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Erschienen in: Pediatric Surgery International 1/2012

01.01.2012 | Case Report

Congenital extrahepatic portosystemic shunt (Abernethy malformation) treated endovascularly with vascular plug shunt closure

verfasst von: Matthew Passalacqua, Kevin T. Lie, Hooman Yarmohammadi

Erschienen in: Pediatric Surgery International | Ausgabe 1/2012

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Abstract

A 3-year-old boy, who presented with progressive cyanosis and hypoxia, was diagnosed with a large congenital extrahepatic portosystemic shunt, interrupted IVC with azygos continuation, and multiple congenital anomalies. Traditionally open and laparoscopic surgical techniques have been used to treat this malformation. Endovascular repair using a 16-mm Amplatzer vascular plug (AGA Medical Corporation, Golden Valley, Minnesota, USA) was used to occlude the shunt. Immediate post-placement venography demonstrated cessation of flow within the shunt and increased portal venous flow. The patient’s hypoxia and cyanosis decreased significantly, and he was discharged on the 5th post-procedure day in stable clinical condition. Three months follow-up evaluation demonstrated the vascular plug in place, unchanged in position.
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Metadaten
Titel
Congenital extrahepatic portosystemic shunt (Abernethy malformation) treated endovascularly with vascular plug shunt closure
verfasst von
Matthew Passalacqua
Kevin T. Lie
Hooman Yarmohammadi
Publikationsdatum
01.01.2012
Verlag
Springer-Verlag
Erschienen in
Pediatric Surgery International / Ausgabe 1/2012
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-011-2944-y

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