Ausgabe 1/2023
Inhalt (143 Artikel)
A virtual pediatric rheumatology teaching initiative for physicians in Somaliland
- Open Access
- Letter to the Editor
Muna Mahfud, Matthew Jones, Tim Fader, Emily Hause
Colchicine treatment can be discontinued in a selected group of pediatric FMF patients
- Open Access
- Research article
Keren Cohen, Shiri Spielman, Rotem Semo-Oz, Guy Bitansky, Maya Gerstein, Yonatan Yacobi, Asaf Vivante, Irit Tirosh
Treatment escalation patterns to start biologics in refractory moderate juvenile dermatomyositis among members of the Childhood Arthritis and Rheumatology Research Alliance
- Open Access
- Research article
Matthew A. Sherman, Hanna Kim, Katelyn Banschbach, Amanda Brown, Harry L. Gewanter, Bianca Lang, Megan Perron, Angela Byun Robinson, Jacob Spitznagle, Cory Stingl, Grant Syverson, Heather O. Tory, Charles H. Spencer, Stacey E. Tarvin
Effect of interleukin-1 antagonist on growth of children with colchicine resistant or intolerant FMF
- Open Access
- Research article
Shiran Pinchevski-Kadir, Maya Gerstein, Oren Pleniceanu, Yonatan Yacobi, Asaf Vivante, Ortal Erez Granat, Shiri Spielman, Rotem Semo Oz, Irit Tirosh
Multi-inflammatory syndrome in children (MIS-C) associated with COVID-19: a nursing perspective experience report from a high-income tertiary paediatric hospital context
- Open Access
- COVID-19
- Research article
Henrik Hjelmgren, Karin Andersson, Jessica Widegren, Erika Bergman, Anna Vermé, Karina Mördrup, Marcus Öhlander, Cecilia Bartholdson
An iceberg I can’t handle: a qualitative inquiry on perceptions towards paediatric rheumatology among healthcare workers in Kenya
- Open Access
- Research article
Angela Migowa, Sasha Bernatsky, Anthony Ngugi, Helen E. Foster, Peter Muriuki, Adelaide Lusambili, Stanley Luchters
Dry synovitis, a rare entity distinct from juvenile idiopathic arthritis
- Open Access
- Research article
Lien De Somer, Brigitte Bader-Meunier, Sylvain Breton, Sara Brachi, Carine Wouters, Francesco Zulian
A novel mutation in the proteoglycan 4 gene causing CACP syndrome: two sisters report
- Open Access
- Case Report
İlknur Bağrul, Serdar Ceylaner, Yasemin Tasci Yildiz, Serife Tuncez, Elif Arslanoglu Aydin, Esra Bağlan, Semanur Ozdel, Mehmet Bülbül
Pain-coping scale for children and their parents: a cross-sectional study in children with musculoskeletal pain
- Open Access
- Research article
Maria Backström, Hanna Vuorimaa, Maarit Tarkiainen, Eliisa Löyttyniemi, Liisa Kröger, Kristiina Aalto, Katariina Rebane, Kati Markula-Patjas, Merja Malin, Sirja Sard, Paula Keskitalo, Katja Korkatti, Minna-Maija Grönlund, Milja Möttönen, Heini Pohjankoski, Maiju Hietanen, Johanna Kärki, Paula Vähäsalo
Macrophage activation syndrome in children with Kikuchi-Fujimoto disease
- Open Access
- Research article
Zixuan Shen, Jiayun Ling, Xiaona Zhu, Jun Yang, Tingyan He
Childhood-onset primary Sjögren’s syndrome in a tertiary center in China: clinical features and outcome
- Open Access
- Research article
Yinv Gong, Haimei Liu, Guomin Li, Tao Zhang, Yifan Li, Wanzhen Guan, Qiaoqian Zeng, Qianying Lv, Xiaomei Zhang, Wen Yao, Yu Shi, Hong Xu, Li Sun
Correction: PSTPIP1-associated myeloid-related proteinaemia inflammatory (PAMI) syndrome; a case presenting as a perinatal event with early central nervous system involvement?
- Open Access
- Correction
Bethany Gillies Whiteside, Hannah Titheradge, Eslam Al-Abadi
Axial involvement in enthesitis-related arthritis: results from a single-center cohort
- Open Access
- Research article
Yanli Guo, Yuying Fang, Tonghao Zhang, Yuting Pan, Panpan Wang, Zhidan Fan, Haiguo Yu
Subtype frequency, demographic features, treatment and outcome of Juvenile Arthritis in one Centre in Abu Dhabi in the United Arab Emirates
- Open Access
- Research article
K. Khawaja, R. Kalas, N. Almasri
Identification of a variant in NLRP3 gene in a patient with Muckle-Wells syndrome: a case report and review of literature
- Open Access
- Case Report
Jia Liu, Ranran Zhang, Zhi Yi, Yi Lin, Hong Chang, Qiuye Zhang
IgG4 related pericardium and lung disease in pediatric patient complicated with fatal massive hemoptysis: a case report and review of literature
- Open Access
- Case Report
Moustafa Ali Saad, Hamdy Ahmed, Rasmia Elgohary, Hala Ibrahem El Gendy
Profiling the peripheral immune response to ex vivo TNF stimulation in untreated juvenile idiopathic arthritis using single cell RNA sequencing
- Open Access
- Research article
Kathleen J. Imbach, Nicole J. Treadway, Vaishali Prahalad, Astrid Kosters, Dalia Arafat, Meixue Duan, Talia Gergely, Lori A. Ponder, Shanmuganathan Chandrakasan, Eliver E. B. Ghosn, Sampath Prahalad, Greg Gibson
Strategic use of levofolinic acid for methotrexate-induced side effects in juvenile idiopathic arthritis: a prospective observational study
- Open Access
- Short Report
Giorgia Martini, Alessandra Meneghel, Michele Fastiggi, Filippo Dell’Apa, Fabio Vittadello, Francesco Zulian
Juvenile idiopathic arthritis patients with positive family history of autoimmune thyroid disease might benefit from serological screening: analysis of the international Pharmachild registry
- Open Access
- Research article
Joeri W. van Straalen, Laurie Baas, Gabriella Giancane, Lyudmila Grebenkina, Jurgen Brunner, Gabriel Vega-Cornejo, Vyacheslav G. Chasnyk, Liora Harel, Simone Appenzeller, Elisabeth Gervais, Sytze de Roock, Nico M. Wulffraat, Nicolino Ruperto, Joost F. Swart
Efficacy and safety of TNF inhibitors in the treatment of juvenile idiopathic arthritis: a systematic literature review
- Open Access
- Research article
Gerd Horneff, Kirsten Minden, Catherine Rolland, Ana C. Hernandez Daly, Cecilia Borlenghi, Nicolino Ruperto
Outcome of adalimumab monotherapy in paediatric non-infectious uveitis
- Open Access
- Research article
DA Al-Julandani, NK Bagri, N Tsang, S Clarke, A Upadhyay, C Guly, AV Ramanan
Maternal and infant outcomes of pregnancy associated with anti-SSA/RO antibodies: a systematic review and meta-analysis
- Open Access
- Research article
Xiangrui Sheng, Xiaohui Song, Yue Xiong, Tian Ren, Xin Chang, Jian Wu, Jing Cao, Tao Cheng, Mingjun Wang
A Chinese girl of Blau syndrome with renal arteritis and a literature review
- Open Access
- Review
Qiaoqian Zeng, Haimei Liu, Guomin Li, Yifan Li, Wanzhen Guan, Tao Zhang, Yinv Gong, Xiaomei Zhang, Qianying Lv, Bingbing Wu, Hong Xu, Li Sun
Individual and environmental determinants associated with longer times to access pediatric rheumatology centers for patients with juvenile idiopathic arthritis, a JIR cohort study
- Open Access
- Research article
Aurélie Chausset, Céline Lambert, Alexandre Belot, Etienne Merlin, Elvira Cannizzaro, Isabelle Kone-Paut, Claire Ballot, Valérie Devauchelle, Sylvaine Poignant, Raffaella Carlomagno, Anne Lohse, Catherine Barbier, Véronique Despert, Aurélia Carbasse, Laetitia Sparsa, Eva Adank, Federica Vanoni, Héloise Reumaux, Pascal Pillet, Daniela Kaiser, Michael Hofer, Caroline Freychet, Anne-Marie Schott
Clinical phenotypes and prognosis of cytomegalovirus infection in the pediatric systemic lupus erythematosus: a longitudinal analysis
- Open Access
- Research article
Tianyu Zhang, Zhongxun Yu, Sihao Gao, Yuelun Zhang, Changyan Wang, Shan Jian, Lin Wang, Lijuan Gou, Ji Li, Mingsheng Ma, Hongmei Song
Impaired cardiorespiratory and neuromuscular fitness in children and adolescents with juvenile idiopathic arthritis: a cross-sectional case–control study in the era of biologic drug therapies
- Open Access
- Research article
Kati Räsänen, Kati Markula-Patjas, Saija Kantanen, Kalle Sipilä, Timo A. Lakka, Pekka Arikoski, Eija Piippo-Savolainen
Etanercept for patients with juvenile idiopathic arthritis: drug levels and influence of concomitant methotrexate: observational study
- Open Access
- Research article
Tiina Levälampi, Johanna Kärki, Katariina Rebane, Paula Vähäsalo, Merja Malin, Liisa Kröger, Minna-Maija Grönlund, Maria Backström, Heini Pohjankoski, Hannu Kautiainen, Sakari Jokiranta, Kristiina Aalto
Risk factors for subsequent lupus nephritis in patients with juvenile-onset systemic lupus erythematosus: a retrospective cohort study
- Open Access
- Research article
Tzu-Chuan Hsu, Yao-Hsu Yang, Li-Chieh Wang, Jyh-Hong Lee, Hsin-Hui Yu, Yu-Tsan Lin, Ya-Chiao Hu, Bor-Luen Chiang
The effect of TNF treatment uptake on incident hospital admission in Western Australia
- Open Access
- Research article
Erin Kelty, Ebony Quintrell, David B. Preen, Prue Manners, Johannes Nossent
Unexpectedly high incidence of Kawasaki Disease in a Canadian Atlantic Province- an 11-year retrospective descriptive study
- Open Access
- Research article
Abdulrahman Alkanhal, Joseph Saunders, Fajer Altammar, Adam M. Huber, Andrew Lynk, Alison MacLeod, Oliva Ortiz-Alvarez, Meighan Adams, Suzanne Ramsey, Elizabeth Stringer, Andrew Warren, Bianca Lang
Adherence, helpfulness and barriers to treatment in juvenile idiopathic arthritis – data from a German Inception cohort
- Open Access
- Research article
Sabine Kirchner, Jens Klotsche, Ina Liedmann, Martina Niewerth, Debbie Feldman, Frank Dressler, Ivan Foeldvari, Dirk Foell, Johannes-Peter Haas, Gerd Horneff, Anton Hospach, Tilmann Kallinich, J. B. Kuemmerle-Deschner, Kirsten Moenkemoeller, Frank Weller-Heinemann, Daniel Windschall, Kirsten Minden, Claudia Sengler
The effect of etanercept therapy on adrenal steroid metabolism in juvenile idiopathic arthritis: a steroid metabolomics approach
- Open Access
- Research article
Yonatan Butbul Aviel, Ariel Keinan, Michaela F. Hartmann, Stefan A. Wudy, Dov Tiosano
Distinct phenotypes of multisystem inflammatory syndrome in children: a cohort study
- Open Access
- Research article
Thomas Renson, Nils D. Forkert, Kimberly Amador, Paivi Miettunen, Simon J. Parsons, Muhammed Dhalla, Nicole A. Johnson, Nadia Luca, Heinrike Schmeling, Rebeka Stevenson, Marinka Twilt, Lorraine Hamiwka, Susanne Benseler
Retropharyngeal abscess-like as an atypical presentation of Kawasaki disease: a case report and literature review
- Open Access
- Review
Rim Kasem Ali Sliman, Joris M. van Montfrans, Najwan Nassrallah, Mohamad Hamad Saied
The feasibility of existing JADAS10 cut-off values in clinical practice: a study of data from The Finnish Rheumatology Quality Register
- Open Access
- Research article
M. Backström, H. Salo, J. Kärki, K. Aalto, K. Rebane, T. Levälampi, M-M. Grönlund, L. Kröger, H. Pohjankoski, M. Hietanen, K. Korkatti, L. Kuusalo, V. Rantalaiho, J. Huhtakangas, H. Relas, T. Pääkkö, E. Löyttyniemi, T. Sokka-Isler, P. Vähäsalo
Why so low? An unusual case of myositis in a child
- Open Access
- Case Report
Meagan E. Chriswell, Robert C. Fuhlbrigge, Mark A. Lovell, Matthew Monson, Jessica L. Bloom
Evaluating key performance indicators of the process of care in juvenile idiopathic arthritis
- Open Access
- Research article
Sarah M. Cooper, Gillian R. Currie, Seija Kromm, Marinka Twilt, Deborah A. Marshall
Efficacy and safety of baricitinib in Japanese patients with autoinflammatory type I interferonopathies (NNS/CANDLE, SAVI, And AGS)
- Open Access
- Research article
Nobuo Kanazawa, Taeko Ishii, Yasushi Takita, Atsushi Nishikawa, Ryuta Nishikomori
Barriers to care in juvenile localized and systemic scleroderma: an exploratory survey study of caregivers’ perspectives
- Open Access
- Research article
Leigh A. Stubbs, Andrew M. Ferry, Danielle Guffey, Christina Loccke, Erin Moriarty Wade, Pamela Pour, Kaveh Ardalan, Peter Chira, Ingrid M. Ganske, Daniel Glaser, Gloria Higgins, Nadia Luca, Katharine F. Moore, Vidya Sivaraman, Katie Stewart, Natalia Vasquez-Canizares, Raegan D. Hunt, Renata S. Maricevich, Kathryn S. Torok, Suzanne C. Li
Antibodies to histone in the pediatric population: a retrospective chart review
- Open Access
- Research article
C. Matt Justice, Terry L. Moore
Paediatric autoimmune diseases with ELANE mutations associated with neutropenia
- Open Access
- Research article
Dan Zhang, Gaixiu Su, Sheng Hao, Jianming Lai, Shunqiao Feng
Clinical characteristics and risk factors of coronary artery lesions in chinese pediatric Takayasu arteritis patients: a retrospective study
- Open Access
- Research article
Yingjie Xu, Lingfeng Luo, Gaixiu Su, Jia Zhu, Min Kang, Dan Zhang, Jianming Lai, Xiaohui Li
Clinical features, treatment, and outcomes of celiac-associated arthritis: a retrospective cohort study
- Open Access
- Research article
Ana Luiza Altaffer, Pamela Weiss
Natural autoimmunity in oligoarticular juvenile idiopathic arthritis
- Open Access
- Research article
Elena Tsitsami, Ioannis Sarrigeorgiou, Maria Tsinti, Erasmia C. Rouka, Sotirios G. Zarogiannis, Peggy Lymberi
High prevalence of sacroiliitis and early structural changes in the sacroiliac joint in children with enthesitis-related arthritis: findings from a tertiary centre in Hong Kong
- Open Access
- Research article
Oi Man Chan, Billy Ming-Hei Lai, Agnes Sze-Yin Leung, Ting Fan Leung, Assunta Chi-Hang Ho
Disease relapse rate in children with autoimmune rheumatic diseases after COVID-19 infection and vaccination
- Open Access
- Research article
Tjaša Šinkovec Savšek, Mojca Zajc Avramovič, Tadej Avčin, Miša Korva, Tatjana Avšič Županc, Nataša Toplak
Aquaporin-4 IgG antibodies: predictors of positivity and their relationship with neuropsychiatric disorders and white matter lesions in Juvenile systemic lupus erythematosus
- Open Access
- Research article
Yasmeen Shaaban, Hala EL-Marsafawy, Reham M El-Farahaty, Sherine El-Ziny, Ahmed M EL-Refaey
Touraine-Solente-Gole syndrome: pathogenic variant in SLCO2A1 presented with polyarthralgia and digital clubbing
- Open Access
- Case Report
Rafaela Nicolau, Tiago Beirão, Francisca Guimarães, Francisca Aguiar, Sara Ganhão, Mariana Rodrigues, Ana Grangeia, Iva Brito
Serum levels of soluble urokinase plasminogen activator receptor in juvenile idiopathic arthritis: a single-center Swedish case-control study
- Open Access
- Research article
Per Lewander, Lina Wirestam, Charlotte Dahle, Jonas Wetterö, Christopher Sjöwall
Differences between leukemic arthritis and juvenile idiopathic arthritis
- Open Access
- Research article
Alfonso Ragnar Torres Jimenez, Eunice Solis Vallejo, Adriana Ivonne Cespedes Cruz, Julia Veronica Ramirez Miramontes, Guadalupe del Consuelo Cortina Olvera, Alejandra Velazquez Cruz, Berenice Sanchez Jara
Increasing access to psychological services within pediatric rheumatology care
- Open Access
- Research article
Alana Goldstein-Leever, Christine Bearer, Vidya Sivaraman, Shoghik Akoghlanian, James Gallup, Stacy Ardoin
HLA-B*27 is associated with CNO in a European cohort
- Open Access
- Research article
Daire O’Leary, Dalila Ali Al Julandani, Muhammad Zia, Jens Klotsche, Kirsten Minden, Marion Roderick, Athimalaipet V. Ramanan, Orla G. Killeen, Anthony G. Wilson
MicroRNA-27a-3p enhances the inflammatory phenotype of Juvenile Idiopathic Arthritis fibroblast-like synoviocytes
- Open Access
- Research article
Claire H. Bullock, Sarah M. McAlpine, Sarah E. Roberts, Beata Derfalvi
Paediatric Cogan´s syndrome - review of literature, case report and practical approach to diagnosis and management
- Open Access
- Review
Kristina Rücklová, Thekla von Kalle, Assen Koitschev, Katrin Gekeler, Miriam Scheltdorf, Anita Heinkele, Friederike Blankenburg, Ina Kötter, Anton Hospach
A case series of ten plus one deficiency of adenosine deaminase 2 (DADA2) patients in Iran
- Open Access
- Case Report
Kosar Asna Ashari, Nahid Aslani, Nima Parvaneh, Raheleh Assari, Morteza Heidari, Mohammadreza Fathi, Fatemeh Tahghighi Sharabian, Alireza Ronagh, Mohammad Shahrooei, Alireza Moafi, Nima Rezaei, Vahid Ziaee
Encouraging visual outcomes in children with idiopathic and JIA associated uveitis: a population-based study
- Open Access
- Research article
Mira Siiskonen, Iida Hirn, Roosa Pesälä, Pasi Ohtonen, Nina Hautala
A systematic review of the psychosocial factors associated with pain in children with juvenile idiopathic arthritis
- Open Access
- Research article
Yvonne N. Brandelli, Christine T. Chambers, Sean P. Mackinnon, Jennifer A. Parker, Adam M. Huber, Jennifer N. Stinson, Emily M. Wildeboer, Jennifer P. Wilson, Olivia Piccolo
Bone mineral density in egyptian children with juvenile idiopathic arthritis: possible correlation to serum RANKL / osteoprotegerin (OPG) ratio and OPG gene polymorphisms
- Open Access
- Research article
Riham Eid, Maha Abdelsalam, Aya Ahmed Fathy, Hadil M. Abolenein, Eman Bakr Elmarghany, Aya Ahmed El-Hanafy, Nashwa Hamdy, Dina Salama Abd-Elmagid, Nermeen A. Niazy, Dina M. Abd-El Ghaffar
Knee acoustic emissions as a noninvasive biomarker of articular health in patients with juvenile idiopathic arthritis: a clinical validation in an extended study population
- Open Access
- Short Report
Quentin Goossens, Miguel Locsin, Sevda Gharehbaghi, Priya Brito, Emily Moise, Lori A Ponder, Omer T Inan, Sampath Prahalad
ANCA-negative eosinophilic granulomatosis with polyangiitis in a girl misdiagnosed as asthma and pulmonary tuberculosis
- Open Access
- Letter to the Editor
Fang Yang, Jiwei Zhao, Jieying Wang, Jiangrong Liao, Jinlin Liu, Yanxia Chen
A multi-site pilot randomized clinical trial of the Treatment and Education Approach for Childhood-onset Lupus (TEACH) program: study design and COVID-19 adaptations
- Open Access
- Research article
Natoshia R. Cunningham, Alaina Miller, Samantha L. Ely, Mallet R. Reid, Ashley Danguecan, Sarah I. Mossad, Luana Flores Pereira, Khalid Abulaban, Elizabeth Kessler, Natalie Rosenwasser, Kabita Nanda, Tamar Rubinstein, Mathew Reeves, Sara Ahola Kohut, Jennifer Stinson, Tala El Tal, Deborah M. Levy, Linda Hiraki, Emily A. Smitherman, Andrea M. Knight
Correction to: Touraine-Solente-Gole syndrome: pathogenic variant in SLCO2A1 presented with polyarthralgia and digital clubbing
- Open Access
- Correction
Rafaela Nicolau, Tiago Beirão, Francisca Guimarães, Francisca Aguiar, Sara Ganhão, Mariana Rodrigues, Ana Grangeia, Iva Brito
Currently recommended skin scores correlate highly in the assessment of patients with Juvenile Dermatomyositis (JDM)
- Open Access
- Research article
Alexander Gebreamlak, Katherine M. Sawicka, Rose Garrett, Y. Ingrid Goh, Kayla M. Baker, Brian M. Feldman
Kawasaki disease (KD) and multisystem inflammatory syndrome in children (MIS-C) in a Middle Eastern patient cohort
- Open Access
- Research article
Lemis Yavuz, Sarmad AlHamdani, Samah Alasrawi, Deena Wafadari, Ali Al-Fraihat, Marwa A. Bebars, Jaidev Nath, Diego Arango, Marco Pallavidino, Ruchi Jain, Sinan Yavuz, Mohamed AlAwadhi, Abdulla Alkhayat, Ahmad Abou Tayoun, Walid Mohammad Abuhammour
Priorities in Chronic nonbacterial osteomyelitis (CNO) – results from an international survey and roundtable discussions
- Open Access
- Research article
M. Mohanna, E. Roberts, L. Whitty, J. F. Gritzfeld, C. E. Pain, H. J. Girschick, J. Preston, M. Hadjittofi, C. Anderson, P. J. Ferguson, A. Theos, C. M. Hedrich
Childhood-Onset ANCA- Associated Vasculitis: single center experience from Central California
- Open Access
- Research article
Deepika Singh, Sukesh Sukumaran
Resilience and its associations in children with Systemic Lupus Erythematosus and Juvenile Idiopathic Arthritis
- Open Access
- Short Report
Rebecca Trachtman, Julie Samuels, Emma Wojtal, Brian M Feldman
Disability and disease-related damage in Thai children and adolescents with juvenile idiopathic arthritis
- Open Access
- Research article
Sirikarn Tangcheewinsirikul, Maynart Sukharomana, Sirirat Charuvanij
Withdrawing biologics in non-systemic JIA: what matters to pediatric rheumatologists?
- Open Access
- Research article
Janine A. van Til, Michelle M. A. Kip, Ellen J. H. Schatorjé, Gillian Currie, Marinka Twilt, Susanne M. Benseler, Joost F. Swart, Sebastiaan J. Vastert, Nico Wulffraat, Rae S. M. Yeung, C. G. M. (Karin) Groothuis-Oudshoorn, Sanne Warta, Deborah A. Marshall, Maarten J. IJzerman
The successes and challenges of harmonising juvenile idiopathic arthritis (JIA) datasets to create a large-scale JIA data resource
- Open Access
- Research article
Saskia Lawson-Tovey, Samantha Louise Smith, Nophar Geifman, Stephanie Shoop-Worrall, Sandra Ng, Michael R. Barnes, Lucy R. Wedderburn, Kimme L. Hyrich, Melissa Kartawinata, Zoe Wanstall, Bethany R. Jebson, Alyssia McNeece, Elizabeth Ralph, Vasiliki Alexiou, Fatjon Dekaj, Aline Kimonyo, Fatema Merali, Emma Sumner, Emily Robinson, Freya L. Feilding, Andrew Dick, Michael W. Beresford, Emil Carlsson, Joanna Fairlie, Jenna F. Gritzfeld, Athimalaipet Ramanan, Teresa Duerr, Stephen Eyre, Soumya Raychaudhuri, Andrew Morris, Annie Yarwood, Samantha Smith, John Bowes, Paul Martin, Melissa Tordoff, Michael Stadler, Wendy Thomson, Damian Tarasek, Chris Wallace, Wei-Yu Lin, Sarah Clarke, Toby Kent, Thierry Sornasse, Daniela Dastros-Pitei, Sumanta Mukherjee, Jacqui Roberts, Rami Kallala, Helen Neale, John Ioannou, Hussein Al-Mossawi
Immunodeficiency due to a novel variant in PIK3CD: a case report
- Open Access
- Case Report
Niloofar Shashaani, Zahra Chavoshzadeh, Leila Ghasemi, Shabnam Hajiani Ghotbabadi, Sara Shiari, Samin Sharafian, Reza Shiari
How common is remission in rheumatoid factor-positive juvenile idiopathic arthritis patients? The multicenter Pediatric Rheumatology Academy (PeRA) research group experience
- Open Access
- Research article
Semanur Ozdel, Hafize Emine Sönmez, Şengül Çağlayan, Özlem Akgün, Tuncay Aydın, Özge Baba, İlknur Bağrul, Gülçin Otar Yener, Kübra Öztürk, Ferhat Demir, Deniz Gezgin Yıldırım, Şerife Gül Karadağ, Esra Bağlan, Mustafa Çakan, Mukaddes Kalyoncu, Balahan Bora Makay, Şevket Erbil Ünsal, Sevcan Bakkaloğlu, Mehmet Bülbül, Betül Sözeri, Nuray Aktay Ayaz
Meningococcal ACWY conjugate vaccine immunogenicity in adolescents with primary or secondary immune deficiencies, a prospective observational cohort study
- Open Access
- Short Report
Milou Ohm, Joeri W van Straalen, Gerrie de Joode-Smink, Joris van Montfrans, Marije Bartels, Joanne G van Wildenbeest, Caroline A Lindemans, Roos AW Wennink, Joke H de Boer, Elisabeth AM Sanders, Frans M Verduyn-Lunel, Guy AM Berbers, Nico M Wulffraat, Marc H.A. Jansen
“I’d like more options!”: Interviews to explore young people and family decision-making needs for pain management in juvenile idiopathic arthritis
- Open Access
- Research article
Karine Toupin-April, Isabelle Gaboury, Laurie Proulx, Adam M. Huber, Ciarán M. Duffy, Esi M. Morgan, Linda C. Li, Elizabeth Stringer, Mark Connelly, Jennifer E. Weiss, Michele Gibbon, Hannah Sachs, Aditi Sivakumar, Alexandra Sirois, Emily Sirotich, Natasha Trehan, Naomi Abrahams, Janice S. Cohen, Sabrina Cavallo, Tania El Hindi, Marco Ragusa, France Légaré, William B. Brinkman, Paul R. Fortin, Simon Décary, Rebecca Lee, Sabrina Gmuca, Gail Paterson, Peter Tugwell, Jennifer N. Stinson
Identifying circRNA-associated-ceRNA networks in juvenile spondyloarthropathies patients
- Open Access
- Research article
Wei Qijiao, Zhang Tao, Liu Haimei, Li Guomin, Sun Li
Clinical outcomes and safety of anakinra in the treatment of multisystem inflammatory syndrome in children: a single center observational study
- Open Access
- Research article
Brian L.P. Dizon, Christopher Redmond, Emily C. Gotschlich, Sangeeta Sule, Tova Ronis, Kathleen M. Vazzana, Matthew A. Sherman, Rachael Connor, Abigail Bosk, Niti Dham, Ashraf S. Harahsheh, Elizabeth Wells, Roberta DeBiasi, Hemalatha Srinivasalu
C1-C2 subluxation in enthesitis-related arthritis: two case reports and literature review of ten cases
- Open Access
- Case Report
Wing Hin Stanford Siu, Chao-Jan Wang, Chieh-Tsai Wu, Chao-Yi Wu, Liang-Shiou Ou
Whole-exome sequencing analysis identifies novel variants associated with Kawasaki disease susceptibility
- Open Access
- Research article
Xing Zhang, Ying Sun, Lijuan Meng, Caixia Ye, Huifeng Han, Tiesong Zhang, Yue Feng, Jianxiao Li, Lifen Duan, Yanfei Chen
The protective effect of COVID-19 vaccines on developing multisystem inflammatory syndrome in children (MIS-C): a systematic literature review and meta-analysis
- Open Access
- Review
Mohamad Hamad Saied, Laura van der Griend, Joeri W van Straalen, Nico M. Wulffraat, Sebastiaan Vastert, Marc H A Jansen
Monoarticular juvenile idiopathic arthritis as a distinct clinical entity A proof-of-concept study
- Open Access
- Research article
Francesco Zulian, Beatrice Pierobon, Maria Elisabetta Zannin, Caterina Politi, Fabio Vittadello, Alessandra Meneghel, Francesca Tirelli, Giorgia Martini
Impact of SARS-CoV-2 on the clinical presentation of juvenile idiopathic inflammatory myopathies
- Open Access
- Research article
Jessica Perfetto, Donna A. Yoo, Carolina Y. Tamashiro, Megan M. Perron, Natalia Vasquez-Canizares, Dawn M. Wahezi
Long-term efficacy of sialendoscopy in treating childhood Sjögren’s disease with chronological monitoring by salivary gland ultrasonography: A novel approach
- Open Access
- Case Report
Kristin Drew, René Kronlage, Seunghee Cha, Akaluck Thatayatikom, Thomas Schrepfer
A novel PRKDC mutation caused B lymphocytes V(D)J rearrangement disorder in the SLE-DAH like symptoms patient
- Open Access
- Case Report
Hongwei Li, Yawen Zhang, Biyun Zhang, Dehui Chen
A case series on recurrent and persisting IgA vasculitis (Henoch Schonlein purpura) in children
- Open Access
- Research article
Julien Marro, Chloe Williams, Clare E. Pain, Louise Oni
Elevated serum IFN-γand IFN-γ/IL-6 ratio in Kikuchi-Fujimoto disease
- Open Access
- Research article
Tingyan He, Zixuan Shen, Jiayun Ling, Xiaona Zhu, Jun Yang
Pediatric-onset limited ANCA-associated vasculitis arising during pre-existing chronic recurrent multifocal osteomyelitis
- Open Access
- Case Report
Esraa Eloseily, Michael Henrickson
Significant pain decrease in children with non-systemic Juvenile Idiopathic Arthritis treated to target: results over 24 months of follow up
- Open Access
- Research article
Katinka Spekking, Janneke Anink, Piroska de Boer, Sytske Anne Bergstra, J. Merlijn van den Berg, Dieneke Schonenberg-Meinema, Lisette W. A. van Suijlekom-Smit, Marion A. J. van Rossum, Yvonne Koopman-Keemink, Rebecca ten Cate, Cornelia F. Allaart, Daniëlle M. C. Brinkman, Petra C. E. Hissink Muller
Successful experience of tofacitinib treatment in patients with Fibrodysplasia Ossificans Progressiva
- Open Access
- Research article
Irina P. Nikishina, Svetlana V. Arsenyeva, Valeria G. Matkava, Alia N. Arefieva, Mariya I. Kaleda, Alexandr V. Smirnov, Leonid M. Blank, Mikhail M. Kostik
Extreme Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis (PFAPA): a discrete group of patients
- Open Access
- Research article
Mor Broide, Yoel Levinsky, Rotem Tal, Liora Harel, Shoval Shoham, Sabreen Abu Ahmad, Yonatan Butbul Aviel, Gil Amarilyo
Disease characteristics of HLA-B27 positive and negative finnish patients with juvenile idiopathic arthritis - results of the 18-year cohort follow-up study
- Open Access
- Research article
Suvi Oili Orvokki Peltoniemi, Mia Glerup, Pekka Lahdenne, Kari K Eklund, Kristiina Aalto
Survey of adolescents’ needs and parents’ views on sexual health in juvenile idiopathic arthritis
- Open Access
- Research article
Carine Savel, Aurélie Chausset, Pauline Berland, Candy Guiguet-Auclair, Laura Cabane, Bruno Fautrel, Philippe Gaudin, Pascale Guillot, Gilles Hayem, Delphine Lafarge, Etienne Merlin, Nadine Pezière, Christelle Sordet, Sonia Trope, Anne Tournadre, Sandrine Malochet, Jean-David Cohen
Disease evolution in systemic juvenile idiopathic arthritis: an international, observational cohort study through JIRcohort
- Open Access
- Research article
M. Wallimann, K. Bouayed, E. Cannizzaro, D. Kaiser, A. Belot, E. Merlin, S. Poignant, C. Wouters, F. Hofer, T. Saurenmann, A. Koryllou, R. Carlomagno, M. Mejbri, M. Hofer, K. Theodoropoulou
Panniculitis with late onset enthesitis-related arthritis: a case report
- Open Access
- Case Report
Wenxiu Mo, Fei Sun, Tongxin Han, Huawei Mao
Childhood-onset rheumatoid arthritis at a tertiary hospital in Senegal, West Africa
- Open Access
- Research article
Mounib M. Sabounji, Hilaire Lissimo, Amina Deme
Subcutaneous tocilizumab in the management of non-infectious uveitis in children: a brief report
- Open Access
- Research article
Francesca Burlo, Cristina Tumminelli, Serena Pastore, Gabriele Stocco, Debora Curci, Marianna Lucafò, Alberto Tommasini, Andrea Taddio
The impact of the COVID-19 pandemic on patients with juvenile idiopathic inflammatory myopathies
- Open Access
- Research article
Dawn M. Wahezi, Dominique Jerome, Evin Rothschild, Belina Yi, Jeffrey Dvergsten, Stacey Tarvin, Susan Kim, Tamar Rubinstein
A case of neonatal sweet syndrome associated with mevalonate kinase deficiency
- Open Access
- Case Report
Margaret Irwin, Veeraya K. Tanawattanacharoen, Amy Turner, Mary Beth F. Son, Rebecca C. Hale, Craig D. Platt, Juan Putra, Birgitta A.R. Schmidt, Mollie G. Wasserman
Predictors of persisting pain in children with Juvenile Idiopathic Arthritis: a case control study nested in the ReACCh-Out cohort
- Open Access
- Research article
Tara McGrath, Jaime Guzman, Lori Tucker, Natalie J. Shiff, Maryna Yaskina, Susan Tupper, Dax G. Rumsey, Susanne Benseler, Roberta Berard, Gilles Boire, Roxana Bolaria, David Cabral, Bonnie Cameron, Sarah Campillo, Mercedes Chan, Gaëlle Chédeville, Anne-Laure Chetaille, Paul Dancey, Jean Dorval, Ciarán Duffy, Janet Ellsworth, Brian Feldman, Debbie Feldman, Katherine Gross, Ellie Haddad, Kristin Houghton, Adam Huber, Nicole Johnson, Roman Jurencak, Bianca Lang, Maggie Larché, Ronald Laxer, Claire LeBlanc, Deborah Levy, Nadia Luca, Paivi Miettunen, Kimberly Morishita, Kiem Oen, Ross Petty, Suzanne Ramsey, Alan Rosenberg, Johannes Roth, Claire Saint-Cyr, Heinrike Schmeling, Rayfel Schneider, Earl Silverman, Lynn Spiegel, Elizabeth Stringer, Rosie Scuccimarri, Shirley Tse, Stuart Turvey, Karen Watanabe Duffy, Rae Yeung
Screening utility and acceptability of the Kiswahili-pGALS (paediatric Gait, Arms, Legs, Spine) at a tertiary referral hospital in Kenya-A diagnostic accuracy study
- Open Access
- Research article
Jacqueline E. Kawishe, Anthony Ngugi, Stanley Luchters, Helen Foster, Angela Migowa
Rapid and sustained response to JAK inhibition in a child with severe MDA5 + juvenile dermatomyositis
- Open Access
- Case Report
Timmy Strauss, Claudia Günther, Anja Schnabel, Christine Wolf, Gabriele Hahn, Min Ae Lee-Kirsch, Normi Brück
Structural ultrasound of joints and tendons in healthy children: development of normative data
- Open Access
- Research article
Ruth Wittoek, Céline Decock, Nele Dewaele, Lara Arnold, Pieter Baeyens, Ignace De Schrijver, Lisa Pardaens, Ioannis Raftakis, Thomas Renson, Charline Rinkin, Alexander D. J. Thooft, Tine Vanhaverbeke, Caroline Verbist
Macrophage activation syndrome in juvenile dermatomyositis: a case report and a comprehensive review of the literature
- Open Access
- Review
Yong Chang, Xueyan Shan, Yongpeng Ge
Biologic switching patterns among children with non-systemic juvenile idiopathic arthritis
- Open Access
- Research article
Mia Lindegaard Pedersen, Amalie Neve-Græsbøll, Troels Herlin, Mia Glerup
Treat-to-target strategies for the management of familial Mediterranean Fever in children
- Open Access
- Research article
Lisa Ehlers, Elisabeth Rolfes, Mareike Lieber, Dominik Müller, Elke Lainka, Faekah Gohar, Günter Klaus, Hermann Girschick, Jana Hörstermann, Jasmin Kümmerle-Deschner, Jürgen Brunner, Katharina Palm-Beden, Klaus Tenbrock, Lusine von Wrangel, Maria Faßhauer, Norbert Blank, Ralf Trauzeddel, Anne Sae Lim von Stuckrad, Sonja Higgins, Tatjana Welzel, Thomas Lutz, Véronique Hentgen, Dirk Foell, Helmut Wittkowski, Tilmann Kallinich
Involvement of the systemic microcirculation in pediatric uveitis
- Open Access
- Research article
Carlyn V. Kouwenberg, Julia Spierings, Evianne L. de Groot, Joke H. de Boer, Viera Kalinina Ayuso
Prevalence of tissue transglutaminase antibodies and IgA deficiency are not increased in juvenile idiopathic arthritis: a case-control study
- Open Access
- Research article
Angela Taneja Kohli, Aimee O. Hersh, Lori Ponder, Lai Hin Kimi Chan, Kelly A. Rouster-Stevens, Anne E. Tebo, Subra Kugathasan, Stephen L. Guthery, John F. Bohnsack, Sampath Prahalad
‘The current mental health status of children and young people with JIA, and their wider family’: a charity partner collaboration survey
- Open Access
- Research article
Polly Livermore, S. Ainsworth, R. Beesley, S. Douglas, E. Earle, D. Wilson, L. Woolley, J. Clinch
Anakinra and hepatotoxicity in pediatric rheumatology: a case series
- Open Access
- Case Report
Frederico Rajão Martins, André Costa Azevedo, Sara Ganhão, Francisca Aguiar, Mariana Rodrigues, Iva Brito
Juvenile Dermatomyositis in Afro-Caribbean children: a cohort study in the French West Indies
- Open Access
- Short Report
Arthur Felix, Frederique Delion, Fabienne Louis-Sidney, Lindsay Osei, Aurélie Armougon, Remi Bellance, Moustapha Dramé, Christophe Deligny, Benoit Suzon, Yves Hatchuel
Performance of interferon-gamma levels may lead to earlier diagnosing macrophage activation syndrome complicating systemic juvenile idiopathic arthritis
- Open Access
- Letter to the Editor
Meiping Lu, Liping Teng, Yiping Xu, Xuefeng Xu
Impact of physiotherapy on orofacial manifestations of juvenile idiopathic arthritis
- Open Access
- Research article
Stratos Vassis, Cory M. Resnick, Mette Nørgaard, Kathleen M. Strawn, Helle Grove, Beatrice Noeldeke, Troels Herlin, Thomas Klit Pedersen, Peter Bangsgaard Stoustrup
Tocilizumab reduces the unmanageable inflammatory reaction of a patient with Aicardi-Goutières syndrome type 7 during treatment with ruxolitinib
- Open Access
- Case Report
Wei Wang, Wei Wang, Siming Peng, Sihao Gao, Meiying Quan, Lijuan Gou, Changyan Wang, Zhixing Sun, Zhuo Li, Dongmei Lian, Hongmei Song
Nailfold capillary density in 140 untreated children with juvenile dermatomyositis: an indicator of disease activity
- Open Access
- Short Report
Lauren M. Pachman, Gabrielle Morgan, Marisa S. Klein-Gitelman, Najah Ahsan, Amer Khojah
A single-center study of clinical features of pediatric Sjögren’s syndrome
- Open Access
- Research article
Ling Hou, Ningning Wang, Chengguang Zhao, Xiuli Wang, Yue Du
Majority of new patient referrals to a large pediatric rheumatology center result in non-rheumatic diagnosis
- Open Access
- Research article
Daniel D Reiff, John M Bridges, Eileen C Rife, Victoria L Gennaro, Linda McAllister, Annelle Reed, Carolyn Smith, Bethany Walker, Peter Weiser, Emily A Smitherman, Matthew L Stoll, Melissa L Mannion, Randy Q Cron
A narrative review of the literature on illness uncertainty in hypermobile ehlers-danlos syndrome: implications for research and clinical practice
- Open Access
- Review
Estée C.H. Feldman, Kendra J. Homan, Sara E. Williams, Tracy V. Ting, Kenneth R. Goldschneider, Susmita Kashikar-Zuck
Accuracy and adequacy of photoprotection in pediatric systemic lupus erythematosus patients, and the effect of education on photoprotection: a prospective study
- Open Access
- Research article
Porntipa Suebsarakam, Dara Mairiang
Efficacy and safety of thalidomide in children with monogenic autoinflammatory diseases: a single-center, real-world-evidence study
- Open Access
- Research article
Caihui Zhang, Zhongxun Yu, Sihao Gao, Mingsheng Ma, Lijuan Gou, Changyan Wang, Lin Wang, Ji Li, Linqing Zhong, Yu Zhou, Wei Wang, Hongmei Song
Connective tissue nevus misdiagnosed as juvenile localized scleroderma
- Open Access
- Research article
F. Tirelli, C. Giraudo, M. Soliani, F. Calabrese, G. Martini, P. Gisondi, A. Meneghel, Francesco Zulian
Systemic lupus erythematosus combined with Castleman disease and secondary paraneoplastic pemphigus: a case report
- Open Access
- Case Report
Xin Ma, Jiyuan Li, Linlin Fan, Hongwei Jiang, Gaishao Shi, Dongfeng Ge, Xiaofei Shi
A qualitative evaluation of the specific carbohydrate diet for juvenile idiopathic arthritis based on children’s and parents’ experiences
- Open Access
- Research article
Naima Hagström, Elin Lövestam, Afsaneh Koochek, Lillemor Berntson
Circulating prolactin level in Juvenile Systemic Lupus Erythematosus and its correlation with disease activity: a case control study
- Open Access
- Research article
Hend Mehawed Soliman, Balsam Sherif Fahmy, Moataz Gamal Ali, Eman Shafik Shafie
Adolescent and caregiver preferences for juvenile idiopathic arthritis treatment: a discrete-choice experiment
- Open Access
- Research article
Flora McErlane, Marco Boeri, Cooper Bussberg, Joseph C. Cappelleri, Rebecca Germino, Lori Stockert, Caroline Vass, Adam M. Huber
Potential regulatory role of the Nrf2/HMGB1/TLR4/NF-κB signaling pathway in lupus nephritis
- Open Access
- Research article
Shi-jie Li, Dan-dan Ruan, Wei-zhen Wu, Min Wu, Qiu-yan Wu, Han-lu Wang, Yuan-yuan Ji, Yan-ping Zhang, Xin-fu Lin, Zhu-ting Fang, Li-sheng Liao, Jie-wei Luo, Mei-zhu Gao, Jia-bin Wu
Case report: JAK1/2 inhibition with baricitinib in the treatment of STING-associated vasculopathy with onset in infancy
- Open Access
- Case Report
Jianqiang Wu, Qing Zhou, Hua Zhou, Meiping Lu
Correction: Importance of pediatric rheumatologists and transitional care for juvenile idiopathic arthritis-associated uveitis: a retrospective series of 9 cases
- Open Access
- Correction
Susumu Yamazaki, Asami Shimbo, Yuko Akutsu, Hiroshi Takase, Tomohiro Morio, Masaaki Mori
Reliability of the tunisian pediatric gait, arms, legs, and spine: toward a valid screening tool for tunisian children with musculoskeletal conditions
- Open Access
- Research article
Lassoued Ferjani Hanene, Narjess Amdouni, Rabhi Emna, Sahli Hela, Ben Abdelgheni Kaouther, Ben Nessib Dorra, Kaffel Dhia, Maatallah Kaouther, Hamdi Wafa
Reporting of determinants of health inequities and participant characteristics in randomized controlled trials of juvenile idiopathic arthritis in Canada: a scoping review
- Open Access
- Research article
Niloofar Gheshlaghi, Megan Thomas, Natasha Trehan, Mark Harrison, Mary A. De Vera
Reverse complete heart block using transcutaneous pacing and repeated plasmapheresis in a neonate with lupus: a case report
- Open Access
- Case Report
Yanfei Liu, Wanwei Li, Kun Zhou, Zhangxue Hu
Tuberculosis among children and adolescents with rheumatic diseases - case series
- Open Access
- Short Report
Lenita de Melo Lima, Adriana Rodrigues Fonseca, Clemax Couto Sant’Anna, Ana Alice Amaral Ibiapina Parente, Rafaela Baroni Aurilio, Maria de Fátima Bazhuni Pombo Sant’Anna
Juvenile dermatomyositis: association between nail fold capillary end row loop– area under the curve– and disease damage indicators
- Open Access
- Research Article
Amer Khojah, Gabrielle Morgan, Marisa S. Klein-Gitelman, Lauren M. Pachman
Ovarian dysfunction in adolescent girls with autoimmune rheumatic diseases
- Open Access
- Research article
Mohamed Taman, El-Hadidy NM, Hamed Yousef, Doaa Mosad Mosa
“Online survey of COVID-19 immunization and infection in patients with systemic juvenile idiopathic arthritis and adult-onset still’s disease.”
- Open Access
- Research article
Mariana Correia Marques, Subrata Paul, Carol Lake, Ly-Lan Bergeron, Rashmi Sinha, Luciana Peixoto, Marinka Twilt, Michael J. Ombrello
Is it possible to extend the dose interval of canakinumab treatment in children with familial Mediterranean fever? PeRA group experience
- Open Access
- Research article
Gülşah Kavrul Kayaalp, Şengül Çağlayan, Fatma Gül Demirkan, Vafa Guliyeva, Gülçin Otar Yener, Kübra Öztürk, Ferhat Demir, Semanur Özdel, Mustafa Çakan, Hafize Emine Sönmez, Betül Sözeri, Nuray Aktay Ayaz
Impact of anakinra use on clinical outcomes in children with moderate or severe multisystem inflammatory syndrome in children: a propensity score matched retrospective cohort study
- Open Access
- Research article
Esra B. Akkoyun, Zachary Most, Harita Katragadda, Andrew Yu, Lorien Nassi, Nicole Oakman, Sarah Ginsburg, Mia Maamari
Chronic limping in childhood, what else other than juvenile idiopathic arthritis: a case series
- Open Access
- Case Report
Cristina Tumminelli, Serena Pastore, Andrea Taddio
Identification of key biomarkers in RF-negative polyarticular and oligoarticular juvenile idiopathic arthritis by bioinformatic analysis
- Open Access
- Research article
Yun Liu, Xuemei Tang
Bridging gaps: a qualitative inquiry on improving paediatric rheumatology care among healthcare workers in Kenya
- Open Access
- Research article
Angela Migowa, Sasha Bernatsky, Anthony K. Ngugi, Helen E. Foster, Peterrock Muriuki, Roselyter M. Riang’a, Stanley Luchters
Towards telehealth delivery in pediatric rheumatology practice
- Open Access
- Commentary
Raju Khubchandani, Tadej Avčin, Angelo Ravelli
Role of ultrasound and inflammatory factors in the management of pediatric hip joint effusion
- Open Access
- Research article
Seyed Ali Alamdaran, Mohadeseh Taheri-nezhad, Ahmad Nouri, Farzaneh Khoroushi, Mohammad Hasan Aalami, Abdoreza Malek, Arezou Mohtasham, Mohamadreza Alizadeh
Lung infection or inflammation-a puzzling case of MDA-5 associated juvenile dermatomyositis
- Open Access
- Letter to the Editor
Anusha Vuppala, Manush Sondhi, Sarwat Umer
Defining a therapeutic range for adalimumab serum concentrations in the management of pediatric noninfectious uveitis, a step towards personalized treatment
- Open Access
- Research article
Jo L. Dehoorne, Helena Groth, Emma Carlé, Ilse De Schrijver, Celine Sys, Patricia Delbeke, Elke O. Kreps, Thomas Renson, Carolien Bonroy
Transition readiness among finnish adolescents with juvenile idiopathic arthritis
- Open Access
- Research article
Katriina Mikola, Katariina Rebane, Hannu Kautiainen, Kristiina Aalto