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Erschienen in: Clinical Oral Investigations 5/2017

20.10.2016 | Original Article

Dental anomalies in 14 patients with IP: clinical and radiological analysis and review

verfasst von: Fernanda D. Santa-Maria, Luiza Monteavaro Mariath, Cláudia S. Poziomczyk, Marcia A. P. Maahs, Rafael F. M. Rosa, Paulo R. G. Zen, Lavínia Schüller-Faccini, Ana Elisa Kiszewski

Erschienen in: Clinical Oral Investigations | Ausgabe 5/2017

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Abstract

Objectives

Current knowledge on dental anomalies in patients with incontinentia pigmenti (IP) has been obtained by examining case reports; however, an overall characterization of such alterations remains lacking. The objective of this study was to determine the frequency, type and location of dental alterations in IP using a case series.

Methods

Fourteen patients (9 children and 5 adults) with a clinical diagnosis of IP who presented dental anomalies were included in this study. All patients were administered a clinical questionnaire, dental examination and radiological investigation.

Results

In the present case series, agenesis of primary dentition was present in 60 % of patients and agenesis of permanent tooth was present in 92.8 % of patients. Most cases were missing at least 6 teeth. Second molar agenesis was present in 13 patients (92.8 %). Anomalies in dental crowns occurred in 71.4 % of cases, and the central incisor was most frequently affected. Two adult patients still had primary teeth. Malocclusion was found in 10 patients (71.4 %). High-arched palate was observed in 7 (50 %) patients.

Conclusions

Patients with IP present alterations in both primary and permanent dentition. Because the agenesis of permanent teeth is more common, primary teeth are not always replaced. In addition, the durability of primary dentition appears to be greater in IP.

Clinical significance

This study shows that patients with IP experience significant loss of teeth, especially in permanent dentition, and have an increased risk of high-arched palate compared to the general population. Prophylactic care of primary teeth in IP is relevant for improving functional and aesthetic outcomes until dental prostheses are implanted.
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Metadaten
Titel
Dental anomalies in 14 patients with IP: clinical and radiological analysis and review
verfasst von
Fernanda D. Santa-Maria
Luiza Monteavaro Mariath
Cláudia S. Poziomczyk
Marcia A. P. Maahs
Rafael F. M. Rosa
Paulo R. G. Zen
Lavínia Schüller-Faccini
Ana Elisa Kiszewski
Publikationsdatum
20.10.2016
Verlag
Springer Berlin Heidelberg
Erschienen in
Clinical Oral Investigations / Ausgabe 5/2017
Print ISSN: 1432-6981
Elektronische ISSN: 1436-3771
DOI
https://doi.org/10.1007/s00784-016-1977-y

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