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Journal of Neurology

Ausgabe 8/2016

Inhalt (29 Artikel)

Open Access Review

Clinical features, pathogenesis, and treatment of myasthenia gravis: a supplement to the Guidelines of the German Neurological Society

Nico Melzer, Tobias Ruck, Peter Fuhr, Ralf Gold, Reinhard Hohlfeld, Alexander Marx, Arthur Melms, Björn Tackenberg, Berthold Schalke, Christiane Schneider-Gold, Fritz Zimprich, Sven G. Meuth, Heinz Wiendl

Original Communication

Tissue damage within normal appearing white matter in early multiple sclerosis: assessment by the ratio of T1- and T2-weighted MR image intensity

A. Beer, V. Biberacher, P. Schmidt, R. Righart, D. Buck, A. Berthele, J. Kirschke, C. Zimmer, B. Hemmer, M. Mühlau

Open Access Original Communication

Heterogeneity in clinical features and disease severity in ataxia-associated SYNE1 mutations

Sarah Wiethoff, Joshua Hersheson, Conceicao Bettencourt, Nicholas W. Wood, Henry Houlden

Original Communication

Relapse frequency in transitioning from natalizumab to dimethyl fumarate: assessment of risk factors

Jonathan Zurawski, Ashley Flinn, Lindsay Sklover, Jacob A. Sloane

Original Communication

Postural motor learning in people with Parkinson’s disease

Daniel S. Peterson, Bauke W. Dijkstra, Fay B. Horak

Open Access Original Communication

Event-related EEG power modulations and phase connectivity indicate the focus of attention in an auditory own name paradigm

Julia Lechinger, Tomasz Wielek, Christine Blume, Gerald Pichler, Gabriele Michitsch, Johann Donis, Walter Gruber, Manuel Schabus

Original Communication

Objective characterization of daily living transitions in patients with Parkinson’s disease using a single body-fixed sensor

Hagar Bernad-Elazari, Talia Herman, Anat Mirelman, Eran Gazit, Nir Giladi, Jeffrey M. Hausdorff

Original Communication

Expanding the spectrum of PEX10-related peroxisomal biogenesis disorders: slowly progressive recessive ataxia

Mathilde Renaud, Claire Guissart, Martial Mallaret, Sacha Ferdinandusse, David Cheillan, Nathalie Drouot, Jean Muller, Mireille Claustres, Christine Tranchant, Mathieu Anheim, Michel Koenig

Original Communication

XPR1 mutations are a rare cause of primary familial brain calcification

Mathieu Anheim, Uriel López-Sánchez, Donatella Giovannini, Anne-Claire Richard, Jawida Touhami, Ludovic N’Guyen, Gabrielle Rudolf, Anne Thibault-Stoll, Thierry Frebourg, Didier Hannequin, Dominique Campion, Jean-Luc Battini, Marc Sitbon, Gaël Nicolas

Original Communication

PROSPERA: a randomized, controlled trial evaluating rasagiline in progressive supranuclear palsy

Georg Nuebling, Mira Hensler, Sabine Paul, Andreas Zwergal, Alexander Crispin, Stefan Lorenzl

Original Communication

Subcortical matter in the α-synucleinopathies spectrum: an MRI pilot study

S. Gazzina, E. Premi, R. Turrone, J. Acosta-Cabronero, M. C. Rizzetti, M. S. Cotelli, R. Gasparotti, A. Padovani, B. Borroni

Original Communication

Alterations of functional and structural connectivity of freezing of gait in Parkinson’s disease

Min Wang, Siming Jiang, Yongsheng Yuan, Li Zhang, Jian Ding, Jianwei Wang, Jiejin Zhang, Kezhong Zhang, Jie Wang

Original Communication

Cognition and eating behavior in amyotrophic lateral sclerosis: effect on survival

R. M. Ahmed, J. Caga, E. Devenney, S. Hsieh, L. Bartley, E. Highton-Williamson, E. Ramsey, M. Zoing, G. M. Halliday, O. Piguet, J. R. Hodges, M. C. Kiernan

Original Communication

A series of Greek children with pure hereditary spastic paraplegia: clinical features and genetic findings

Alexandros A. Polymeris, Alessandra Tessa, Katherine Anagnostopoulou, Anna Rubegni, Daniele Galatolo, Argirios Dinopoulos, Artemis D. Gika, Sotiris Youroukos, Eleni Skouteli, Filippo M. Santorelli, Roser Pons

Original Communication

Natalizumab discontinuation is associated with a rebound of cognitive impairment in multiple sclerosis patients

Pietro Iaffaldano, Rosa Gemma Viterbo, Maria Trojano

Original Communication

Safety and efficacy of dimethyl fumarate in multiple sclerosis: a multi-center observational study

A. Miclea, V. I. Leussink, H. P. Hartung, R. Gold, R. Hoepner

Original Communication

Clinical prediction of large vessel occlusion in anterior circulation stroke: mission impossible?

Mirjam R. Heldner, Kety Hsieh, Anne Broeg-Morvay, Pasquale Mordasini, Monika Bühlmann, Simon Jung, Marcel Arnold, Heinrich P. Mattle, Jan Gralla, Urs Fischer

Open Access Original Communication

Patient-reported adverse effects of high-dose intravenous methylprednisolone treatment: a prospective web-based multi-center study in multiple sclerosis patients with a relapse

Peter Joseph Jongen, Ioanna Stavrakaki, Bernard Voet, Erwin Hoogervorst, Erik van Munster, Wim H. Linssen, Ludovicus G. Sinnige, Wim I. Verhagen, Leo H. Visser, Ruud van der Kruijk, Freek Verheul, Jan Boringa, Marco Heerings, Werner Gladdines, Fredrik Lönnqvist, Pieter Gaillard

Letter to the Editors

Whipple’s disease without gastrointestinal symptoms: a challenging diagnosis

Marta Campagnolo, Sofia Tognon, Sara Pompanin, Andrea Sattin, Annachiara Cagnin, Chiara Briani

Letter to the Editors

Nicolaides–Baraitser syndrome: defining a phenotype

Elena Pretegiani, Francesca Mari, Alessandra Renieri, Silvana Penco, Maria Teresa Dotti

Letter to the Editors

A painted staircase illusion to alleviate freezing of gait in Parkinson’s disease

Sabine Janssen, Mileha Soneji, Jorik Nonnekes, Bastiaan R. Bloem

Letter to the Editors

The role of polymyography in the treatment of cervical dystonia

Roberto Erro, Kailash P. Bhatia, Marcello Esposito, Carla Cordivari

Open Access Letter to the Editors

l-Arginine intervention at hyper-acute phase protects the prolonged MRI abnormality in MELAS

Miyuki Kitamura, Shuichi Yatsuga, Toshi Abe, Nataliya Povalko, Reo Saiki, Kikumi Ushijima, Yushiro Yamashita, Yasutoshi Koga

Open Access Neurological Update

The effect of shunt surgery on neuropsychological performance in normal pressure hydrocephalus: a systematic review and meta-analysis

Katie A. Peterson, George Savulich, Dan Jackson, Clare Killikelly, John D. Pickard, Barbara J. Sahakian

Pioneers in Neurology

Luigi Calori (1807–1896)

Francesco M. Galassi, Giorgio Gruppioni, Alessandro Ruggeri, Raffaella Bianucci, Frank J. Rühli

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