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Pancreatoblastoma in a neonate with Wiedemann-Beckwith syndrome

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Abstract

The association of pancreatoblastoma and Wiedemann-Beckwith syndrome has not been noted previously. In this report we describe a child with Wiedemann-Beckwith syndrome who had a pancreatoblastoma resected on day 27 of life. He is also the first reported case of Wiedemann-Beckwith syndrome in a black baby.

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Koh, T.H.H.G., Cooper, J.E., Newman, C.L. et al. Pancreatoblastoma in a neonate with Wiedemann-Beckwith syndrome. Eur J Pediatr 145, 435–438 (1986). https://doi.org/10.1007/BF00439255

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  • DOI: https://doi.org/10.1007/BF00439255

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