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Surgical and Radiologic Anatomy

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01.05.2011 | Anatomic Variations

Congenital absence of the portal vein in a middle-aged man

verfasst von: Flavio Barchetti, Luigi Pellegrino, Najwa Al-Ansari, Valentina De Marco, Paolo Scarpato, Pasquale Ialongo

Erschienen in: Surgical and Radiologic Anatomy | Ausgabe 4/2011

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Abstract

Congenital absence of the portal vein with systemic diversion of mesenteric blood is extremely rare. We report a case of a congenital absence of the portal vein, accidentally discovered in a 59-year-old man, completely asymptomatic and not associated with other malformations or biochemical disorders. Ultrasonography imaging showed the absence of the portal vein and the distal tract of superior mesenteric and splenic veins draining together into a dilated left renal vein. Computed tomography and magnetic resonance confirmed the presence of a congenital portosystemic venous shunt and also revealed two hepatic arteries: one arising from the celiac trunk and the other from the superior mesenteric artery.

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Titel: Congenital absence of the portal vein in a middle-aged man
verfasst von: Flavio Barchetti
Luigi Pellegrino
Najwa Al-Ansari
Valentina De Marco
Paolo Scarpato
Pasquale Ialongo
Publikationsdatum: 01.05.2011
Verlag: Springer-Verlag
Erschienen in: Surgical and Radiologic Anatomy / Ausgabe 4/2011
Print ISSN: 0930-1038
Elektronische ISSN: 1279-8517
DOI: https://doi.org/10.1007/s00276-010-0711-8

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