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Anomalous left coronary artery from the right coronary cusp with gene positive apical hypertrophic cardiomyopathy: a case report and literature review

Published online by Cambridge University Press:  17 December 2013

Justin Georgekutty ,
Russell R. Cross ,
Joanna B. Rosenthal ,
Deneen M. Heath ,
Pranava Sinha  and
Anitha S. John
Justin Georgekutty
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Russell R. Cross
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Joanna B. Rosenthal
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Deneen M. Heath
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Pranava Sinha
Affiliation:
Department of Pediatrics, Division of Cardiac Surgery, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Anitha S. John*
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
*
Correspondence to: Dr A. S. John, MD, PhD, Assistant Professor of Pediatrics and Internal Medicine, Division of Cardiology, Children’s National Medical Center, 111 Michigan Ave NW, West Wing, 3.5, Washington, DC 20010, United States of America. Tel: 202 476 3543; Fax: 202 476 5700; E-mail: anjohn@childrensnational.org
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Abstract

In the United States, hypertrophic cardiomyopathy and coronary artery anomalies account for the leading two causes of sudden death in athletes. We present a case of a patient with an anomalous origin of the left main from the right coronary sinus with associated gene-confirmed hypertrophic cardiomyopathy. The patient underwent surgical repair with unroofing of the intramural portion of the left main coronary artery with a good result. We also review the reported cases in the medical literature describing this uncommon association between anomalous coronary artery origin and hypertrophic cardiomyopathy.

Keywords

Anomalous coronary arteryhypertrophic cardiomyopathysudden cardiac death
Type
Review Articles
Information
Cardiology in the Young , Volume 24 , Issue 3 , June 2014 , pp. 397 - 402
Copyright
© Cambridge University Press 2013 

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