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Die Dermatologie
Erschienen in: Der Hautarzt 5/2020

17.04.2020 | Gelenkschmerzen | Leitthema

Klinische Symptomatik autoinflammatorischer Erkrankungen

verfasst von: Dr. E. Rolfes, G. Ngoumou, H. Bonnekoh, K. Krause, T. Kallinich

Erschienen in: Die Dermatologie | Ausgabe 5/2020

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Zusammenfassung

Systemische autoinflammatorische Erkrankungen sind gekennzeichnet durch eine über die angeborene Immunität vermittelte spontan ablaufende chronische Entzündungsreaktion, die sich an vielen Organsystemen und insbesondere auch an der Haut manifestiert. Die Diagnostik bleibt trotz neuer molekulargenetischer Verfahren eine Herausforderung, jedoch ist eine frühe Diagnosestellung zur Prävention von Langzeitkomplikationen, wie z. B. der Amyloidose, entscheidend. Hautmanifestationen sind oft früh im Krankheitsverlauf zu beobachten und können bei der Diagnosestellung entscheidend sein.
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Metadaten
Titel
Klinische Symptomatik autoinflammatorischer Erkrankungen
verfasst von
Dr. E. Rolfes
G. Ngoumou
H. Bonnekoh
K. Krause
T. Kallinich
Publikationsdatum
17.04.2020
Verlag
Springer Medizin
Erschienen in
Die Dermatologie / Ausgabe 5/2020
Print ISSN: 2731-7005
Elektronische ISSN: 2731-7013
DOI
https://doi.org/10.1007/s00105-020-04582-7

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