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15.06.2023 | IgA-Vaskulitis | CME

Immunglobulin-A-Vaskulitis (früher Schoenlein-Henoch-Purpura) – ein Update

verfasst von: Dr. med. Toni Hospach, Dominik Müller, Martin Pohl

Erschienen in: Monatsschrift Kinderheilkunde | Ausgabe 7/2023

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Zusammenfassung

Die Immunglobulin(Ig)A-Vaskulitis (IgAV, früher Schoenlein-Henoch-Purpura) ist eine systemische, immunkomplexvermittelte Vaskulitis der kleinen Gefäße, die ist durch die klinische Trias aus palpabler Purpura, Bauch- und Gelenkschmerzen gekennzeichnet. Es ist die häufigste Vaskulitis im Kindes- und Jugendalter. Die Diagnose ist klinisch zu stellen. Die kutane Vaskulitis zeigt überwiegend eine Spontanremission. Die Nieren sind häufig und in unterschiedlichem Ausmaß betroffen. Bei schweren Verläufen können ein akutes Nierenversagen und ein nephrotisches Syndrom auftreten sowie renale Langzeitschäden verbleiben.
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Metadaten
Titel
Immunglobulin-A-Vaskulitis (früher Schoenlein-Henoch-Purpura) – ein Update
verfasst von
Dr. med. Toni Hospach
Dominik Müller
Martin Pohl
Publikationsdatum
15.06.2023
Verlag
Springer Medizin
Erschienen in
Monatsschrift Kinderheilkunde / Ausgabe 7/2023
Print ISSN: 0026-9298
Elektronische ISSN: 1433-0474
DOI
https://doi.org/10.1007/s00112-023-01770-2

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