Polysplenia Syndrome with Various Visceral Anomalies in an Adult : Embryological and Clinical Considerations

Shinjiro MUNETA; Shuji SAKAI; Hiroshi FUKUDA; Yoichi IMAMURA; Isao MATSUMOTO

doi:10.2169/internalmedicine.31.1026

Shinjiro MUNETA, Shuji SAKAI, Hiroshi FUKUDA, Yoichi IMAMURA, Isao MATSUMOTO

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Keywords: short pancreas, preduodenal portal vein, azygos continuation of the inferior vena cava, bilateral hyparterial bronchi, malrotation of the bowel

JOURNAL FREE ACCESS

1992 Volume 31 Issue 8 Pages 1026-1031

DOI https://doi.org/10.2169/internalmedicine.31.1026

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Abstract

A 26-year-old female with polysplenia syndrome is reported. She had numerous visceral anomalies including polysplenia, a short pancreas, a preduodenal portal vein, malrotation of the bowel, azygos continuation of the in erior vena cava, bilateral hyparterial bronchi and symmetrical liver lobation. Embryological and clinical considerations of polysplenia syndrome are described.
(Internal Medicine 31 : 1026-1031, 1992)

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