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Clin Colon Rectal Surg 2012; 25(02): 083-089
DOI: 10.1055/s-0032-1313778
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Familial Adenomatous Polyposis: Challenges and Pitfalls of Surgical Treatment

Satish K. Warrier
1   Department of Colorectal Surgery, Digestive Disease Institute, Cleveland Clinic, Cleveland, Ohio.
2   Sanford R. Weiss, M.D. Center for Hereditary Colorectal Neoplasia, Digestive Disease Institute, Cleveland Clinic, Cleveland, Ohio.
,
Matthew F. Kalady
1   Department of Colorectal Surgery, Digestive Disease Institute, Cleveland Clinic, Cleveland, Ohio.
2   Sanford R. Weiss, M.D. Center for Hereditary Colorectal Neoplasia, Digestive Disease Institute, Cleveland Clinic, Cleveland, Ohio.
› Author Affiliations
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Publication History

Publication Date:
30 May 2012 (online)

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Abstract

Surgical management of familial adenomatous polyposis (FAP) is complex and requires both sound judgment and technical skills. Because colorectal cancer risk approaches 100%, prophylactic colorectal surgery remains a cornerstone of management. Both patient factors and disease characteristics influence surgical decision-making regarding the timing of prophylactic surgery, the extent of resection, and types of reconstruction. Making appropriate choices can be challenging and there is continued debate regarding optimal strategies. This chapter reviews the controversies in colorectal surgery for FAP.

Keywords

familial adenomatous polyposis - total proctocolectomy - colorectal surgery
 

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