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Erschienen in: Journal of General Internal Medicine 5/2017

16.02.2017 | Clinical Practice: Clinical Vignettes

Nutcracker Syndrome and Sickle Cell Trait: A Perfect Storm for Hematuria

verfasst von: Amier Ahmad, MD, Samuel K. McElwee, MD, Ryan R. Kraemer, MD

Erschienen in: Journal of General Internal Medicine | Ausgabe 5/2017

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Abstract

We describe the case of a 27-year-old woman with a history of sickle cell trait (SCT) who presented with several months of hematuria and was found to have nutcracker syndrome (NCS). While SCT is a common cause of hematuria resulting from renal papillary necrosis, our patient had concomitant abdominal pain and anemia, prompting further evaluation and the subsequent diagnosis of NCS. Interestingly, the anoxia in the left renal vein from NCS predisposes patients with SCT to sickling. Our case highlights key clinical features of both NCS and SCT and the relationship between the two disease processes.
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Metadaten
Titel
Nutcracker Syndrome and Sickle Cell Trait: A Perfect Storm for Hematuria
verfasst von
Amier Ahmad, MD
Samuel K. McElwee, MD
Ryan R. Kraemer, MD
Publikationsdatum
16.02.2017
Verlag
Springer US
Erschienen in
Journal of General Internal Medicine / Ausgabe 5/2017
Print ISSN: 0884-8734
Elektronische ISSN: 1525-1497
DOI
https://doi.org/10.1007/s11606-017-4008-z

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