Erschienen in:
29.09.2022 | Hauptreferate: Hauptprogramm der DGP
Histiocytic and dendritic cell neoplasms
verfasst von:
Prof. Dr. Dr. h.c. Stefano A. Pileri, Federica Melle, BS, PhD, Giovanna Motta, BS, PhD, Valentina Tabanelli, MD
Erschienen in:
Die Pathologie
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Sonderheft 1/2022
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Abstract
Background
Histiocytic and dendritic cell neoplasms (HDCNs) represent very rare tumors, which have been the subject of debate during the last few years.
Objectives
We aimed to provide a comprehensive review of the subject.
Materials and methods
The experience gained by the authors in large international studies and as a national reference center has been summarized to highlight the characteristics of each entity.
Results
The clinical, morphologic, phenotypic, and molecular data of the different entities included under the heading of HDCNs are extensively discussed.
Conclusion
Currently, HDCNs are classified in the group of orphan diseases for which a standardized therapy is lacking. An international registry would facilitate expansion and dissemination of knowledge of these diseases and improve their treatment.