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Erschienen in: Heart Failure Reviews 1/2010

01.01.2010

Cardiomyopathy in Duchenne muscular dystrophy: pathogenesis and therapeutics

verfasst von: Abdallah Fayssoil, Olivier Nardi, David Orlikowski, Djillali Annane

Erschienen in: Heart Failure Reviews | Ausgabe 1/2010

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Abstract

Duchenne muscular dystrophy (DMD) is an X-linked recessive disorder caused by the absence of dystrophin, a sarcolemmal protein which links the cytoskeleton to the extracellular matrix by interacting with a large number of proteins. Heart failure is a classic complication of this disease. The authors review the pathogenesis and therapeutics of cardiac involvement in DMD.
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Metadaten
Titel
Cardiomyopathy in Duchenne muscular dystrophy: pathogenesis and therapeutics
verfasst von
Abdallah Fayssoil
Olivier Nardi
David Orlikowski
Djillali Annane
Publikationsdatum
01.01.2010
Verlag
Springer US
Erschienen in
Heart Failure Reviews / Ausgabe 1/2010
Print ISSN: 1382-4147
Elektronische ISSN: 1573-7322
DOI
https://doi.org/10.1007/s10741-009-9156-8

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