Key Points
• Notochordal tumors may be benign or malignant
• Notochordal tumors have a predilection for the spheno-occipital and sacral regions
• Benign notochordal tumors tend to be detected on MRI but demonstrate little or no abnormality on radiographs, CT or bone scintigraphy.
• Chordoma accounts for 50% of malignant sacral tumors.
• Sacral chordomas are predominently osteolytic with 90% showing varying degrees of calcification on CT, all showing an anterior soft tissue mass and 77% a posterior soft tissue mass on MRI.
• Biopsy identification of choirdoid tissue needs to be carefully correlated with MRI and CT appearances to decide if it represents BNCT or chordoma.
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Cassar-Pullicino, V., Mangham, D. (2009). Notochordal Tumours. In: Davies, A., Sundaram, M., James, S. (eds) Imaging of Bone Tumors and Tumor-Like Lesions. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-77984-1_20
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