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CC BY-NC-ND 4.0 · J Neurol Surg Rep 2018; 79(04): e98-e102
DOI: 10.1055/s-0038-1676455
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Sporadic Hemangioblastoma of the Cavernous Sinus and Meckel's Cave

Ali Kord Valeshabad
1   Department of Radiology, University of Illinois at Chicago, Chicago, Illinois, United States
,
Lekui Xiao
1   Department of Radiology, University of Illinois at Chicago, Chicago, Illinois, United States
,
Sepideh Amin-Hanjani
2   Department of Neurosurgery, University of Illinois at Chicago, Chicago, Illinois, United States
,
Alaa Alsadi
3   Department of Pathology, University of Illinois at Chicago, Chicago, Illinois, United States
,
Tibor Valyi-Nagy
3   Department of Pathology, University of Illinois at Chicago, Chicago, Illinois, United States
,
Jinsuh Kim
4   Department of Radiology, University of Alabama at Birmingham, Birmingham, Alabama, United States
› Author Affiliations
Further Information

Publication History

13 February 2018

28 August 2018

Publication Date:
12 December 2018 (online)

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Abstract

Objectives To describe an extremely rare case of sporadic hemangioblastoma (HB) within the cavernous sinus and Meckel's cave with extension to the cerebellopontine angle (CPA) cistern.

Methods A 73-year-old male presented with hearing loss, unilateral ptosis, and facial numbness.

Results The imaging showed a complex cystic-solid mass centered at the left cavernous sinus and Meckel's cave with extension to the CPA cistern. Patient underwent retrosigmoid craniectomy for partial resection of the CPA angle component of the mass. Surgical pathology confirmed the diagnosis of HB and patient was scheduled for subsequent radiotherapy of the residual mass.

Conclusions We present an exceptional case of supratentorial HB without associated von Hippel–Lindau (VHL) disease, which was predominantly located in the cavernous sinus and Meckel's cave and led to multiple cranial nerve symptoms. We describe imaging characteristics and radiologic–pathologic correlation of this atypically located HB, which can be difficult to consider in the differential diagnosis presurgically.

Keywords

hemangioblastoma - cavernous sinus - Meckel's cave - cerebellopontine angle - denervation atrophy
 

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