Skip to main content
Erschienen in: Indian Journal of Hematology and Blood Transfusion 3/2014

01.09.2014 | Case Report

Hemophagocytic Lymphohistiocytosis

verfasst von: A. M. V. R. Narendra, G. Varun Kumar, A. Krishna Prasad, M. Shetty, Megha S. Uppin, V. R. Srinivasan

Erschienen in: Indian Journal of Hematology and Blood Transfusion | Ausgabe 3/2014

Einloggen, um Zugang zu erhalten

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is an immune disorder characterized by uncontrolled inflammation due to defective immune response. It may be familial or acquired, but both share a common feature of threatening the life of a patient and may lead to death unless treated by appropriate treatment. Here in we report a case of adult HLH.
Literatur
1.
Zurück zum Zitat Janaka GE, Shneider EM (2004) Modern management of children with hemophagocytic lymphohistiocytosis. Br J Haematol 124:4–14CrossRef Janaka GE, Shneider EM (2004) Modern management of children with hemophagocytic lymphohistiocytosis. Br J Haematol 124:4–14CrossRef
2.
Zurück zum Zitat Feldmann J, Callebut I et al (2003) Munc13-4 is essential for cytolytic granules fusion and is mutated in form of familial phagocytic lymphohistiocytosis. Cell 115:461–473PubMedCrossRef Feldmann J, Callebut I et al (2003) Munc13-4 is essential for cytolytic granules fusion and is mutated in form of familial phagocytic lymphohistiocytosis. Cell 115:461–473PubMedCrossRef
3.
Zurück zum Zitat Henter JI, Arico M et al (2007) HLH-2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis. Pediatr Blood Cancer 48(2):124–131PubMedCrossRef Henter JI, Arico M et al (2007) HLH-2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis. Pediatr Blood Cancer 48(2):124–131PubMedCrossRef
4.
Zurück zum Zitat Henter JI, Elinder G et al (1991) Incidence in Sweden and Clinical features of familial hemophagocytic lymohohistiocytosis. Acta Paediatr Scand 80(4):428–435PubMedCrossRef Henter JI, Elinder G et al (1991) Incidence in Sweden and Clinical features of familial hemophagocytic lymohohistiocytosis. Acta Paediatr Scand 80(4):428–435PubMedCrossRef
5.
6.
Zurück zum Zitat Ramchandra B, Balasubramanian S et al (2011) Profile of Hemophagocytic lymphohistiocytosis in children in a tertiary care hospital in India. Indian Paediatr 48:31–35CrossRef Ramchandra B, Balasubramanian S et al (2011) Profile of Hemophagocytic lymphohistiocytosis in children in a tertiary care hospital in India. Indian Paediatr 48:31–35CrossRef
7.
Zurück zum Zitat Pramanik S, Pal P et al (2009) Reactive hemophagocytic lymphohistiocytosis. Indian J Paediatr 76(6):643–645CrossRef Pramanik S, Pal P et al (2009) Reactive hemophagocytic lymphohistiocytosis. Indian J Paediatr 76(6):643–645CrossRef
8.
Zurück zum Zitat Bakshi S, Pautu JL (2005) EBV-associated hemophagocytic lymphohistiocytosis with spontaneous regression. Indian Paediatr 42:1253–1255 Bakshi S, Pautu JL (2005) EBV-associated hemophagocytic lymphohistiocytosis with spontaneous regression. Indian Paediatr 42:1253–1255
9.
Zurück zum Zitat Chandra SR, Syamlal S et al (2007) An interesting case of hemiplegia in a child. Ann Indian Acad Neurol 10:49–51CrossRef Chandra SR, Syamlal S et al (2007) An interesting case of hemiplegia in a child. Ann Indian Acad Neurol 10:49–51CrossRef
10.
Zurück zum Zitat Mathew LG, Cherian T et al (2000) Hemophagocytic lymphohistiocytosis-case series. Indian Pediatr 37(5):526–531PubMed Mathew LG, Cherian T et al (2000) Hemophagocytic lymphohistiocytosis-case series. Indian Pediatr 37(5):526–531PubMed
11.
Zurück zum Zitat Agarwal D, Gupta R et al (2010) Hemophagocytic lymphohistiocytosis in a B-cell lymphoproliferaltive disorder: report of rare association. Indian J Hematol Blood Transfus 26(2):74–76CrossRef Agarwal D, Gupta R et al (2010) Hemophagocytic lymphohistiocytosis in a B-cell lymphoproliferaltive disorder: report of rare association. Indian J Hematol Blood Transfus 26(2):74–76CrossRef
12.
Zurück zum Zitat Sashidharan PK, Prashanti Varghese C et al (2011) Primary hemophagocytic syndrome in a young girl. Natl Med J India 24(1):19–20 Sashidharan PK, Prashanti Varghese C et al (2011) Primary hemophagocytic syndrome in a young girl. Natl Med J India 24(1):19–20
Metadaten
Titel
Hemophagocytic Lymphohistiocytosis
verfasst von
A. M. V. R. Narendra
G. Varun Kumar
A. Krishna Prasad
M. Shetty
Megha S. Uppin
V. R. Srinivasan
Publikationsdatum
01.09.2014
Verlag
Springer India
Erschienen in
Indian Journal of Hematology and Blood Transfusion / Ausgabe 3/2014
Print ISSN: 0971-4502
Elektronische ISSN: 0974-0449
DOI
https://doi.org/10.1007/s12288-012-0210-7

Weitere Artikel der Ausgabe 3/2014

Indian Journal of Hematology and Blood Transfusion 3/2014 Zur Ausgabe

Update Onkologie

Bestellen Sie unseren Fach-Newsletter und bleiben Sie gut informiert.