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Child's Nervous System
Erschienen in: Child's Nervous System 10/2007

01.10.2007 | Review Paper

Pansynostosis: a review

verfasst von: Jeffrey P. Blount, Robert G. Louis Jr., R. Shane Tubbs, John H. Grant

Erschienen in: Child's Nervous System | Ausgabe 10/2007

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Abstract

Introduction

Although rare, pansynostoses are seen and treated by the craniofacial surgeon. To date, a single source that reviews these more severe forms of craniosynostosis is lacking in the literature.

Materials and methods

The present paper outlines and reviews the associations of both syndromic and nonsyndromic cases, potential mechanisms, and the anatomy involved with such forms of premature fusion of the cranial sutures.

Results

Pansynostosis is seen in a myriad of syndromes but can also be identified in nonsyndromic cases. Raised intracranial pressure is a concern in these patients.

Conclusions

Early recognition and treatment of patients with pansynostosis of the cranial sutures is important.
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Metadaten
Titel
Pansynostosis: a review
verfasst von
Jeffrey P. Blount
Robert G. Louis Jr.
R. Shane Tubbs
John H. Grant
Publikationsdatum
01.10.2007
Verlag
Springer-Verlag
Erschienen in
Child's Nervous System / Ausgabe 10/2007
Print ISSN: 0256-7040
Elektronische ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-007-0362-1

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