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Child's Nervous System
Erschienen in: Child's Nervous System 10/2011

01.10.2011 | Special Annual Issue

Hydrocephalus and Chiari type I malformation

verfasst von: Concezio Di Rocco, Paolo Frassanito, Luca Massimi, Simone Peraio

Erschienen in: Child's Nervous System | Ausgabe 10/2011

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Abstract

Intoduction

Hydrocephalus has been related to Chiari type I malformation (CIM) for a long time. The pathogenesis of this association is complex and still debated.

Discussion

A supratentorial hypertensive hydrocephalus may cause CIM, exerting pressure from above. Another pathogenetic hypothesis is based on the clinical and radiological data from patients affected by complex craniosynostosis, in which this association is more commonly observed as the consequence of a “cephalo-cranial disproportion” ultimately leading to a secondary hydrocephalus. In some cases, the concomitant presence of a stenosis of the jugular foramina would determine a condition of upward venous hypertension, resulting in the development of CIM and an associated hydrocephalus due to cerebellar parenchyma turgor.

Conclusions

The radiological association of ventricular enlargement and hindbrain herniation would be the result of heterogeneous pathogenetic mechanisms which would then require specific therapeutic approaches. In this context, the endoscopic third ventricle-cisternostomy is gaining an increasing interest because of its more physiologic correction of the altered CSF dynamics and its minor interference on the developmental processes responsible for the association of hydrocephalus and CIM.
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Metadaten
Titel
Hydrocephalus and Chiari type I malformation
verfasst von
Concezio Di Rocco
Paolo Frassanito
Luca Massimi
Simone Peraio
Publikationsdatum
01.10.2011
Verlag
Springer-Verlag
Erschienen in
Child's Nervous System / Ausgabe 10/2011
Print ISSN: 0256-7040
Elektronische ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-011-1545-3

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