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Pediatric Rheumatology

Ausgabe 1/2020

Inhalt (89 Artikel)

Persistent osteoarticular pain in children: early clinical and laboratory findings suggestive of acute lymphoblastic leukemia (a multicenter case-control study of 147 patients)

  • Open Access
  • Research article

Mathilde Louvigné, Josué Rakotonjanahary, Laurence Goumy, Aude Tavenard, Jean-François Brasme, Fanny Rialland, André Baruchel, Marie-Françoise Auclerc, Véronique Despert, Marie Desgranges, Sylvie Jean, Albert Faye, Ulrich Meinzer, Mathie Lorrot, Chantal Job-Deslandre, Brigitte Bader-Meunier, Virginie Gandemer, Isabelle Pellier, Emilie De Carli, Stéphanie Proust, Coralie Mallebranche, Mylène Duplan, Chloé Henry, Liana Carausu, Sophie Haro, Fanny Falaque, Damien Bodet, Marianna Deparis, Caroline Thomas, Sara Weinhard, Marie-Laure Couec, Estelle Thébaud, Morgane Cleirec, Frédéric Millot, Laurence Blanc, Chrystelle Dupraz, Natacha Maledon, Jacinthe Bonneau, Céline Chappe, Sophie Taque, Fabienne Toutain, Sophie Pertuisel, Chloé Puiseux, Jeremie Gaudichon, Pascale Blouin, Marion Gillibert Yvert, Anne Jourdain, Charlotte Hucault, Jill Serre, Julien Lejeune

Tocilizumab modifies clinical and laboratory features of macrophage activation syndrome complicating systemic juvenile idiopathic arthritis

  • Open Access
  • Research article

Masaki Shimizu, Mao Mizuta, Nami Okamoto, Takahiro Yasumi, Naomi Iwata, Hiroaki Umebayashi, Yuka Okura, Noriko Kinjo, Tomohiro Kubota, Yasuo Nakagishi, Kenichi Nishimura, Mariko Mohri, Masato Yashiro, Junko Yasumura, Hiroyuki Wakiguchi, Masaaki Mori

Development and validation of the CAREGIVERS questionnaire: multi-assessing the impact of juvenile idiopathic arthritis on caregivers

  • Open Access
  • Research article

Marcia Daniela Torres-Made, Ingris Peláez-Ballestas, Fernando García-Rodríguez, Ana Victoria Villarreal-Treviño, Brenda de Jesús Fortuna-Reyna, Manuel Enrique de la O-Cavazos, Nadina Eugenia Rubio-Pérez

Pediatric chronic nonbacterial osteomyelitis of the mandible: Seattle Children’s hospital 22-patient experience

  • Open Access
  • Research article

Austin Gaal, Matthew L. Basiaga, Yongdong Zhao, Mark Egbert

Patient and physician discordance of global disease assessment in juvenile dermatomyositis: findings from the Childhood Arthritis & Rheumatology Research Alliance Legacy Registry

  • Open Access
  • Research article

Heather Tory, David Zurakowski, Susan Kim, L. Abramson, E. Anderson, M. Andrew, N. Battle, M. Becker, H. Benham, T. Beukelman, J. Birmingham, P. Blier, A. Brown, H. Brunner, A. Cabrera, D. Canter, D. Carlton, B. Caruso, L. Ceracchio, E. Chalom, J. Chang, P. Charpentier, K. Clark, J. Dean, F. Dedeoglu, B. Feldman, P. Ferguson, M. Fox, K. Francis, M. Gervasini, D. Goldsmith, G. Gorton, B. Gottlieb, T. Graham, T. Griffin, H. Grosbein, S. Guppy, H. Haftel, D. Helfrich, G. Higgins, A. Hillard, J. R. Hollister, J. Hsu, A. Hudgins, C. Hung, A. Huttenlocher, N. Ilowite, A. Imlay, L. Imundo, C. J. Inman, J. Jaqith, R. Jerath, L. Jung, P. Kahn, A. Kapedani, D. Kingsbury, K. Klein, M. Klein-Gitelman, A. Kunkel, S. Lapidus, S. Layburn, T. Lehman, C. Lindsley, M. Macgregor-Hannah, M. Malloy, C. Mawhorter, D. McCurdy, K. Mims, N. Moorthy, D. Morus, E. Muscal, M. Natter, J. Olson, K. O’Neil, K. Onel, M. Orlando, J. Palmquist, M. Phillips, L. Ponder, S. Prahalad, M. Punaro, D. Puplava, S. Quinn, A. Quintero, C. Rabinovich, A. Reed, C. Reed, S. Ringold, M. Riordan, S. Roberson, A. Robinson, J. Rossette, D. Rothman, D. Russo, N. Ruth, K. Schikler, A. Sestak, B. Shaham, Y. Sherman, M. Simmons, N. Singer, S. Spalding, H. Stapp, R. Syed, E. Thomas, K. Torok, D. Trejo, J. Tress, W. Upton, R. Vehe, E. von Scheven, L. Walters, J. Weiss, P. Weiss, N. Welnick, A. White, J. Woo, J. Wootton, A. Yalcindag, C. Zapp, L. Zemel, A. Zhu

The use of S100 proteins testing in juvenile idiopathic arthritis and autoinflammatory diseases in a pediatric clinical setting: a retrospective analysis

  • Open Access
  • Research article

Najla Aljaberi, Elena Tronconi, Grant Schulert, Alexei A. Grom, Daniel J. Lovell, Jennifer L. Huggins, Michael Henrickson, Hermine I. Brunner

Pregnancy outcomes and perinatal complications of Asian mothers with juvenile idiopathic arthritis – a case-control registry study

  • Open Access
  • Research article

Shang Jun Zhang-Jian, Huang-Yu Yang, Meng-Jun Chiu, I-Jun Chou, Chang-Fu Kuo, Jing-Long Huang, Kuo-Wei Yeh, Chao-Yi Wu

Quantitative analysis of facial asymmetry based on three-dimensional photography: a valuable indicator for asymmetrical temporomandibular joint affection in juvenile idiopathic arthritis patients?

  • Open Access
  • Research article

Joëlle M. Bernini, Christian J. Kellenberger, Martina Eichenberger, Theodore Eliades, Spyridon N. Papageorgiou, Raphael Patcas

Correction to: Physical activity and health-related quality of life in chronic non-bacterial osteomyelitis

  • Open Access
  • Correction

Julia Nentwich, Katharina Ruf, Hermann Girschick, Annette Holl-Wieden, Henner Morbach, Helge Hebestreit, Christine Hofmann

Pharmacological conditioning for juvenile idiopathic arthritis: a potential solution to reduce methotrexate intolerance

  • Open Access
  • Hypothesis

Rosanne M. Smits, Dieuwke S. Veldhuijzen, Henriet van Middendorp, Petra C. E. Hissink Muller, Wineke Armbrust, Elizabeth Legger, Nico M. Wulffraat, Andrea W. M. Evers

Children’s fear of needle injections: a qualitative study of training sessions for children with rheumatic diseases before home administration

  • Open Access
  • Research article

Kari Sørensen, Helge Skirbekk, Gunnvald Kvarstein, Hilde Wøien

Correction to: Proposal for a definition for response to treatment, inactive disease and damage for JIA associated uveitis based on the validation of a uveitis related JIA outcome measures from the Multinational Interdisciplinary Working Group for Uveitis in Childhood (MIWGUC)

  • Open Access
  • Correction

Ivan Foeldvari, Jens Klotsche, Gabriele Simonini, Clive Edelsten, Sheila T. Angeles-Han, Regitze Bangsgaard, Joke de Boer, Gabriele Brumm, Rosa Bou Torrent, Tamas Constantin, Cinzia DeLibero, Jesus Diaz, Valeria Maria Gerloni, Margarida Guedes, Arnd Heiligenhaus, Kaisu Kotaniemi, Sanna Leinonen, Kirsten Minden, Vasco Miranda, Elisabetta Miserocchi, Susan Nielsen, Martina Niewerth, Irene Pontikaki, Carmen Garcia de Vicuna, Carla Zilhao, Steven Yeh, Jordi Anton

Adolescent Sjogren’s syndrome presenting as psychosis: a case series

  • Open Access
  • Case Report

Erin K. Hammett, Cristina Fernandez-Carbonell, Courtney Crayne, Alexis Boneparth, Randy Q. Cron, Suhas M. Radhakrishna

Consensus protocols for the diagnosis and management of the hereditary autoinflammatory syndromes CAPS, TRAPS and MKD/HIDS: a German PRO-KIND initiative

  • Open Access
  • Research article

Sandra Hansmann, Elke Lainka, Gerd Horneff, Dirk Holzinger, Nikolaus Rieber, Annette F. Jansson, Angela Rösen-Wolff, Gabi Erbis, Martina Prelog, Juergen Brunner, Susanne M. Benseler, Jasmin B. Kuemmerle-Deschner

Correction to: Biomarkers associating endothelial dysregulation in pediatric-onset systemic lupus erythematous

  • Open Access
  • Correction

Wan-Fang Lee, Chao-Yi Wu, Huang-Yu Yang, Wen-I Lee, Li-Chen Chen, Liang-Shiou Ou, Jing-Long Huang

Maintenance of antibody response to diphtheria/tetanus vaccine in patients aged 2–5 years with polyarticular-course juvenile idiopathic arthritis receiving subcutaneous abatacept

  • Open Access
  • Short Report

Hermine I. Brunner, Nikolay Tzaribachev, Gabriel Vega Cornejo, Rik Joos, Elisabeth Gervais, Rolando Cimaz, Inmaculada Calvo Penadés, Rubén Cuttica, Thomas Lutz, Pierre Quartier, Yash Gandhi, Marleen Nys, Robert Wong, Alberto Martini, Daniel J. Lovell, Nicolino Ruperto, Jordi Anton, Graciela Espada, Bernard Lauwerys, Ingrid Louw, Kirsten Minden, Mahmood Moosa Ally, Riana Van Zyl, Diego Oscar Viola, Richard Mouy, Brigitte Bader-Meunier, Michaela Semeraro

Expert panel consensus recommendations for diagnosis and treatment of secondary osteoporosis in children

  • Open Access
  • Research article

Rocío Galindo-Zavala, Rosa Bou-Torrent, Berta Magallares-López, Concepción Mir-Perelló, Natalia Palmou-Fontana, Belén Sevilla-Pérez, Marta Medrano-San Ildefonso, Mª. Isabel González-Fernández, Almudena Román-Pascual, Paula Alcañiz-Rodríguez, Juan Carlos Nieto-Gonzalez, Mireia López-Corbeto, Jenaro Graña-Gil

Factors impacting referral of JIA patients to a tertiary level pediatric rheumatology center in North India: a retrospective cohort study

  • Open Access
  • Research article

Manjari Agarwal, Caroline Freychet, Sumidha Jain, Abhay Shivpuri, Anju Singh, Veronique Dinand, Sujata Sawhney

Patient factors associated with waiting time to pediatric rheumatologist consultation for patients with juvenile idiopathic arthritis

  • Open Access
  • Research article

Claire E. H. Barber, Cheryl Barnabe, Susanne Benseler, Ricky Chin, Nicole Johnson, Nadia Luca, Paivi Miettunen, Marinka Twilt, Dwaraka Veeramreddy, Natalie J. Shiff, Heinrike Schmeling

The elevated serum levels of calcineurin and nuclear factor of activated T-cells 1 in children with Kawasaki disease

  • Open Access
  • Research article

Yameng Sun, Jingjing Liu, Zhimin Geng, Yijing Tao, Fenglei Zheng, Ying Wang, Songling Fu, Wei Wang, Chunhong Xie, Yiying Zhang, Fangqi Gong

A case of rectal ulcers during aspirin therapy in acute Kawasaki disease

  • Open Access
  • Letter to the Editor

Yong Han, Chenmin Hu, Yanping Yu

Assessment of traditional and non-traditional risk factors for premature atherosclerosis in children with juvenile dermatomyositis and pediatric controls

  • Open Access
  • Research article

Dawn M. Wahezi, Emily J. Liebling, Jaeun Choi, Marija Dionizovik-Dimanovski, Qi Gao, Jillian Parekh

Importance of pediatric rheumatologists and transitional care for juvenile idiopathic arthritis-associated uveitis: a retrospective series of 9 cases

  • Open Access
  • Case Report

Susumu Yamazaki, Asami Shimbo, Yuko Akutsu, Hiroshi Takase, Tomohiro Morio, Masaaki Mori

Inpatient mortality in transition-aged youth with rheumatic disease: an analysis of the National Inpatient Sample

  • Open Access
  • Research article

Paul T. Jensen, Keumseok Koh, Rebecca E. Cash, Stacy P. Ardoin, Ayaz Hyder

Choroidal vascularity index as a biomarker of systemic inflammation in childhood Polyarteritis Nodosa and adenosine deaminase-2 deficiency

  • Open Access
  • Research article

Ata BAYTAROĞLU, Sibel KADAYIFÇILAR, Abdullah AĞIN, Özge DELİKTAŞ, Selcan DEMİR, Yelda BİLGİNER, Jale KARAKAYA, Seza ÖZEN, Bora ELDEM

Spectrum of paediatric rheumatic disorders at a tertiary hospital in Tanzania

  • Open Access
  • Research article

Francis F. Furia, Evance Godfrey, Naomi Mwamanenge, Peter Swai

Consensus treatment plans for periodic fever, aphthous stomatitis, pharyngitis and adenitis syndrome (PFAPA): a framework to evaluate treatment responses from the childhood arthritis and rheumatology research alliance (CARRA) PFAPA work group

  • Open Access
  • Research article

Gil Amarilyo, Deborah Rothman, Kalpana Manthiram, Kathryn M. Edwards, Suzanne C. Li, Gary S. Marshall, Cagri Yildirim-Toruner, Kathleen Haines, Polly J. Ferguson, Geraldina Lionetti, Julie Cherian, Yongdong Zhao, Patricia DeLaMora, Grant Syverson, Simona Nativ, Marinka Twilt, Ian C. Michelow, Yuriy Stepanovskiy, Akaluck Thatayatikom, Liora Harel, Shoghik Akoghlanian, Lori Tucker, Mariana Correia Marques, Hemalatha Srinivasalu, Evan J. Propst, Greg R. Licameli, Fatma Dedeoglu, Sivia Lapidus, Ronald Laxer, Lisa Imundo, Paul Tsoukas, Peter Wright, Kelly Brown, Rima Khasawneh, Rosie Scuccimarri, Evan Mulvihill, Meghan Aabo, Edwin Anderson, Leslie Abramson, Daniela Adelean, Danielle Dumez, Marla Guzman, Renee Pang, Ellen Go, Katalin Koranyi, Donald Goldsmith, Hanna Kim, Andrew Zeft, Rayfel Schnieder, Victoria Statler, Lauren Steele, Lori Broderick, Hal Hoffman, Sriharsha Cherukumilli Grevich, Elizabeth Chalom, Michal Cidon, Robert Sundel, Nadine Saad, Deborah McCurdy, Grant Schulert, Ali Yalcindag, Eric Yen, Sara Stern, Karen Durrant, Yonatan Butbul, Jonathan Hausmann

Experiences, perspectives and expectations of adolescents with juvenile idiopathic arthritis regarding future work participation; a qualitative study

  • Open Access
  • Research article

E. Charlotte van Gulik, Floris Verkuil, Anouk M. Barendregt, Dieneke Schonenberg-Meinema, Amara Nassar-Sheikh Rashid, Taco W. Kuijpers, J. Merlijn van den Berg, Jan L. Hoving

Treating juvenile idiopathic arthritis to target: what is the optimal target definition to reach all goals?

  • Open Access
  • Commentary

Casper G. Schoemaker, Joost F. Swart, Nico M. Wulffraat

COVID-19 and what pediatric rheumatologists should know: a review from a highly affected country

Francesco Licciardi, Teresa Giani, Letizia Baldini, Ennio Giulio Favalli, Roberto Caporali, Rolando Cimaz

Feasibility and acceptability of an innovative adherence intervention for young adults with childhood-onset systemic Lupus Erythematosus

  • Open Access
  • Research article

Onengiya Harry, Lori E. Crosby, Constance Mara, Tracy V. Ting, Jennifer L. Huggins, Avani C. Modi

Type 1 interferonopathy presenting as juvenile idiopathic arthritis with interstitial lung disease: report of a new phenotype

  • Open Access
  • Case Report

S. L. N. Clarke, L. Robertson, G. I. Rice, L. Seabra, T. N. Hilliard, Y. J. Crow, A. V. Ramanan

The association of MEFV gene mutations with the disease risk and severity of systemic juvenile idiopathic arthritis

  • Open Access
  • Research article

Linqing Zhong, Wei Wang, Ji Li, Mingsheng Ma, Lijuan Gou, Changyan Wang, Zhongxun Yu, Tiannan Zhang, Yanqing Dong, Qijiao Wei, Hongmei Song

Nephrological disorders and neurological involvement in pediatric primary Sjogren syndrome:a case report and review of literature

  • Open Access
  • Case Report

Jingya Zhao, Qin Chen, Yunyun Zhu, Meng Zhao, Jun Liu, Zhenzhong Zhang, Xiaoting Gong

Recurrent Henoch-Schönlein Purpura with bullous rash and pulmonary nodules

  • Open Access
  • Case Report

Christopher Zheng, Julie Childers, Egla Rabinovich, Kristina Nazareth-Pidgeon

Assessing the reporting quality of physical activity programs in randomized controlled trials for the management of juvenile idiopathic arthritis using three standardized assessment tools

  • Open Access
  • Research article

Teresa-Rose Kattackal, Sabrina Cavallo, Lucie Brosseau, Aditi Sivakumar, Michael J. Del Bel, Michelle Dorion, Erin Ueffing, Karine Toupin-April

Usefulness of magnetic resonance enterography in detecting signs of sacroiliitis in young patients with inflammatory bowel disease

  • Open Access
  • Research article

Teresa Giani, Azzurra Bernardini, Massimo Basile, Marco Di Maurizo, Anna Perrone, Sara Renzo, Viola Filistrucchi, Rolando Cimaz, Paolo Lionetti

Prevalence of co-existing autoimmune disease in juvenile idiopathic arthritis: a cross-sectional study

  • Open Access
  • Research article

Teresa A. Simon, Gowri Priya Harikrishnan, Hugh Kawabata, Sanket Singhal, Hermine I. Brunner, Daniel J. Lovell

Salivary gland ultrasound in the diagnostic workup of juvenile Sjögren’s syndrome and mixed connective tissue disease

  • Open Access
  • Research article

Manuela Krumrey-Langkammerer, Johannes-Peter Haas

Vitamin C deficiency mimicking inflammatory bone disease of the hand

  • Open Access
  • Case Report

Emily J. Liebling, Raymond W. Sze, Edward M. Behrens

C-type natriuretic peptide stimulates osteoblastic proliferation and collagen-X expression but suppresses fibroblast growth factor-23 expression in vitro

  • Open Access
  • Research article

Wei Xia Chen, Hui Hui Liu, Rui Xue Li, Goshgar Mammadov, Jing Jing Wang, Fei Fei Liu, Sama Samadli, Yang Fang Wu, Dong Dong Zhang, Huang Huang Luo, Peng Hu

Artificial intelligence for interpretation of segments of whole body MRI in CNO: pilot study comparing radiologists versus machine learning algorithm

  • Open Access
  • Research article

Chandrika S. Bhat, Mark Chopra, Savvas Andronikou, Suvadip Paul, Zach Wener-Fligner, Anna Merkoulovitch, Izidora Holjar-Erlic, Flavia Menegotto, Ewan Simpson, David Grier, Athimalaipet V. Ramanan

Effect of different doses of aspirin on the prognosis of Kawasaki disease

  • Open Access
  • Research article

Jinxin Wang, Huiqiao Chen, Hongying Shi, Xuting Zhang, Yiping Shao, Biyao Hang, Zhipeng Xu, Xing Rong, Maoping Chu, Huixian Qiu

Neonatal Kawasaki disease with multiple arterial aneurysms: a case report

  • Open Access
  • Case Report

Qu-ming Zhao, Xue-cun Liang, Lin Wu, Fang Liu

Failure of anti Interleukin-1 β monoclonal antibody in the treatment of recurrent pericarditis in two children

  • Open Access
  • Case Report

Sara Signa, Matteo D’Alessandro, Rita Consolini, Angela Miniaci, Marta Bustaffa, Chiara Longo, Maria A. Tosca, Martina Bizzi, Roberta Caorsi, Leonardo Oliveira Mendonça, Andrea Pession, Angelo Ravelli, Marco Gattorno

Image guided sacroiliac joint corticosteroid injections in children: an 18-year single-center retrospective study

  • Open Access
  • Research article

Racha Chamlati, Bairbre Connolly, Ronald Laxer, Jennifer Stimec, Jyoti Panwar, Shirley Tse, Prakash Muthusami, Joao Amaral, Michael Temple, Dimitri A. Parra

Adenosine deaminase 2 activity negatively correlates with age during childhood

  • Open Access
  • Research article

Sarah M. Bowers, Kristen M. Gibson, David A. Cabral, Kelly L. Brown

High prevalence of rare FBLIM1 gene variants in an Italian cohort of patients with Chronic Non-bacterial Osteomyelitis (CNO)

  • Open Access
  • Research article

Adamo Pio d’Adamo, Anna Monica Bianco, Giovanna Ferrara, Martina La Bianca, Antonella Insalaco, Alberto Tommasini, Manuela Pardeo, Marco Cattalini, Francesco La Torre, Martina Finetti, Clotilde Alizzi, Gabriele Simonini, Virginia Messia, Serena Pastore, Rolando Cimaz, Marco Gattorno, Andrea Taddio

Successful treatment of refractory hyperferritinemic syndromes with canakinumab: a report of two cases

  • Open Access
  • Case Report

Riccardo Papa, Valentina Natoli, Roberta Caorsi, Francesca Minoia, Marco Gattorno, Angelo Ravelli

Assessment and treatment of Down syndrome-associated arthritis: a survey of pediatric rheumatologists

  • Open Access
  • Research article

Anna Nicek, Nasreen Talib, Daniel Lovell, Chelsey Smith, Mara L. Becker, Jordan T. Jones

Subclinical cardiovascular risk signs in adults with juvenile idiopathic arthritis in sustained remission

  • Open Access
  • Research article

Inmaculada Concepción Aranda-Valera, Iván Arias de la Rosa, Rosa Roldán-Molina, María del Carmen Ábalos-Aguilera, Carmen Torres-Granados, Alejandra Patiño-Trives, María Luque-Tevar, Alejandro Ibáñez-Costa, Rocío Guzmán-Ruiz, María del Mar Malagón, Alejandro Escudero-Contreras, Chary López-Pedrera, Eduardo Collantes-Estévez, Nuria Barbarroja

The paediatric global musculoskeletal task force - ‘towards better MSK health for all’

  • Open Access
  • Commentary

Helen E. Foster, Christiaan Scott, Carl J. Tiderius, Matthew B. Dobbs

Neurological involvement in Kawasaki disease: a retrospective study

  • Open Access
  • Research article

Xiaoliang Liu, Kaiyu Zhou, Yimin Hua, Mei Wu, Lei Liu, Shuran Shao, Chuan Wang

A familial case of Kikuchi-Fujimoto disease in dizygotic twins

  • Open Access
  • Case Report

Ashfaque Quadir, Ken Peacock, Peter Hsu, Davinder Singh-Grewal, Stephen Alexander

Recurrent synovitis of hip and MEFV gene related arthritis in children

  • Open Access
  • Research article

Farhad Salehzadeh, Mehrdad Mirzarahimi

Kawasaki disease with a concomitant primary Epstein - Barr virus infection

  • Open Access
  • Case Report

Nataly Rosenfeld, Diana Tasher, Adi Ovadia, Shirly Abiri, Ilan Dalal

Reproductive health needs of adolescent and young adult women with pediatric rheumatic diseases

  • Open Access
  • Research article

Kristine Carandang, Veronica Mruk, Stacy P. Ardoin, Brittany Huynh, Megan E. B. Clowse, Elise D. Berlan, Cuoghi Edens

A case report of a novel compound heterozygous mutation in a Brazilian patient with deficiency of Interleukin-1 receptor antagonist (DIRA)

  • Open Access
  • Review

Leonardo Oliveira Mendonça, Alice Grossi, Francesco Caroli, Robson Aguiar de Oliveira, Jorge Kalil, Fabio Fernandes Morato Castro, Alessandra Pontillo, Isabella Ceccherini, Myrthes Anna Maragna Toledo Barros, Marco Gattorno

Juvenile Spondyloarthritis: focus on uveitis

  • Open Access
  • Short Report

Achille Marino, Pamela F. Weiss, Timothy G. Brandon, Melissa A. Lerman

Establishing an international awareness day for paediatric rheumatic diseases: reflections from the inaugural World Young Rheumatic Diseases (WORD) Day 2019

  • Open Access
  • Commentary

Eve M. D. Smith, Sammy Ainsworth, Michael W. Beresford, Veerle Buys, Wendy Costello, Yona Egert, Helen E. Foster, Lovro Lamot, Berent J. Prakken, Christiaan Scott, Simon R. Stones

A case of Myhre syndrome mimicking juvenile scleroderma

  • Open Access
  • Case Report

Barbara Jensen, Rebecca James, Ying Hong, Ebun Omoyinmi, Clarissa Pilkington, Neil J. Sebire, Kevin J. Howell, Paul A. Brogan, Despina Eleftheriou

Utility of the EULAR Sjögren syndrome disease activity index in Japanese children: a retrospective multicenter cohort study

  • Open Access
  • Research article

Naomi Iwata, Minako Tomiita, Ichiro Kobayashi, Yusaburo Inoue, Yukiko Nonaka, Nami Okamoto, Hiroaki Umebayashi, Ryoki Hara, Yasuhiko Ito, Yasunori Sato, Masaaki Mori

Bacterial infections in a pediatric cohort of primary and acquired complement deficiencies

  • Open Access
  • Research article

Taha Al-Shaikhly, Kristen Hayward, Matthew L. Basiaga, Eric J. Allenspach

Efficacy and safety of intraarticular corticosteroid injections in adolescents with juvenile idiopathic arthritis in the temporomandibular joint: a Norwegian 2-year prospective multicenter pilot study

  • Open Access
  • Research article

Paula Frid, Thomas A. Augdal, Tore A. Larheim, Josefine Halbig, Veronika Rypdal, Nils Thomas Songstad, Annika Rosén, Karin B. Tylleskär, Johanna Rykke Berstad, Berit Flatø, Peter Stoustrup, Karen Rosendahl, Eva Kirkhus, Ellen Nordal

Functional benefits of corticosteroid and IVIG combination therapy in a coronary artery endothelial cell model of Kawasaki disease

  • Open Access
  • Research article

Takashi Inoue, Shokei Murakami, Kenji Matsumoto, Akio Matsuda

The spectrum of pediatric amplified musculoskeletal pain syndrome

  • Open Access
  • Research article

David D. Sherry, Maitry Sonagra, Sabrina Gmuca

Determinants of disease activity change over time in Enthesitis related arthritis: effect of structured outcome monitoring and clinical decision support

  • Open Access
  • Research article

Francesca Tirelli, Rui Xiao, Timothy G. Brandon, Jon M. Burnham, Joyce C. Chang, Pamela F. Weiss

Heme oxygenase-1 deficiency presenting with interstitial lung disease and hemophagocytic flares

  • Open Access
  • Case Report

Alice S. Chau, Bonnie L. Cole, Jason S. Debley, Kabita Nanda, Aaron B. I. Rosen, Michael J. Bamshad, Deborah A. Nickerson, Troy R. Torgerson, Eric J. Allenspach

Joint injection practice variations in pediatric rheumatology – a global survey and call for action

  • Open Access
  • Research article

Anita Dhanrajani, Raju P. Khubchandani

Telemedicine in pediatric rheumatology: this is the time for the community to embrace a new way of clinical practice

Susan Shenoi, Kristen Hayward, Megan L. Curran, Elizabeth Kessler, Jay J. Mehta, Meredith P. Riebschleger, Helen E. Foster

Onset age is a risk factor for refractory pediatric IgA vasculitis: a retrospective cohort study

  • Open Access
  • Research article

Chun-Hua Liao, Melody Tsai, Yao-Hsu Yang, Bor-Luen Chiang, Li-Chieh Wang

Safety and immunogenicity of the quadrivalent human papillomavirus vaccine in patients with juvenile dermatomyositis: a real-world multicentre study

  • Open Access
  • Research article

Ingrid Herta Rotstein Grein, Natalia Balera Ferreira Pinto, Noortje Groot, Camila Bertini Martins, Aline Lobo, Nadia Emi Aikawa, Cassia Barbosa, Maria Teresa Terreri, Aline Coelho Moreira da Fraga, Sheila Knupp Feitosa de Oliveira, Flavio Sztajnbok, Luciana B. Paim Marques, Aline Garcia Islabão, Simone Appenzeller, Blanca Bica, Juliana de Oliveira Sato, Claudia Saad Magalhães, Virgínia Ferriani, Hella Pasmans, Rutger Schepp, Fiona van der Klis, Sytze de Roock, Nico Wulffraat, Gecilmara Salviato Pileggi

Longitudinal assessment of racial disparities in juvenile idiopathic arthritis disease activity in a treat-to-target intervention

  • Open Access
  • Research article

Joyce C. Chang, Rui Xiao, Jon M. Burnham, Pamela F. Weiss

Juvenile idiopathic arthritis fibroblast-like synoviocytes influence chondrocytes to alter BMP antagonist expression demonstrating an interaction between the two prominent cell types involved in endochondral bone formation

  • Open Access
  • Research article

Megan M. Simonds, Amanda R. Schlefman, Suzanne M. McCahan, Kathleen E. Sullivan, Carlos D. Rose, AnneMarie C. Brescia

Atrial thrombus as a complication of SLE and APS in an 8-year-old child

  • Open Access
  • Case Report

Hai-bo Yan, Yu-mei Li

Validation of novel patient-centred juvenile idiopathic arthritis-specific patient-reported outcome and experience measures (PROMs/PREMs)

  • Open Access
  • Research article

Laura E. Lunt, Stephanie Shoop-Worrall, Nicola Smith, Gavin Cleary, Janet McDonagh, Andrew D. Smith, Wendy Thomson, Flora McErlane

Use of PROMIS® to screen for depression in children with arthritis

  • Open Access
  • Research article

Yufan Yan, Karen L. Rychlik, Marc B. Rosenman, Michael L. Miller

Kompaktes Leitlinien-Wissen Pädiatrie (Link öffnet in neuem Fenster)

Mit medbee Pocketcards schnell und sicher entscheiden.
Leitlinien-Wissen kostenlos und immer griffbereit auf ihrem Desktop, Handy oder Tablet.

Neu im Fachgebiet Pädiatrie

KI-Chatbots bieten 24/7-Sprechstunde für Patienten

Medizinischen Rat von Chatbots auf der Basis sogenannter künstlicher Intelligenz haben laut Umfragen bereits knapp die Hälfte aller Erwachsenen schon einmal eingeholt. Welche Chancen und Risiken birgt das?

Mehr als ein Fünftel der Kleinkinder entwickelt eine funktionelle Obstipation

In einer schwedischen Geburtskohorte zeigte etwa jedes fünfte Kind in den ersten 30 Lebensmonaten eine funktionelle Obstipation. Die Studie liefert differenzierte Daten zu Stuhlfrequenz, -konsistenz, Risikofaktoren und Therapieverläufen und unterstreicht den Bedarf an langfristiger Betreuung.

Zu frühe Geburt – 10 IQ-Punkte weniger

Kommen Kinder zu früh oder mit sehr niedrigem Geburtsgewicht auf die Welt, hat dies oft kognitive Auswirkungen bis ins Erwachsenenalter: Der IQ bleibt niedriger, die Schulleistungen sind schlechter und der Förderbedarf ist höher als im Durchschnitt.

Dislozierte Radiusfraktur bei Kindern: Konservative Therapie im Aufwind!

Selbst stark dislozierte distale Radiusfrakturen heilen bei Kindern im Gipsverband offenbar ähnlich gut wie nach operativer Versorgung. Das legt eine randomisierte Studie aus Großbritannien nahe. Vorteile der konservativen Behandlung: weniger Komplikationen und deutlich geringere Kosten.

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Bildnachweise
Die Leitlinien für Ärztinnen und Ärzte, Vater recherchiert am Smartphone/© Elnur / stock.adobe.com (Symbolbild mit Fotomodell), Tastuntersuchung bei Kind/© Maria / stock.adobe.com (Symbolbild mit Fotomodell), Frühgeborenes/© manonallard / Getty Images / iStock (Symbolbild mit Fotomodell), Kind mit Gipsarm/© nycshooter / Getty Images / iStock (Symbolbild mit Fotomodell)