Abstract
The anaesthetic management for Caesarean delivery is described in a patient with May- Hegglin anomaly. The condition, which is inherited as an autosomal dominant characteristic, has features of thrombocytopenia and a bleeding diathesis. Labour was induced and she received type specific platelet transfusion. Spinal anaesthesia, using five per cent lidocaine, 75 mg, with epinephrine and 0.5 mg morphine sulphate produced satisfactory operating conditions, excellent postoperative analgesia, and uncomplicated initial recovery.
Résumé
Une primipare porteuse d’un syndrome de May-Hegglin (thrombocytopénie et diathèse hémorragique), transmis par mode autosomal dominant se présenta à l’hôpital en travail. On lui donna des oxytociques et on lui fît une transfusion de plaquettes de son groupe sanguin. Pour la césarienne, on pratique une anesthésie rachidienne en injectant 75 mg de lidocaine à cinq pour cent avec adrénaline et 0.5 mg de sulfate de morphine. Les conditions opératoires et l’analgésie post-opératoire ont été tout a fait adéquates.
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Kotelko, D.M. Anaesthesia for caesarean delivery in a patient with May-Hegglin anomaly. Can J Anaesth 36, 328–330 (1989). https://doi.org/10.1007/BF03010774
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DOI: https://doi.org/10.1007/BF03010774