Summary
Patients with the Beckwith-Wiedemann (B-W) syndrome have been reported to have an increased risk of congenital heart disease and of idiopathic cardiomegaly on chest x-ray. In the infant described here, reversible obstructive hypertrophic cardiomyopathy was documented and its relationship to the metabolic features of the B-W syndrome is discussed.
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References
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Ryan, C.A., Boyle, M.H. & Burggraf, G.W. Reversible obstructive hypertrophic cardiomyopathy in the Beckwith-Wiedemann syndrome. Pediatr Cardiol 10, 225–228 (1989). https://doi.org/10.1007/BF02083298
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DOI: https://doi.org/10.1007/BF02083298