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Erschienen in: Pediatric Cardiology 1/2013

01.01.2013 | Case Report

Hemangioendothelioma: A Rare Case of a Primary Intracardiac Tumor

verfasst von: Andrea Beaton, Trevor Kuttler, Ali Hassan, Dilip S. Nath, Christine Reyes, Richard A. Jonas, Gerard R. Martin

Erschienen in: Pediatric Cardiology | Ausgabe 1/2013

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Abstract

Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach–Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.
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Metadaten
Titel
Hemangioendothelioma: A Rare Case of a Primary Intracardiac Tumor
verfasst von
Andrea Beaton
Trevor Kuttler
Ali Hassan
Dilip S. Nath
Christine Reyes
Richard A. Jonas
Gerard R. Martin
Publikationsdatum
01.01.2013
Verlag
Springer-Verlag
Erschienen in
Pediatric Cardiology / Ausgabe 1/2013
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-012-0280-1

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