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Section Editor: Marilyn J. Siegel, MD

Cystic Type IV Sacrococcygeal Teratoma

Journal of Perinatology volume 22, pages 331–332 (2002)Cite this article

Sacrococcygeal teratoma is the most common neonatal neoplasm. It is found predominantly in females and discovered in the neonatal period.1 These tumors are believed to arise from embryologically multipotent cells of Hensen's node, which lies within the coccyx.1

The tumors are classified, according to Altman Classification of the Surgical Section of the American Academy of Pediatrics, into four types: Type I, those tumors that are predominantly external projecting from the sacrococcygeal region and presenting with distortion of the buttocks; Type II, those tumors that are predominantly external, but have a large intrapelvic component; Type III, those that are predominantly intrapelvic with a small external, buttock mass; Type IV, those that are entirely internal with no external or buttock component.1 Type IV sacrococcygeal teratomas may occur as a familial form inherited as an autosomal dominant condition. In this entity, a presacral mass (teratoma, anterior meningocele, dermoid cyst, lipoma, neurofibroma, enteric cysts, or hamartoma) is associated with anal stenosis and typical Scimitar defect of the sacrum. This is often referred to as Currarino triad.2,4 Approximately 45% of teratomas is Type I, 35% is Type II, 10% Type III, and 10% Type IV.4

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  1. Department of Radiology, Washington University School of Medicine, St. Louis Children's Hospital, 510 South Kingshighway Boulevard, St. Louis, MO, USA

    Thomas E Herman MD & Marilyn J Siegel MD

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  1. Thomas E Herman MD
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  2. Marilyn J Siegel MD
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Herman, T., Siegel, M. Cystic Type IV Sacrococcygeal Teratoma. J Perinatol 22, 331–332 (2002). https://doi.org/10.1038/sj.jp.7210706

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