Erschienen in:
01.02.2010 | Case Report
Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature
verfasst von:
Elizabeth E. Adams, Vincent P. R. Aluquin, C. April Bingham, James R. Stone, Linda B. Pauliks
Erschienen in:
Pediatric Cardiology
|
Ausgabe 2/2010
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Abstract
Behçet’s disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet’s disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart’s right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.