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Annals of Hematology

Ausgabe 8/2025

Inhalt (39 Artikel)

Infectious complications in CLL/SLL patients receiving Bruton's Tyrosine Kinase inhibitors – systematic review and meta-analysis of randomized controlled trials

  • Open Access
  • Review

Shira Buchrits, Gal Trieman, Odil Giladi, Liron Hofstetter, Ronit Gurion, Galit Granot, Adi Shacham-Abulafia, Pia Raanani, Anat Gafter-Gvili

The evaluation, management, and future of indolent systemic mastocytosis

  • Open Access
  • Review

Arjun Syal, Jennifer Toh, Alissa McInerney, Douglas Tremblay

Next-generation Bruton tyrosine kinase inhibitors and degraders in the treatment of B-cell malignancies: advances and challenges

  • Open Access
  • Review

Yao Wang, Yaping Zhang, Jiaqi Liu, Yongning Jiang, Jianyong Li, Wenyu Shi

Prognostic significance of in patients with chronic lymphocytic leukemia: A meta-analysis

  • Open Access
  • Review

Liping Huang, Xinyi Shi, Ningning Tang, Juan Liu, Yanli Liang, Xin Wang

Beyond transfusions and transplants: genomic innovations rewriting the narrative of thalassemia

  • Open Access
  • Review

Liangbin Shi, Xili Yan, Yanwei Xia, Yingdi Zhao, Xiuling Zhu, Qiang Li, Zhiliang Xu

Somatic mutations and the efficacy of immunosuppressive therapy in severe/very severe aplastic anemia and transfusion-dependent nonsevere aplastic anemia

  • Open Access
  • Research

Lei Ye, Li Zhang, Donglei Zhang, Xin Zhao, Yuan Li, Youzhen Xiong, Liwei Fang, Meili Ge, Jun Shi, Fengkui Zhang, Liping Jing

Optimizing hemophagocytic lymphohistiocytosis screening in children: validation of the HLH-Screen score

  • Open Access
  • Research

Xiao Li, Zhexuan Tang, Lifang Zhou, Xun Li, Lihui Deng, Haipeng Yan, Xiangyu Wang, Longlong Xie, Ting Luo, Yufan Yang, Xinping Zhang, Jiaotian Huang, Yefei Lei, Zhenghui Xiao, Xiulan Lu

Predictive factors of romiplostim response in patients with refractory aplastic anemia: data from two clinical trials

  • Open Access
  • Research

Jun Ho Jang, Kinuko Mitani, Yoshiaki Tomiyama, Koji Miyazaki, Koji Nagafuji, Kensuke Usuki, Nobuhiko Uoshima, Tomoaki Fujisaki, Hiroshi Kosugi, Itaru Matsumura, Ko Sasaki, Masahiro Kizaki, Masashi Sawa, Michihiro Hidaka, Naoki Kobayashi, Satoshi Ichikawa, Yuji Yonemura, Kenta Murotani, Mami Shimizu, Akira Matsuda, Keiya Ozawa, Shinji Nakao, Jong Wook Lee

Analysis of fecal microbiome in Chinese patients with non-severe aplastic anemia

  • Open Access
  • Research

Xiaolan Zhang, Jingjing Xie, Heng Wang, Jun Li

Genetic modifiers of frequent vaso-occlusive hospitalizations among individuals with sickle cell disease (SCD)

  • Open Access
  • Research

Mina Cintho Ozahata, Isabel Gomes, Beatriz A. Oliveira, Miriam Park, Daniela O. W. Rodrigues, Anna Bárbara Carneiro-Proietti, Cláudia Máximo, Allison Ashley-Koch, Marilyn Telen, Shannon Kelly, Brian Custer, Ester Cerdeira Sabino, Carla Luana Dinardo

Analysis of the current situation and influencing factors of home treatment for children with hemophilia in China

  • Open Access
  • Research

Chunli Wang, Runhui Wu, Xumei Wang, Wei Chi, Xinyi Wu, Guoqing Liu

Three novel heterozygous ANK1 loss-of-function variants cause hereditary spherocytosis in Chinese families

  • Open Access
  • Research

Yang Wang, Tao Liu, Wen Wang, Yuzhuopu Li, Li Xiao, Yan Xiang, Lan Huang, Yongjie Zhang, Jie Yu

Urinary metabolomics predicts early rituximab response in steroid-nonresponsive pediatric patients with primary immune thrombocytopenia

  • Open Access
  • Research

Yuncui Yu, Zhenping Chen, Jing Wei, Xingjuan Xie, Juntao Ouyang, Zheyan Lin, Jingyao Ma, Peng Guo, Runhui Wu, Jingang Gui

Semen quality in acute leukemia patients: a retrospective study

  • Open Access
  • Research

Alessandra Buonacquisto, Maria Ilaria Del Principe, Francesco Pallotti, Serena Bianchini, Elisa Buzzatti, Luisa Caponecchia, Sabina Chiaretti, Gaia Cicolani, Anna Chiara Conflitti, Silvia Di Chiano, Ludovica Fucci, Deborah Kasmi, Clara Minotti, Giovangiacinto Paterno, Ilaria Tiravanti, Adriano Venditti, Francesco Lombardo, Donatella Paoli

t(8;21)AML patients with RUNX1e6::RUNX1T19a splice variant have poor prognosis

  • Open Access
  • Research

Yuying Fan, Lanhui Chen, Sijin Liu, Jinwen Dang, Jianmei Chang, Caifeng Guo, Yang Xu, Wenzheng Guo, Hongwei Wang, Yanhong Tan

Sirolimus modulates the erythroid differentiation of K562 cells by upregulating SHP1

  • Open Access
  • Research

Yuan Yang, Zengwei Tang, Qinglin Hu, Chen Yang, Miao Chen, Hongmei Jing, Bing Han

Gene expression analysis of patients with chronic myeloid leukemia who discontinued tyrosine kinase inhibitor

  • Open Access
  • Research

Hyunkyung Park, Hyeong-Joon Kim, Sang-Kyun Sohn, Yoonsuk Baik, Dongho Kim, Sung-Yeoun Lee, Jee Hyun Kong, Hawk Kim, Dong-Yeop Shin, Jae-Sook Ahn, Jinny Park, Seonyang Park, Inho Kim

Durable outcomes with manageable safety leading to prolonged survival with tagraxofusp for treatment-naïve patients with blastic plasmacytoid dendritic cell neoplasm: real world results from a European Named Patient Program

  • Open Access
  • Research

Marco Herling, Emanuele Angelucci, Tobias Matthieu Benoit, Giulia Rivoli, Antonio Curti, Katharina S. Götze, Stefan Wirths, Dimoula Erakli, Michael Zuurman, Eric Deconinck

De-escalated Teclistamab dosing in relapsed/refractory multiple myeloma: Czech myeloma group real-world evidence analysis

  • Open Access
  • Research

Martin Stork, Jakub Radocha, Jana Mihalyova, Ivan Spicka, Tomas Pika, Alexandra Jungova, Ivanna Boichuk, Klara Mensikova, Jan Straub, Frantisek Sedlak, Jiri Minarik, Petra Krhovska, Denisa Novakova, Michaela Hornakova, Zdenka Knechtova, Nela Sendlerova, Tereza Dekojova, Vladimir Maisnar, Tomas Jelinek, Roman Hajek, Ludek Pour

Prophylactic Tocilizumab prior to infusion of CD19 CAR T-cells reduces therapy-related complications in older lymphoma patients

  • Open Access
  • Research

Sebastian M. Stolz, Albulena Musa, Adrian Bachofner, Andriyana K. Bankova, Elise Gourri, Markus G. Manz, Max J. Rieger, Dominik Schneidawind, Nathan Wolfensberger, Thorsten Zenz, Wiebke Rösler

Exploring the baseline cardiac function and its correlation with risk stratification in children diagnosed with acute lymphoblastic leukemia

  • Open Access
  • Research

Diana R. Lazar, Dana Maniu, Florin-Leontin Lazar, Cristina Blag, Madalina Bota, Mihnea Zdrenghea, Simona Cainap

Pola-R-CHP performed well in first-line Polarix trial-ineligible and IPI 0–1 DLBCL patients

  • Open Access
  • Research

Yuhong Ren, Luya Cheng, Jingli Zhuang, Zhimei Wang, Ling Yuan, Zhixiang Cheng, Yang Ke, Weiguang Wang, Jing Li, Peng Liu

Real-world efficacy and safety outcomes of acalabrutinib in chronic lymphocytic leukemia: primary results of a French multicentre observational study (NAOS)

  • Open Access
  • Research

Anne Quinquenel, Stéphane Leprêtre, Marie Sarah Dilhuydy, Lucile Bussot, Zora Marjanovic, Omar Benbrahim, Romain Guièze, Alberto Santagostino, Caroline Dartigeas, Pierre Feugier, Damien Roos-Weil, Ghandi Damaj, Kamel Laribi, Loic Ysebaert, Vincent Levy

Autologous stem cell transplantation from 2011 to 2022 in Japanese patients aged ≥ 65 years with relapsed or refractory diffuse large B-cell lymphoma

  • Open Access
  • Research

Satoshi Yamasaki, Shohei Mizuno, Kota Yoshifuji, Eri Matsuki, Masashi Sawa, Takashi Akasaka, Naoyuki Uchida, Hitoji Uchiyama, Keisuke Kataoka, Nobuhiro Hiramoto, Yoshinobu Kanda, Kazuya Ishiwata, Toshio Wakayama, Takahiro Fukuda, Makoto Yoshimitsu, Makoto Onizuka, Marie Ohbiki, Yoshiko Atsuta, Ritsuro Suzuki, Shinichi Kako

Comparative longitudinal analysis of pulmonary function post-pediatric Allo-HSCT: benign vs. malignant diseases and early predictors

  • Open Access
  • Research

Hongjuan Li, Yan Gu, Xiaowei Zhao, Guoyu Ding, Yuqi Zhao, Xiaoyue Zhang, Yan Han, Xue Li, Hongmei Wang

Second allogeneic transplantation in relapsed acute leukemia – a risk worth taking?

  • Open Access
  • Research

Patrycja Zielińska, Karolina Gruenpeter, Agata Wieczorkiewicz-Kabut, Krzysztof Białas, Anna Koclęga, Izabela Noster, Izabela Szewczyk, Kinga Boral, Katarzyna Wiśniewska-Piąty, Aleksandra Butrym, Jarosław Czyż, Ewa Lutwin, Grzegorz Helbig

Effectiveness of venetoclax based therapy in t(11;14) multiple myeloma with extensive extramedullary disease: a case report

  • Open Access
  • Case Report

Kerstin Brinkert, Bernd Heinrich, Annamaria Brioli, Michael Heuser, Hans Heinrich Kreipe, Florian H. Heidel, Arnold Ganser, Gernot Beutel

Sickle cell β-thalassemia diagnosed at age 40: a case report

  • Open Access
  • Case Report

Christos G. Nikolaidis, Despoina Gyriki, Dimitrios G. Gogos, Elisavet Stavropoulou

Hyperhemolysis in a sickle cell disease patient in pregnancy

  • Open Access
  • Case Report

Kristen Warncke, Alecia Nero, Ravindra Sarode, Brian D. Adkins, Jamie Morgan, Natalie Bavli

Clinical features and fusion gene analysis of two Torque Teno Mini virus associated acute promyelocytic leukemia cases

  • Open Access
  • Case Report

Deyan Liu, Jiaqi Chen, Yu Luo, Shu Yan, Hua Nan, Xue Chen, Zhongyuan Lin, Liejun Jiang, Huihe Tang, Hongyan Ma, Yumeng Niu, Jiancheng Fang, Panxiang Cao, Lili Yuan, Xiaoli Ma, Xiaosu Zhou, Fanyong LV, Yan Dai, Hongxing Liu

Consequences and impacts of PEG-IFNα2a shortage: first lessons from a MPN French center

  • Open Access
  • Brief Report

Laura Cailly, Wayne-Corentin Lambert, Jean-Richard Eveillard, Brigitte Pan-Petesch, Laura Herbreteau, Laetitia Rio, Lanig Civi, Adrian Tempescul, Florence Dalbies, Hussam Saad, Cristina Bagacean, Marie-Anne Couturier, Gaelle Guillerm, Eric Lippert, Jean-Christophe Ianotto

Venetoclax plus azacitidine as genetic-driven bridge-to-transplant therapy for IDH2-mutated acute myeloid leukaemia (AML) refractory to intensive chemotherapy: proof-of-concept case reports

  • Open Access
  • Correspondence

Gaetano Cimino, Matteo Caridi, Valeria Cardinali, Sofia Sciabolacci, Sara De Santis, Camilla Rellini, Caterina Matteucci, Cristina Mecucci, Paolo Sportoletti, Francesco Zorutti, Alessandra Carotti, Roberta La Starza, Antonio Pierini, Maria Paola Martelli

Validation of the simplified geriatric prognostic index in a Hellenic database of older patients (≥ 70 years old) with diffuse large B-cell lymphoma and similar disorders

  • Open Access
  • Correspondence

Theodoros P. Vassilakopoulos, Fotios Panitsas, Maria Panagiota Arapaki, Amalia Anastasopoulou, Christina Apostolopoulou, Evgenia Verrou, Christina H. Kalpadakis, Alexia Piperidou, Athanasios Liaskas, Sotirios Sachanas, Theodora Triantafyllou, Aikaterini Bitsani, Maria Dimou, Maria Anastasia Ioakeim, Panagiotis Tsirigotis, Marina P. Siakantaris, Vassiliki Pappa, Panayiotis Panayiotidis, Gerassimos A. Pangalis, Eirini Katodritou, Maria K. Angelopoulou, Sotirios G. Papageorgiou

The incidence of paroxysmal nocturnal hemoglobinuria cell clones in the Nordic countries

  • Open Access
  • Correspondence

Torkild Høieggen Pedersen, Eirik Tjønnfjord, Eva-Stina Korkama, Mariann Vikman, Ahmad Ahmadi, Ulrik Malthe Overgaard, Christian Kjellander

Correction to: Mutational heterogeneities in STAT3 and clonal hematopoiesis-related genes in acquired pure red cell aplasia

  • Open Access
  • Correction

Toru Kawakami, Fumihiro Kawakami, Shuji Matsuzawa, Taku Yamane, Yuga Mizuno, Ami Asakura, Daigo Higano, Shotaro Miyairi, Kaoko Sakai, Sayaka Nishina, Hitoshi Sakai, Yasushi Kubota, Yumiko Higuchi, Hideyuki Nakazawa, Fumihiro Ishida

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Wie riskant ist ein Zungenkuss bei Zöliakie?

Die Angst vor unbemerkter Glutenzufuhr ist für viele Zöliakiekranke ein dauernder Begleiter. Ob die Sorge auch bei intensivem Küssen angebracht ist, wurde an der Columbia University unter (fast) standardisierten Bedingungen untersucht.

Standard-Echo: Leitlinie versus deutsche Realität

Deutschland hat erstmals eine eigene Leitlinie für die transthorakale Echokardiografie. Die Realität weicht von diesen Empfehlungen deutlich ab.

HRT nach Oophorektomie auch bei BRCA-Varianten sicher?

Eine Hormonersatztherapie (HRT) nach einer risikoreduzierenden bilateralen Salpingo-Oophorektomie geht bei pathogenen BRCA-Varianten nicht mit einem erhöhten Brustkrebsrisiko einher. Allerdings sind die statistischen Unsicherheiten der Studie sehr groß.

Impfungen: unterschätzte Säule der kardiovaskulären Prävention!

Neben Lebensstilmodifikation sowie medikamentösen und interventionellen Therapien sind auch Impfungen eine wirksame Option zur Prävention kardiovaskulärer Erkrankungen. In der Versorgungsrealität findet das jedoch noch zu wenig Berücksichtigung.

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Die Leitlinien für Ärztinnen und Ärzte, Mann und Frau küssen sich/© AS/peopleimages.com / Stock.adobe.com (Symbolbild mit Fotomodellen), Ältere Dame hält Tabletten und Packungsbeilage in den Händen/© Vladimir Vladimirov / Getty Images / iStock (Symbolbild mit Fotomodell)