SFTPs are very rare tumors; only about 800 cases have been reported since it was described by Lamperer and Rabin in 1931 until 2002 [
4,
5]. The incidence rate of SFTPs is 2.8 of 10,000 persons [
6]. Pleural solitary fibrous tumors mainly originate from submesothelial mesodermal tissues of the visceral pleura. SFTPs are mostly benign, and the ratio of malignant degeneration is approximately 12–15% [
6]. SFTPs are a comparatively rare disease composed of about 5% of total pleural tumor developments [
7]. Clinical manifestations of malignant cases are aggressive with local invasion, but metastasis is rare [
8]. SFTPs most frequently occur in individuals aged in their 40s through 60s, and no sex difference in the incidence rate has been reported [
6]. Usually, they are incidentally detected on a chest radiograph, as they do not have noticeable symptoms. About 50% of patients experience respiratory symptoms, such as pleuritic chest pain, coughing, and shortness of breath, or systemic symptoms, such as osteoarthritis, fever, and weight loss [
7]. The paraneoplastic syndrome of hypoglycemia that occurs particularly due to insulin-like growth factor 2 (IGF-II), which is secreted from fibrous tumor cells, is called Doege-Potter syndrome. Only 45 cases of Doege-Potter syndrome have been reported from 1979 to 2011 [
9]. Doege-Potter syndrome develops because of excessive secretion of IGF-II [
6]. To make a histological diagnosis, an optical microscope and immunohistochemical staining are used. Histological sections show diverse shades of grey and a spiral, solid area mixed with soft phlegmatic components and spindle cells with patternless patterns, collagenous stroma with cellularity and hypocellularity tissue [
10,
11] According to the standards suggested by England et al. [
11], malignancy is determined in patients with invasive growth with an unclear boundary, high cell density, 4 or more mitoses per 10 high magnification fields of view, pleomorphism, and the presence of bleeding and necrosis. Cell necrosis and dense tissues are additional signs of a malignant tumor. In a more recent study, a huge size (>15 cm) and, elderly age (>55 years) were the predicted features for a poor prognosis [
2].The definite treatment of SFTPs is surgical treatment with free resection margin [
12]. Prognosis is mostly dependent on the possibility of excision, the size, number of division, and diversity of the cells, and the presence of necrosis [
6]. Excluding the pedunculated tumor, which can be radically treated, the patients was diagnosed as having the disease about 10 year ago and did not undergo surgical resection, death occurred within 10 years [
13]. Even if the tumor is malignant and the patient has polyposis with a clear boundary enabling excision, a good prognosis is possible [
13]. Thus, prognosis is dependent on clear excision. The incidence rate of hypoglycemia associated with a fibrous tumor is very low: only 4% of 360 patients with a solitary fibrous tumor, according to a study conducted in 1981 [
6]. Hypoglycemia has been confirmed to be associated with a large tumor size and high mitosis rate [
8]. In addition, hypoglycemia disappears after the tumor is resected [
12,
14]. For patients without symptoms, a plain radiograph is sufficient for follow-up. Reports on the effects of chemotherapy and irradiation therapy are very rare and limited [
9,
10,
12]. As a result, operative management is the only solution for radical treatment.