Atlantoaxial dislocation due to os odontoideum in patients with Down’s syndrome: literature review and case reports
- 03.11.2019
- Case-Based Update
Erschienen in:
- Verfasst von
- Olga M. Sergeenko
- Konstantin A. Dyachkov
- Sergey O. Ryabykh
- Alexander V. Burtsev
- Alexander V. Gubin
- Erschienen in
- Child's Nervous System | Ausgabe 1/2020
Abstract
Purpose
To clarify etiology, clinical features, and diagnostic and treatment options of atlantoaxial dislocation (AAD) due to os odontoideum (OsO) in patients with Down’s syndrome (DS).
Methods
We described and analyzed three clinical cases of AAD due to OsO in DS patients and reviewed descriptions of similar cases in the scientific sources.
Results
According to literature review, more than 80% of DS patients with odontoid ossicles had atlantoaxial instability (AAI). AAI in DS patients with OsO is more often manifested in childhood and adolescence, rarely in adults when ligament relaxation is reduced. Some patients had acute clinical manifestation after a minor trauma without any precursors; in some of the cases, neurological deterioration increased during several years. We found that the earlier surgical treatment of AAD due to OsO in DS patients carries the higher recovery potential.
Conclusions
Most patients with DS and OsO had AAI. The method of appropriate treatment in such cases is a posterior screw fixation. Preoperative halo traction and posterior fusion have proved to be a very useful tool in the treatment of AAD due to OsO in DS patients. Even if irreducibility of the AAD established preoperatively, it should not be an absolute indication for anterior decompression. In such cases, an attempt to reduce the AAD should be made under general anesthesia during posterior fixation.
Anzeige
- Titel
- Atlantoaxial dislocation due to os odontoideum in patients with Down’s syndrome: literature review and case reports
- Verfasst von
-
Olga M. Sergeenko
Konstantin A. Dyachkov
Sergey O. Ryabykh
Alexander V. Burtsev
Alexander V. Gubin
- Publikationsdatum
- 03.11.2019
- Verlag
- Springer Berlin Heidelberg
- Erschienen in
-
Child's Nervous System / Ausgabe 1/2020
Print ISSN: 0256-7040
Elektronische ISSN: 1433-0350 - DOI
- https://doi.org/10.1007/s00381-019-04401-y
Dieser Inhalt ist nur sichtbar, wenn du eingeloggt bist und die entsprechende Berechtigung hast.
