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J Neurol Surg B Skull Base 2019; 80(02): 196-202
DOI: 10.1055/s-0039-1678731
Invited Review
Georg Thieme Verlag KG Stuttgart · New York

Intralabyrinthine Schwannomas: Disease Presentation, Tumor Management, and Hearing Rehabilitation

Baishakhi Choudhury
1   Department of Otolaryngology Head and Neck Surgery, Loma Linda University Health, Loma Linda, California, United States
,
Matthew L. Carlson
2   Department of Otorhinolaryngology Head and Neck Surgery, Mayo Clinic, Rochester, Minnesota, United States
,
Daniel Jethanamest
3   Department of Otolaryngology Head and Neck Surgery, NYU Langone Health, New York, New York, United States
› Author Affiliations
Further Information

Publication History

29 December 2018

31 December 2018

Publication Date:
01 March 2019 (online)

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Abstract

Intralabyrinthine schwannomas (ILS) are rare tumors that frequently cause sensorineural hearing loss. The development and increased use of magnetic resonance imaging in recent years have facilitated the diagnosis of these tumors that present with otherwise nondiscriminant symptoms such as tinnitus, vertigo, and hearing loss. The following is a review of the presentation, pathophysiology, imaging, and treatment with a focused discussion on auditory rehabilitation options of ILS.

Keywords

intralabyrinthine schwannoma - intracochlear schwannoma - intravestibular schwannoma - primary inner ear schwannoma - dizziness - tinnitus - hearing loss - auditory rehabilitation - inner ear masses
 

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