lijun Meng, Yuanyuan Tian, Yizhen Li, Sheng Xiao, Shaoyan Hu

Patients with follicular lymphoma should be treated according to baseline PET-CT findings with targeted re-biopsy

  • Open Access
  • Research

Anni Nyyssönen, Outi Kuittinen, Tero Vuolio, Elias Vaattovaara, Aino Rajamäki, Taina Turpeenniemi-Hujanen, Marc Sorigue, Hanne Kuitunen, Milla E.L. Kuusisto

Infection events in patients with newly diagnosed multiple myeloma with anti-CD38 monoclonal antibody-based first line regimens: A multicentric Italian experience

  • Open Access
  • Research

Angela Rago, Francesca Fioritoni, Carmine Liberatore, Stefano Pulini, Francesca Fazio, Maria Teresa Petrucci, Valerio De Stefano, Elena Rossi, Tommaso Za, Francesca Di Landro, Laura De Padua, Masssimo Offidani, Sonia More, Annibali Ombretta, Valeria Tomarchio, Maria Antonietta Tafuri, Alfonso Piciocchi, Luca Franceschini, Alessia Fiorini, Tommaso Caravita di Toritto

Pediatric bone marrow microenvironment before and after allogeneic hematopoietic stem cell transplantation: a multicenter retrospective study comparing donors and recipients

  • Open Access
  • Research

Pan Zhang, Ang Wei, Guanghua Zhu, Bin Wang, Chenguang Jia, Yanhui Luo, Yuanfang Jing, Wei Yang, Kaige Zhang, Wei Chen, Maoquan Qin, Jun Yang

Expansion of peripheral helper T cells in the peripheral blood of patients with chronic graft-versus-host disease

  • Open Access
  • Research

Yuanyuan Du, Xuefeng He, Kangkang Lv, Youzhen Ge, Mimi Xu, Li Wan, Meng Zhou, Huizhu Kang, Chengyuan Gu, Ruju Wang, Yue Han, Yongxia Wu, Depei Wu, Yuejun Liu

Developmental stage modulates the prognostic impact of RAS pathway mutations in AML patients undergoing Allo-HSCT

  • Open Access
  • Research

Xiaolin Yuan, Yibo Wu, Yanan Wang, Junqing Wu, Panpan Zhu, Luxin Yang, Xiaoyu Lai, Lizhen Liu, Jimin Shi, Jian Yu, Yanmin Zhao, Weiyan Zheng, Jingsong He, Jie Sun, Wenjun Wu, Yi Zhao, Zhen Cai, He Huang, Shanshan Pei, Yi Luo

Impact of Dara-VTD induction therapy on stem cell mobilization outcomes in newly diagnosed multiple myeloma patients undergoing autologous stem cell transplantation: a multicenter study

  • Open Access
  • Research

Roberta Della Pepa, Salvatore Palmieri, Stefano Rocco, Novella Pugliese, Aldo Leone, Simona Avilia, Marialucia Barone, Rosa Rosamilio, Fabio Trastulli, Danilo De Novellis, Raffaele Fontana, Bianca Serio, Denise Morini, Lorenzo Esposito, Laura De Fazio, Roberta Spisso, Carmine Selleri, Catello Califano, Alessandra Picardi, Mario Annunziata, Fabrizio Pane

Transplantation strategy affects the risk of GvHD after prophylactic and preemptive donor lymphocyte infusion

  • Open Access
  • Research

Eva A.S. Koster, Peter A. von dem Borne, Joost G.K. van der Hem, Peter van Balen, Erik W.A. Marijt, Jennifer M.L. Tjon, Tjeerd J.F. Snijders, Daniëlle van Lammeren, Hendrik Veelken, J.H. Frederik Falkenburg, Liesbeth C. de Wreede, Constantijn J.M. Halkes

Real-world Canadian data on belumosudil therapy in heavily pretreated patients with steroid-refractory chronic graft-versus-host disease: treatment outcomes and risk factor analysis for failure-free survival

  • Open Access
  • Research

Sergio Rodriguez-Rodriguez, Nihar Desai, Christopher Lemieux, Keven Vachon, Kareem Jamani, Mohamed Elemary, Tommy Alfaro-Moya, Eshrak Al-Shaibani, Ivan Pasic, Igor Novitzky-Basso, Fotios Michelis, Auro Viswabandya, Rajat Kumar, Jonas Mattsson, Arjun Law, Sylvie Lachance, Dennis Dong Hwan Kim

Advantages of AI-based whole blood film scanning for blast detection in markedly leucopenic blood films

  • Open Access
  • Research

Geng Wang, Lin Zheng, Zhejun Fang, Guoju Luo, Qian Chen, Qi Qi Zhang, Bo Shen Wu, Xin Wang, Rongrong Cheng, Ping Deng, Binyao Zhang, Jing Jin, Wei Wu

Understanding challenges and barriers to quality end-of-life care for patients with hematologic malignancies: a GIMEMA survey

  • Open Access
  • Research

Leonardo Potenza, Fabio Efficace, Eleonora Borelli, Paola Fazi, Thomas Baldi, Francesca Tartaglia, Francesco Sparano, Claudio Cartoni, Pasquale Niscola, Claudia Mucciarini, Oreofe Odejide, Eduardo Bruera, Camilla Zimmermann, Marco Vignetti, Mario Luppi, Elena Bandieri

Establishing prognostic markers associated with neutrophil extracellular traps and the activated contact system in thrombotic microangiopathy

  • Open Access
  • Research

Su Sung Kim, Ja Yoon Gu, Sung Yoon Choi, Yujin Jung, Yoon Hwan Chang, Seon Young Kim, Hyun Kyung Kim

Development and validation of deep vein thrombosis diagnostic model based on machine learning methods

  • Open Access
  • Research

Bin Yan, Haijun Guo, Tianxi Hu, Yu Zhang, Zhixin Zheng, Weipeng Du, Yuhan Gu

Total thrombus formation analysis in patients with myeloid neoplasia and thrombocytopenia

  • Open Access
  • Research

Katharina Freitag, Georg-Nikolaus Franke, Maria Weise, Carmen Herling, Tristan Klöter, Marco Herling, Annelie Siegemund, Madlen Jentzsch, Sirak Petros, Reinhard Henschler, Klaus H. Metzeler, Christian Pfrepper

Updated Egyptian national guidelines for management of hemophilia A in children & adolescents

  • Open Access
  • Research

Galila Mokhtar, Amal El-Beshlawy, Mohsen El Alfy, Magdy El Ekiaby, Magda Rakha, Ahmed Mansour, Azza A.G. Tantawy, Hoda Hassab, Usama El Safy, Khaled A. Eid, Naglaa Shaheen, Naglaa Omar, Sonia Adolf, Seham Ragab, Mohamed ElKholy, Nayera H.K. Elsherif

Combined heterozygosity for the highly unstable variant hemoglobin Taybe, and α-thalassemia as a rare cause of hemolytic anemia

  • Open Access
  • Case Report

Saskia N. Nagel, Joaquin Brintrup, Yazan Ghannam, Andreas Stallmach, Andreas Hochhaus, Cristina Ripoll, Holger Cario, Karin G. Schrenk

Haploidentical hematopoietic stem cell transplantation for the treatment of congenital dyserythropoietic anemia combined with thalassemia: a report of two cases

  • Open Access
  • Case Report

Changyu Yang, Jian Huang, Kun Yang, Changqing Wei, Lina Lu, Dongmei Liu, Beibei Yang, Guiping Liao, Xiaolin Yin, Yali Zhou

Allogeneic stem cell transplantation with prior pembrolizumab and bendamustine therapy induce complete metabolic response in relapsed/refractory classical hodgkin lymphoma with relapse after nivolumab

  • Open Access
  • Case Report

Ugo Giordano, Agnieszka Kuś, Karolina Kędziora, Mateusz Sawicki, Zbigniew Podgajny, Monika Mordak-Domagała, Zuzanna Dybko, Jarosław Dybko

Clinical and molecular features of primary spinal epidural lymphomas

  • Open Access
  • Case Report

Louisa Adolph, Veit M. Stoecklein, Verena Passerini, Michael Heide, Philipp Karschnia, Stefan Zausinger, Louisa von Baumgarten, Michael von Bergwelt-Baildon, Jörg Christian Tonn, Sophia Stoecklein, Niklas Thon, Christian Schichor, Martina Rudelius, Oliver Weigert

The diagnosis and clinical characterization of -α3.7/--SEA thalassemia patients: two cases report

  • Open Access
  • Case Report

Xiuling Wang, Yu Ding, Zhiyong Huang, Jin Huang

Imatinib and blinatumomab successfully rescued a pediatric B-ALL patient with TERF2::PDGFRB fusion resistant to dasatinib and chemotherapy

  • Open Access
  • Case Report

Fanghua Ye, Leyuan Wang, Yujie Qian, Wenjun Deng, Yan Yu, Liangchun Yang

Primary effusion lymphoma with biphenotypic and bigenotypic features of T-cell receptor and IGH genes in an HIV-negative patient with kidney transplant

  • Open Access
  • Case Report

Taesung Jeon, Young-Hyeh Ko, You-Na Sung, Hyunsung Kim, Ka-Won Kang, Jong-Min Sim, Yeseul Kim

Treatment of EPOR-rearranged acute lymphoblastic leukemia with ruxolitinib: case reports and review of the literature

  • Open Access
  • Case Report

Yiling Dai, Yuan Ai, Shuwen Sun, Maoting Tang, Jinrong Li, Ju Gao, Mingyan Jiang

Unicentric Castleman disease treated with rituximab before surgery: clinicopathologic findings

  • Open Access
  • Case Report

Marco Paulli, Giuseppe Neri, Francesca Antoci, Edoardo D’Este, Marco Minetto, Federico Carpi, Martina La Fauci, Marcello Gambacorta, Marco Lucioni, Luca Arcaini

Treatment of transplantation-associated thrombotic microangiopathy with iptacopan: two cases report

  • Open Access
  • Case Report

Jun Kong, Ze Tian, Dao-Xing Deng, Xiao-Dong Mo

Bone marrow mastocytosis associated with primary cutaneous follicle center lymphoma: an unusual case report

  • Open Access
  • Case Report

Max Vincent John, Ingrid Simonitsch-Klupp, Johannes Griss, Cora Waldstein, Harald Herrmann, Alexander Gaiger, Karoline V. Gleixner, Wolfgang R. Sperr, Peter Valent

Late-onset hemophagocytic lymphohistiocytosis associated with monoallelic STX11 mutation in an adult: a case report and rationale for early allogeneic hematopoietic cell transplantation

  • Open Access
  • Case Report

Jan Mateusz Zaucha, Andrzej Mital, Michał Taszner, Agata Ogłoza, Jan Maciej Zaucha, Rafał Machowicz

Rapidly progressing after umbilical cord blood transplantation in a boy with acute myeloid leukemia with KAT6A::EP300 fusion transcript

  • Open Access
  • Correspondence

Yongren Wang, Wei Zong, Jingjing Fan, LiuCheng Rong, Yongjun Fang

Correction to: Validation of the Spanish version of the EORTC QLQ-CML24 questionnaire for assessment of health-related quality of life in patients with chronic myeloid leukemia

  • Open Access
  • Correction

Elisa Lopez-Fernández, Soledad de Linares-Fernández, Maria Nieves Perez-Marfil, Juan Antonio Vera-Goñi, Magdalena Anguita-Arance, Maria del Carmen Fernández-Valle, Maria Jose Ramírez-Sánchez, Maria Concepción Ruiz-Nuño, Werner González-Molina, Carmen Ferrer-Chaves, Carmen Avellaneda-Molina, Jose Manuel Puerta-Puerta

Correction to: Real-world efficacy and safety outcomes of acalabrutinib in chronic lymphocytic leukemia: primary results of a French multicentre observational study (NAOS)

  • Open Access
  • Correction

Anne Quinquenel, Stéphane Leprêtre, Marie Sarah Dilhuydy, Lucile Bussot, Zora Marjanovic, Omar Benbrahim, Romain Guièze, Alberto Santagostino, Caroline Dartigeas, Pierre Feugier, Damien Roos-Weil, Ghandi Damaj, Kamel Laribi, Loic Ysebaert, Vincent Levy

Correction to: Prognostic value of dynamic minimal residual disease monitoring for adolescent and adult T-lymphoblastic leukemia/lymphoma

  • Open Access
  • Correction

Ying Yang, Xin Zhang, Nenggang Jiang, Yongmei Jin, Yu Liu, Hongyan Liao

Correction to: Evaluated NSUN3 in reticulocytes from HbH-CS disease that reflects cellular stress in erythroblasts

  • Open Access
  • Correction

Haodong Liu, Chunting Peng, Qisheng Su, Shijie Liang, Yuling Qiu, Wuning Mo, Zheng Yang

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Starke Schmerzen im rechten Hoden führen einen 37-jährigen Mann in die urologische Praxis. An ein Trauma kann sich der Fitnesstrainer nicht erinnern. Es gibt auch keine Hinweise auf eine Harnwegsinfektion, Harnsteine oder eine sexuell übertragbare Erkrankung. Was ist Ihre Verdachtsdiagnose?

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