Ausgabe 3/2017
Inhalt (10 Artikel)
Diagnosis of Interstitial Lung Disease Caused by Possible Hypersensitivity Pneumonitis in a Child: Think CGD
Saliha Esenboga, Nagehan Emiralioglu, Deniz Cagdas, Baran Erman, Martin De Boer, Berna Oguz, Nural Kiper, İlhan Tezcan
Rescue of Cytokine Storm Due to HLH by Hemoadsorption in a CTLA4-Deficient Patient
Christine Greil, Fabian Roether, Paul La Rosée, Bodo Grimbacher, Daniel Duerschmied, Klaus Warnatz
Different Immunological Pathways Underlie the Immune Response to Pneumococcal Polysaccharides
Leen Moens, Capucine Picard, Mohammad Shahrooei, Greet Wuyts, Adrian Liston, Alain Fischer, Xavier Bossuyt
Raised Serum IL-8 Levels Are Associated with Excessive Fatigue in Female Carriers of X-Linked Chronic Granulomatous Disease in the UK
Alexandra C. Battersby, Alexander J. Martin, Jessica Tarn, Fai W. Ng, Catherine M. Cale, David Goldblatt, Andrew R. Gennery
Preference of Genetic Diagnosis of CXCR4 Mutation Compared with Clinical Diagnosis of WHIM Syndrome
Asghar Aghamohammadi, Hassan Abolhassani, Jacek Puchalka, Naschla Greif-Kohistani, Samaneh Zoghi, Christoph Klein, Nima Rezaei
Gastrointestinal Manifestations in X-linked Agammaglobulinemia
Sara Barmettler, Iris M. Otani, Jasmit Minhas, Roshini S. Abraham, Yenhui Chang, Morna J. Dorsey, Zuhair K. Ballas, Francisco A. Bonilla, Hans D. Ochs, Jolan E. Walter
Incidence of typically Severe Primary Immunodeficiency Diseases in Consanguineous and Non-consanguineous Populations
Arnon Broides, Amit Nahum, Amarilla B Mandola, Lihi Rozner, Vered Pinsk, Galina Ling, Baruch Yerushalmi, Jacov Levy, Noga Givon-Lavi
Evaluation of the Safety, Tolerability, and Pharmacokinetics of Gammaplex® 10% Versus Gammaplex® 5% in Subjects with Primary Immunodeficiency
Richard L. Wasserman, Isaac R. Melamed, Mark R. Stein, Stephen Jolles, Miranda Norton, James N. Moy
Serial Serum Immunoglobulin G (IgG) Trough Levels in Patients with X-linked Agammaglobulinemia on Replacement Therapy with Intravenous Immunoglobulin: Its Correlation with Infections in Indian Children
Deepti Suri, Sagar Bhattad, Avinash Sharma, Anju Gupta, Amit Rawat, Shobha Sehgal, Surjit Singh, Sudhir Gupta
Infection Profile in Chronic Granulomatous Disease: a 23-Year Experience from a Tertiary Care Center in North India
Amit Rawat, Pandiarajan Vignesh, Avinash Sharma, Jitendra K. Shandilya, Madhubala Sharma, Deepti Suri, Anju Gupta, Vikas Gautam, Pallab Ray, Shivaprakash M. Rudramurthy, Arunaloke Chakrabarti, Kohsuke Imai, Shigeaki Nonoyama, Osamu Ohara, Yu L. Lau, Surjit Singh