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John Walton
2021, Child Neurology: Its Origins, Founders, Growth and EvolutionClinical neurophysiology of anterior horn cell disorders
2019, Handbook of Clinical NeurologyCitation Excerpt :In SMA type III, fibrillation potentials tend to occur more in the proximal muscles compared to distal muscles and more in the lower limbs compared to the upper limbs (Hausmanowa-Petrusewicz et al., 1980). Complex repetitive discharges typically occur with SMA type III and rarely in SMA type I. Only about 20% of patients with SMA type I have electrically detectable fasciculation potentials, whereas about 60% of SMA type III patients have fasciculation potentials (Gardner-Medwin et al., 1967). There are a variety of other techniques that have been applied to motor neuron disease, usually in the research setting.
Inherited Neuronal Atrophy and Degeneration Predominantly of Lower Motor Neurons
2005, Peripheral Neuropathy: 2-Volume Set with Expert Consult BasicInherited Neuronal Atrophy and Degeneration Predominantly of Lower Motor Neurons
2005, Peripheral NeuropathyNeedle electromyography
2004, Handbook of Clinical NeurophysiologyCitation Excerpt :The reported incidence of fibrillation potentials has varied up to 100% (Kuntz et al., 1980). Low-amplitude, short-duration, varying MUPs occur with attempts at reinnervation in young children; they should not suggest an additional myopathy (Gardner-Medwin et al., 1967; Carleton and Brown, 1979; Kuntz et al., 1980). Fasciculation potentials are seen in only 35% or less of children with MND, much less than in ALS; their absence cannot exclude MND.