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Indian Journal of Hematology and Blood Transfusion

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26.10.2015 | Case Report

Dysfibrinogenemia with Subgaleal Hematoma: An Unusual Presentation

verfasst von: Manika Khare, Vijay Kumar, Sadhna Marwah, A. S. Nigam, Gurdeep Buxi

Erschienen in: Indian Journal of Hematology and Blood Transfusion | Sonderheft 1/2016

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Excerpt

Dysfibrinogenemia is a rare familial disorder characterized by abnormal fibrinogen, which results in defective fibrin clot formation. Dysfibrinogenemia can be congenital or acquired. It is inherited as an autosomal dominant trait with high levels of penetrance. It can diverge in severity from asymptomatic to abnormal clinical bleeding and thrombotic tendency [1]. Subgaleal hematoma is a very unusual presentation in dysfibrinogenemia. …

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Titel: Dysfibrinogenemia with Subgaleal Hematoma: An Unusual Presentation
verfasst von: Manika Khare
Vijay Kumar
Sadhna Marwah
A. S. Nigam
Gurdeep Buxi
Publikationsdatum: 26.10.2015
Verlag: Springer India
Erschienen in: Indian Journal of Hematology and Blood Transfusion / Ausgabe Sonderheft 1/2016
Print ISSN: 0971-4502
Elektronische ISSN: 0974-0449
DOI: https://doi.org/10.1007/s12288-015-0606-2

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Dysfibrinogenemia with Subgaleal Hematoma: An Unusual Presentation

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