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European Spine Journal

Erschienen in:

14.03.2018 | Grand Rounds

Hirayama disease

verfasst von: David C. Kieser, P. J. Cox, S. C. J. Kieser

Erschienen in: European Spine Journal | Ausgabe 6/2018

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Abstract

Purpose

Hirayama disease is an initially progressive disease caused by cervical neck flexion compressing the anterior horns of the lower cervical spinal cord. It is primarily seen in young males of Indian or Asian descent. With increasing dispersion of these populations this condition is increasingly being encountered internationally. This grand round reviews this rare but increasingly recognized condition.

Materials and methods

We present a classic case of a young Indian male with progressive hand and forearm weakness. We discuss the typical clinical presentation, appropriate investigations and management of this condition.

Results

Our patient presented with oblique amyotrophy and underwent a diagnostic flexion MRI scan which revealed anterior translation of the posterior dura with compression of the anterior horns of the lower cervical cord. He has been successfully treated in a cervical collar.

Conclusions

This case illustrates the typical presentation, diagnostic investigations and treatment of Hirayama syndrome. It is hoped that this review will alert clinicians of this condition and optimize the management of affected individuals.

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Titel: Hirayama disease
verfasst von: David C. Kieser
P. J. Cox
S. C. J. Kieser
Publikationsdatum: 14.03.2018
Verlag: Springer Berlin Heidelberg
Erschienen in: European Spine Journal / Ausgabe 6/2018
Print ISSN: 0940-6719
Elektronische ISSN: 1432-0932
DOI: https://doi.org/10.1007/s00586-018-5545-9

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Expert’s Comment concerning Grand Rounds case entitled “Hirayama disease” by D. C. Kieser, P. J. Cox, S. C. J. Kieser (Eur Spine J; 2018: doi:10.1007/s00586-018-5545-9)

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Vorsicht mit hohen NSAR-Dosen bei ankylosierender Spondylitis!

Brustkrebs in der Vorgeschichte macht Gelenkersatz komplikationsträchtiger

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