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Erschienen in: Pediatric Cardiology 2/2010

01.02.2010 | Case Report

Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature

verfasst von: Elizabeth E. Adams, Vincent P. R. Aluquin, C. April Bingham, James R. Stone, Linda B. Pauliks

Erschienen in: Pediatric Cardiology | Ausgabe 2/2010

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Abstract

Behçet’s disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet’s disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart’s right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.
Literatur
1.
Zurück zum Zitat Dogan SM, Birdane A, Korkmaz C, Ata N, Timuralp B (2007) Right ventricular thrombus with Behçet’s disease. Tex Heart Inst J 34:360–362PubMed Dogan SM, Birdane A, Korkmaz C, Ata N, Timuralp B (2007) Right ventricular thrombus with Behçet’s disease. Tex Heart Inst J 34:360–362PubMed
2.
Zurück zum Zitat Gürler A, Boyvat A, Türsen U (1997) Clinical manifestations of Behçet’s disease: an analysis of 2,147 patients. Yonsei Med J 38:423–427PubMed Gürler A, Boyvat A, Türsen U (1997) Clinical manifestations of Behçet’s disease: an analysis of 2,147 patients. Yonsei Med J 38:423–427PubMed
3.
Zurück zum Zitat Huong DLT, Wechsler B, Papo T, de Zuttere D, Bletry O, Hernigou A, Delcourt A, Godeau P, Piette J (1997) Endomyocardial fibrosis in Behçet’s disease. Ann Rheum Dis 56:205–208CrossRefPubMed Huong DLT, Wechsler B, Papo T, de Zuttere D, Bletry O, Hernigou A, Delcourt A, Godeau P, Piette J (1997) Endomyocardial fibrosis in Behçet’s disease. Ann Rheum Dis 56:205–208CrossRefPubMed
4.
Zurück zum Zitat International Study Group for Behçet’s Disease (1990) Criteria for diagnosis of Behcet’s disease. Lancet 335:1078–1080 International Study Group for Behçet’s Disease (1990) Criteria for diagnosis of Behcet’s disease. Lancet 335:1078–1080
5.
Zurück zum Zitat Marzban M, Mandegar MH, Karimi A, Abbasi K, Movahedi N, Navabi M, Abbasi S, Moshtaghi N (2008) Cardiac and great vessel involvement in Behçet’s disease. J Card Surg 23:765–768PubMed Marzban M, Mandegar MH, Karimi A, Abbasi K, Movahedi N, Navabi M, Abbasi S, Moshtaghi N (2008) Cardiac and great vessel involvement in Behçet’s disease. J Card Surg 23:765–768PubMed
6.
Zurück zum Zitat Mogulkoc N, Burgess MI, Bishop PE (2000) Intracardiac thrombus in Behçet’s disease. Chest 118:479–487CrossRefPubMed Mogulkoc N, Burgess MI, Bishop PE (2000) Intracardiac thrombus in Behçet’s disease. Chest 118:479–487CrossRefPubMed
7.
Zurück zum Zitat Nakata Y, Awazu M, Kojima Y, Tokumura M, Yamagishi H, Yamashita N (1995) Behçet’s disease presenting with a right atrial vegetation. Pediatr Cardiol 16:150–152CrossRefPubMed Nakata Y, Awazu M, Kojima Y, Tokumura M, Yamagishi H, Yamashita N (1995) Behçet’s disease presenting with a right atrial vegetation. Pediatr Cardiol 16:150–152CrossRefPubMed
8.
Zurück zum Zitat Sakane T, Takeno M, Suzuki N, Inaba G (1999) Behçet’s disease. N Engl J Med 341:1284–1291CrossRefPubMed Sakane T, Takeno M, Suzuki N, Inaba G (1999) Behçet’s disease. N Engl J Med 341:1284–1291CrossRefPubMed
9.
Zurück zum Zitat Tavil B, Kuskonmaz B, Kiper N, Cetin M, Gumruk F, Gurgey A (2009) Pulmonary thromboembolism in childhood: a single-center experience from Turkey. Heart Lung 38:56–65CrossRefPubMed Tavil B, Kuskonmaz B, Kiper N, Cetin M, Gumruk F, Gurgey A (2009) Pulmonary thromboembolism in childhood: a single-center experience from Turkey. Heart Lung 38:56–65CrossRefPubMed
10.
Zurück zum Zitat Treudler R, Orfanos CE, Zouboulis CC (1999) Twenty-eight cases of juvenile onset Admantiades–Behçet disease in Germany. Dermatology 199:15–19CrossRefPubMed Treudler R, Orfanos CE, Zouboulis CC (1999) Twenty-eight cases of juvenile onset Admantiades–Behçet disease in Germany. Dermatology 199:15–19CrossRefPubMed
11.
Zurück zum Zitat Tursen U, Gurler A, Boyvat A (2003) Evaluation of clinical findings according to sex in 2,313 Turkish patients with Behçet’s disease. Int J Dermatol 42:346–351CrossRefPubMed Tursen U, Gurler A, Boyvat A (2003) Evaluation of clinical findings according to sex in 2,313 Turkish patients with Behçet’s disease. Int J Dermatol 42:346–351CrossRefPubMed
12.
Zurück zum Zitat Wechsler B, Du LT, Kieffer E (1999) Cardiovascular manifestation of Behçet’s disease. Ann Med Int 150:542–554 Wechsler B, Du LT, Kieffer E (1999) Cardiovascular manifestation of Behçet’s disease. Ann Med Int 150:542–554
Metadaten
Titel
Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature
verfasst von
Elizabeth E. Adams
Vincent P. R. Aluquin
C. April Bingham
James R. Stone
Linda B. Pauliks
Publikationsdatum
01.02.2010
Verlag
Springer-Verlag
Erschienen in
Pediatric Cardiology / Ausgabe 2/2010
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-009-9565-4

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