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Eur J Pediatr Surg 2009; 19(2): 117-119
DOI: 10.1055/s-2008-1039007
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© Georg Thieme Verlag KG Stuttgart · New York

Retro-hepatic Gastric Volvulus Secondary to Polysplenic Syndrome

L. E. Jesus1 , 2 , A. M. Faccioni2 , H. N. Lemos2
  • 1Department of Pediatric Surgery, Hospital Universitário Antônio Pedro, Niterói, Brazil
  • 2Department of Pediatric Surgery, Hospital dos Servidores do Estado, Rio de Janeiro, Brazil
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Publication History

Publication Date:
17 February 2009 (online)

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Introduction

Heterotaxic syndromes are uncommon embryopathies with an unfavorable prognosis. Left heterotaxy (also called polysplenic syndrome or left isomerism) predominates in females. Cardiac defects are less common and more serious than in asplenic patients, but digestive problems are more common. Intestinal malrotation, gastric volvulus, duodenal sub-occlusion and biliary atresia are possible.

We report a clinical patient who is, as far as the authors are concerned, the first published case of a retro-hepatic gastric volvulus presenting in a patient with left isomerism.

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Dr. M.D. Lisieux Eyer Jesus

Department of Pediatric Surgery
Hospital Universitário Antônio Pedro

R Presidente Domiciano 52/801

24210-270 Niterói

Brazil

Email: lisieux@uol.com.br

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