Bicornuate Uterus with Complete Cervico-Vaginal Agenesis and Skeletal Deformity: A Case Report

Excerpt

Mullerian duct anomalies are one of the most complex female genital tract disorders encountered by obstetricians and gynecologists. The mullerian ducts are differentiated, fused and then canalized to develop fallopian tubes, uterus, cervix and the upper vagina, while the lower part of vagina develops from urogenital sinus. The disruption in the development of mullerian system can lead to a wide variety of uterine and vaginal abnormalities. The American Fertility Society (AFS) classification was previously the most widely accepted for categorizing mullerian duct abnormalities and included seven classes of mullerian anomalies. In 2013, ESHRE consensus introduced the CONUTA classification which classifies the mullerian anomalies into uterine (U), cervical (C) and vaginal (V) abnormalities [1]. This classification has now replaced the AFS classification. Functioning uterus with cervical and vaginal agenesis can lead to the development of hematometra, hematosalpinx, endometriosis and even chronic pelvic pain. The prevalence of congenital vaginal agenesis is 1 in 4000–5000 live births [2], whereas the prevalence of congenital cervical agenesis is 1 in 80,000–100,000 live births [3]. Only 7–8% of patients with vaginal agenesis have a functional uterus. …