Ausgabe 1/2013
Inhalt (34 Artikel)
Primary Immunodeficiency Diseases Worldwide: More Common than Generally Thought
Ahmed Aziz Bousfiha, Leïla Jeddane, Fatima Ailal, Ibtihal Benhsaien, Nizar Mahlaoui, Jean-Laurent Casanova, Laurent Abel
Health Related Quality of Life and Emotional Health in Children with Chronic Granulomatous Disease: A Comparison of Those Managed Conservatively with Those That Have Undergone Haematopoietic Stem Cell Transplant
Theresa Cole, Fiona McKendrick, Penny Titman, Andrew J. Cant, Mark S. Pearce, Catherine M. Cale, David Goldblatt, Andrew R. Gennery
EVER2 Deficiency is Associated with Mild T-cell Abnormalities
Amandine Crequer, Capucine Picard, Vincent Pedergnana, Annick Lim, Shen-Ying Zhang, Laurent Abel, Slawomir Majewski, Jean-Laurent Casanova, Stefania Jablonska, Gerard Orth, Emmanuelle Jouanguy
Increased T-Cell Activation and Th1 Cytokine Concentrations Prior to the Diagnosis of B-Cell Lymphoma in HIV Infected Patients
David Eric Ouedraogo, Alain Makinson, Nils Kuster, Nicolas Nagot, Pierre-Alain Rubbo, Karine Bollore, Vincent Foulongne, Guillaume Cartron, Daniel Olive, Jacques Reynes, Jean-Pierre Vendrell, Edouard Tuaillon
Use of Combination Chemotherapy for Treatment of Granulomatous and Lymphocytic Interstitial Lung Disease (GLILD) in Patients with Common Variable Immunodeficiency (CVID)
Nicole M. Chase, James W. Verbsky, Mary K. Hintermeyer, Jill K. Waukau, Aoy Tomita-Mitchell, James T. Casper, Sumit Singh, Kaushik S. Shahir, William B. Tisol, Melodee L. Nugent, R. Nagarjun Rao, A. Craig Mackinnon, Lawrence R. Goodman, Pippa M. Simpson, John M. Routes
Examining the Use of ICD-9 Diagnosis Codes for Primary Immune Deficiency Diseases in New York State
Elena S. Resnick, Priyanka Bhatt, Peter Sidi, Charlotte Cunningham-Rundles
Home Care Use of Intravenous and Subcutaneous Immunoglobulin for Primary Immunodeficiency in the United States
Faith Huang, Elizabeth Feuille, Charlotte Cunningham-Rundles
Clinical, Immunological and Molecular Characterization of DOCK8 and DOCK8-like Deficient Patients: Single Center Experience of Twenty Five Patients
Zobaida Alsum, Abbas Hawwari, Osama Alsmadi, Safa Al-Hissi, Esteban Borrero, Asma’ Abu-staiteh, Hanif G. Khalak, Salma Wakil, Abdelmoneim M. Eldali, Rand Arnaout, Abdulaziz Al-ghonaium, Saleh Al-Muhsen, Hasan Al-Dhekri, Bandar Al-Saud, Hamoud Al-Mousa
Clinical Variability of Family Members with the C104R Mutation in Transmembrane Activator and Calcium Modulator and Cyclophilin Ligand Interactor (TACI)
Wikke Koopmans, See-Tarn Woon, Anna E. S. Brooks, P. Rod Dunbar, Peter Browett, Rohan Ameratunga
The Prevalances and Patient Characteristics of Primary Immunodeficiency Diseases in Turkey—Two Centers Study
Sara S. Kilic, Mustafa Ozel, Demet Hafizoglu, Neslihan Edeer Karaca, Guzide Aksu, Necil Kutukculer
Granulomatous Disease in CVID: Retrospective Analysis of Clinical Characteristics and Treatment Efficacy in a Cohort of 59 Patients
Jean-Nicolas Boursiquot, Laurence Gérard, Marion Malphettes, Claire Fieschi, Lionel Galicier, David Boutboul, Raphael Borie, Jean-François Viallard, Pauline Soulas-Sprauel, Alice Berezne, Arnaud Jaccard, Eric Hachulla, Julien Haroche, Nicolas Schleinitz, Laurent Têtu, Eric Oksenhendler
Post-Transplantation B Cell Function in Different Molecular Types of SCID
Rebecca H. Buckley, Chan M. Win, Barry K. Moser, Roberta E. Parrott, Elisa Sajaroff, Marcella Sarzotti-Kelsoe
Glucocorticoid Regulates Interleukin-37 in Systemic Lupus Erythematosus
Lijun Song, Feng Qiu, Yuchen Fan, Feng Ding, Huaxiang Liu, Qiang Shu, Weiwei Liu, Xingfu Li
Enhancement of Membrane B7-H3 Costimulatory Molecule but Reduction of Its Soluble Form in Multiple Sclerosis
Juean Jiang, Jianhua Jiang, Cuiping Liu, Guangbo Zhang, Li Gao, Yongjing Chen, Ranran Zhu, Ting Wang, Fengmin Wang, Xueguang Zhang, Qun Xue
A Novel Mutation in the Complement Component 3 Gene in a Patient with Selective IgA Deficiency
Elisangela Santos-Valente, Ismail Reisli, Hasibe Artaç, Raphael Ott, Özden Sanal, Kaan Boztug
Are Transglutaminase 2 Inhibitors Able to Reduce Gliadin-Induced Toxicity Related to Celiac Disease? A Proof-of-Concept Study
Tiina Rauhavirta, Mikko Oittinen, Rami Kivistö, Pekka T. Männistö, J. Arturo Garcia-Horsman, Zhuo Wang, Martin Griffin, Markku Mäki, Katri Kaukinen, Katri Lindfors
Serum Growth Arrest-Specific Protein 6 Levels are a Reliable Biomarker of Disease Activity in Systemic Lupus Erythematosus
Hyoun-Ah Kim, Jin-Young Nam, Ja-Young Jeon, Jeong-Mi An, Ju-Yang Jung, Chang-Bum Bae, Chang-Hee Suh
Levels of Circulating Th17 Cells and Regulatory T Cells in Ankylosing Spondylitis Patients with an Inadequate Response to Anti−TNF-α Therapy
Li Xueyi, Chen Lina, Wu Zhenbiao, Han Qing, Li Qiang, Ping Zhu
Mutations of Complement Factor I and Potential Mechanisms of Neuroinflammation in Acute Hemorrhagic Leukoencephalitis
Lori Broderick, Chhavi Gandhi, James L. Mueller, Christopher D. Putnam, Katayoon Shayan, Patricia C. Giclas, Karin S. Peterson, Seema S. Aceves, Robert M. Sheets, Bradley M. Peterson, Robert O. Newbury, Hal M. Hoffman, John F. Bastian
Complement Activation Contributes to the Injury and Outcome of Kidney in Human Anti-glomerular Basement Membrane Disease
Rui Ma, Zhao Cui, Yun-hua Liao, Ming-hui Zhao
The Ex Vivo Production of IL-6 and IL-21 by CD4+ T Cells is Directly Associated with Neurological Disability in Neuromyelitis Optica Patients
Ulisses C. Linhares, Patrícia B. Schiavoni, Priscila O. Barros, Taissa M. Kasahara, Bruna Teixeira, Thais B. Ferreira, Regina Alvarenga, Joana Hygino, Morgana M. M. Vieira, Vera Carolina B. Bittencourt, Regis M. Andrade, Arnaldo F. Andrade, Cleonice A. M. Bento
Activation of Liver X Receptors Suppresses Inflammatory Gene Expressions and Transcriptional Corepressor Clearance in Rheumatoid Arthritis Fibroblast Like Synoviocytes
Chong-Hyeon Yoon, Yong-Jin Kwon, Sang-Won Lee, Yong-Beom Park, Soo-Kon Lee, Min-Chan Park
An Inhibitory Role for Sema4A in Antigen-Specific Allergic Asthma
Tetsuo Morihana, Sho Goya, Masayuki Mizui, Teruhito Yasui, Durubaka V. R. Prasad, Atsushi Kumanogoh, Manabu Tamura, Takashi Shikina, Yohei Maeda, Yoriko Iwamoto, Hidenori Inohara, Hitoshi Kikutani
Susceptibility to Leprosy is Associated with M-ficolin Polymorphisms
Angelica B. W. Boldt, Maria Iolanda N. Sanchez, Ewalda R. S. Stahlke, Rudi Steffensen, Steffen Thiel, Jens C. Jensenius, Flávia Costa Prevedello, Marcelo Távora Mira, Jürgen F. J. Kun, Iara J. T. Messias-Reason
CCR7+ Central and CCR7− Effector Memory CD4+ T Cells in Human Cutaneous Leishmaniasis
Hossein Keshavarz Valian, Mahmoud Nateghi Rostami, Minoo Tasbihi, Akram Miramin Mohammadi, Seyed Ebrahim Eskandari, Abdolfattah Sarrafnejad, Ali Khamesipour
Th2 Responses in OVA-Sensitized BALB/c Mice Are Down-Modulated By Mycobacterium bovis BCG Treatment
Ana Cláudia Carvalho Gouveia, Alessa Sin Singer Brugiolo, Caio César Souza Alves, Flávia Márcia Castro Silva, Felipe Pereira Mesquita, Jacy Gameiro, Ana Paula Ferreira
Nicotine Up-regulated 4-1BBL Expression by Activating Mek-PI3K Pathway Augments the Efficacy of Bone Marrow-Derived Dendritic Cell Vaccination
Hao Jie Jin, Hua Xiu Sui, Yi Nan Wang, Feng Guang Gao
Antibody Response Against Betaferon® in Immune Tolerant Mice: Involvement of Marginal Zone B-cells and CD4+ T-cells and Apparent Lack of Immunological Memory
Melody Sauerborn, Miranda M. C. van Beers, Wim Jiskoot, Grzegorz M. Kijanka, Louis Boon, Huub Schellekens, Vera Brinks
Human Chitotriosidase: a Sensitive Biomarker of Sarcoidosis
Elena Bargagli, David Bennett, Claudia Maggiorelli, Pasquale Di Sipio, Maria Margollicci, Nicola Bianchi, Paola Rottoli
Patterns of Salivary Analytes Provide Diagnostic Capacity for Distinguishing Chronic Adult Periodontitis from Health
Jeffrey L. Ebersole, Julie L. Schuster, Jason Stevens, Dolph Dawson III, Richard J. Kryscio, Yushin Lin, Mark V. Thomas, Craig S. Miller
Combination of IL-1 Receptor Antagonist, IL-20 and CD40 Ligand for the Prediction of Acute Cellular Renal Allograft Rejection
Xiaoguang Xu, Haiyan Huang, Ming Cai, Yeyong Qian, Zhouli Li, Hongwei Bai, Yong Han, Li Xiao, Wenqiang Zhou, Xinying Wang, Bingyi Shi
Kinetics of IgM and IgA Antibody Response to 23-Valent Pneumococcal Polysaccharide Vaccination in Healthy Subjects
Katharina Schütz, Richard G. Hughes, Antony Parker, Isabella Quinti, Vojtech Thon, Monica Cavaliere, Martina Würfel, Wilhelm Herzog, J. Engelbert Gessner, Ulrich Baumann
Elevated Serum Resistin in Juvenile IdiopathicArthritis: Relation to Categories and Disease Activity
Tamer A. Gheita, Iman I. El-Gazzar, Reem I. El Shazly, Abeer M. Nour El-Din, Enas Abdel-Rasheed, Rasha H. Bassyouni
Selective Expansion of Pro-inflammatory Chemokine CCL2-Loaded CD14+CD16+ Monocytes Subset in HIV-Infected Therapy Naïve Individuals
A. Wahid Ansari, Dirk Meyer-Olson, Reinhold E. Schmidt