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Pediatric Rheumatology

Ausgabe 1/2025

Inhalt (129 Artikel)

Massive pulmonary thromboembolism in a pediatric patient with eosinophilic granulomatosis with polyangiitis: a case-based review emphasizing management

  • Open Access
  • Review

Batuhan Küçükali, Merve Yazol, Çisem Yıldız, Büşra Acun, Nuran Belder, Nihal Karaçayır, Merve Kutlar, Pelin Esmeray Şenol, Zühre Kaya, Deniz Gezgin Yıldırım, Sevcan A. Bakkaloğlu

Factors associated with treatment response in chronic nonbacterial osteomyelitis at a single center: a retrospective cohort study

  • Open Access
  • Research article

Katherine D. Nowicki, Nathan D. Rogers, Carson L. Keeter, Nathan J. Donaldson, Jennifer B. Soep, Yongdong Zhao

Increasing and maintaining rates of standardized depression screening in youth with childhood-onset systemic lupus erythematosus in a pediatric rheumatology clinic

  • Open Access
  • Research article

Emily Datyner, Jodi Dingle, Victoria Newsome, Lisa H. Buckley, Natasha Belsky, Seungweon Park, Manda Mitchell, Brooke Fine, Barron Patterson, T. Brent Graham, Alaina Davis

Monocyte STAT1 phosphorylation and treatment response of JAK inhibitors in chronic nonbacterial osteomyelitis

  • Open Access
  • Research article

Motoshi Sonoda, Keishiro Kinoshita, Nobutaka Harada, Sungyeon Park, Shunichi Adachi, Yutaro Yada, Katsuhide Eguchi, Toshifumi Fujiwara, Makiko Kido-Nakahara, Noriko Kinjo, Masataka Ishimura, Shouichi Ohga

A qualitative study exploring experiences of treatment in paediatric rheumatology - children’s, young people’s, parents’ and carers’ perspectives

  • Open Access
  • Research article

Kassie Gracella Putri, Sunil Sampath, Charlotte Lucy Richardson, Alice McCloskey, Adam Pattison Rathbone

Frequency of remission achievement in the pre-treat-to-target decade in juvenile idiopathic arthritis

  • Open Access
  • Research article

Ana Isabel Rebollo-Giménez, Angela Pistorio, Silvia Maria Orsi, Francesca Ridella, Elena Aldera, Luca Carlini, Valentina Natoli, Marco Burrone, Silvia Rosina, Roberta Naddei, Alessandro Consolaro, Esperanza Naredo, Angelo Ravelli

Joint fluid multi-omics improves diagnostic confidence during evaluation of children with presumed septic arthritis

  • Open Access
  • Research article

Yolanda Peña-López, Naureen G. Tareen, Bo Zhang, Indu Raman, Carlos A. Arana, Chengsong Zhu, Yang Liu, Pratibha Selvakumar, Nicolai S. C. van Oers, Simrat Morris, Lora V. Hooper, Lawson A. B. Copley, Prithvi Raj

Exploring the clinical profiles and management of juvenile dermatomyositis in Africa: a survey of African rheumatology care providers

  • Open Access
  • Research article

Jessica Perfetto, Laura B. Lewandowski, Dawn M. Wahezi, Vanessa Ogega, Joan Ahimbisibwe, Kate Webb, Christiaan Scott, Angela Migowa

Increased interferon I signaling, DNA damage response and evidence of T-cell exhaustion in a patient with combined interferonopathy (Aicardi-Goutières Syndrome, AGS) and cohesinopathy (Cornelia de Lange Syndrome, CdLS)

  • Open Access
  • Research article

Sorina Boiu, Nikolaos Paschalidis, George Sentis, Theodora Manolakou, Andrianos Nezos, Manolis Gialitakis, Maria Grigoriou, Erato Atsali, Melpomeni Giorgi, Argirios Ntinopoulos, Clio Mavragani, Periklis Makrythanasis, Dimitrios T. Boumpas, Aggelos Banos

Significance of differential diagnosis for the elucidation of rare and complicated diseases

  • Open Access
  • Correspondence

Jiro Ichikawa, Tomonori Kawasaki, Kojiro Onohara, Masanori Wako, Satoshi Ochiai, Tetsuo Hagino

An updated overview of Juvenile systemic sclerosis in a French cohort

  • Open Access
  • Research article

Léa Jacquel, Rouba Bechara, Joëlle Terzic, Anne-Cécile Rameau, Emmanuel Chatelus, Linda Rossi-Semerano, Isabelle Kone-Paut, Ulrich Meinzer, Irène Lemelle, Charlotte Rebelle, Diego Urbina, Pascal Pillet, Pauline Choquet, Jad El Maamari, Ariane Zaloszyc

Lack of HLH in FMF

  • Open Access
  • Research

Ozge Basaran, Erdal Sag, Elif Arslanoglu Aydın, Busra Aydın, Nur Kübra Tasdemir, Elif Celikel, Yagmur Bayındır, Semanur Özdel, Yelda Bilginer, Alexei A Grom, Seza Ozen

Infant Kawasaki disease complicated with supraventricular tachycardia: a case report and literature review

  • Open Access
  • Case Report

Nanjun Zhang, Bowen Li, Yu Yan, Shuran Shao, Yimin Hua, Hongyu Duan, Kaiyu Zhou, Chuan Wang, Xiaoliang Liu

Fasciitis-panniculitis syndrome with autoantibodies reacting to adipocyte pericellular fibers: a case report

  • Open Access
  • Case Report

Yu Uehara, Takuji Enya, Kohei Miyazaki, Yoshiyuki Hakata, Sachiyo Kawahara, Masaaki Miyazawa, Keisuke Sugimoto

Safety and effectiveness of intravenous abatacept for polyarticular-course juvenile idiopathic arthritis: An all-case postmarketing surveillance study

  • Open Access
  • Research

Tomo Nozawa, Naomi Iwata, Toru Igarashi, Ichiro Kobayashi, Shoji Ota, Takako Yamada, Etsuya Bando, Katsuyoshi Habiro, Syuji Takei

Mortality in children and adolescents with autoimmune inflammatory rheumatic diseases admitted to the pediatric intensive care unit

  • Open Access
  • Research article

Tinnapat Buranapattama, Suwannee Phumeetham, Nuntawan Piyaphanee, Maynart Sukharomana, Sirirat Charuvanij

Clinical remission rate and drug withdrawal status in articular juvenile idiopathic arthritis

  • Open Access
  • Research article

Akira Oshima, Takasuke Ebato, Masanori Kaneko, Yoshiaki Shikama, Tomoyuki Imagawa

Successful treatment of an anti-MDA5 antibody-positive Juvenile Dermatomyositis patient with refractory interstitial lung disease using tofacitinib

  • Open Access
  • Letter to the Editor

Valentina Natoli, Serena Palmeri, Ana Isabel Rebollo-Giménez, Caterina Matucci-Cerinic, Paola Bocca, Roberta Caorsi, Stefano Volpi, Riccardo Papa, Alessandro Consolaro, Marco Gattorno, Angelo Ravelli, Silvia Rosina

Minor salivary gland biopsy in the diagnosis of definite ocular sarcoidosis in paediatric granulomatous uveitis

  • Open Access
  • Research

Leire Etchandy, Marie-Noelle Meaux, Olivier Richer, Chloé Bianchi, Skander Korbi, Claire Castain, Guillaume Chotard, Marie-Bénédicte Rougier, Emmanuel Ribeiro, Johanna Clet, Pascal Pillet, Jérôme Granel

Cyclophosphamide treatment with a comparison in both pediatric rheumatology and pediatric nephrology practices

  • Open Access
  • Research

Deniz Gezgin Yildirim, Emine Yılmaz Orulluoglu, Cisem Yildiz, Ceyhun Acari, Hatice Adiguzel Dundar, Okan Akaci, Nurver Akinci, Emil Aliyev, Bedriye Nuray Alpman, Ozge Altug Gucenmez, Elif Arslanoglu Aydin, Bahriye Atmis, Pinar Ozge Avar Aydin, Fatma Aydin, Ozge Baba, Esra Baglan, Ilknur Bagrul, Kenan Barut, Ozge Basaran, Umut Selda Bayrakci, Nuran Belder, Burcu Bozkaya Yucel, Bahar Buyukkaragoz, Sengul Caglayan, Mustafa Cakan, Elif Celikel, Ferhat Demir, Selcan Demir, Yasemin Demir Yigit, Fatma Gul Demirkan, Nida Dincel, Seyda Dogantan, Zahide Ekici Tekin, Esra Genc, Fatih Haslak, Rana Isguder, Aslihan Kara, Muserref Kasap Cuceoglu, Ummusen Kaya Akca, Hakan Kisaoglu, Rabia Miray Kisla Ekinci, Zehra Kızıldag, Tuba Kurt, Batuhan Kucukali, Emre Leventoglu, Hulya Nalcacioglu, Gulcin Otar Yener, Semanur Ozdel, Yesim Ozdemir Atikel, Sumeyra Ozdemir Cicek, Sule Pektas Leblebiciler, Erkin Serdaroglu, Hafize Emine Sonmez, Emine Nur Sunar Yayla, Serra Surmeli Doven, Sezgin Sahin, Seher Sener, Ayse Tanatar, Merve Tanidir, Sema Nur Taskin, Betul Tiryaki, Serife Tuncez, Serkan Turkucar, Bahriye Uzun Kenan, Nurdan Yildiz, Kenan Yilmaz, Yilmaz Tabel, Ismail Dursun, Nur Canpolat, Sevgi Mir, Harun Peru, Rezan Topaloglu, Metin Kaya Gurgoze, Ayse Balat, Yelda Bilginer, Banu Celikel Acar, Betul Sozeri, Erbil Unsal, Ozgür Kasapcopur, Sevcan A. Bakkaloglu

Correction: Safety and effectiveness of intravenous abatacept for polyarticular-course juvenile idiopathic arthritis: An all-case postmarketing surveillance study

  • Open Access
  • Correction

Tomo Nozawa, Naomi Iwata, Toru Igarashi, Ichiro Kobayashi, Shoji Ota, Takako Yamada, Etsuya Bando, Katsuyoshi Habiro, Syuji Takei

Mycophenolic acid trough level assessment in patients with lupus nephritis; does it make a difference?

  • Open Access
  • Research

Ahmed E. Abdulgalil, Noha H. Elnagdy, Nehal M. Ramadan, Eman Hamza, Ayman Hammad, Mai S Korkor, Atef Elmougy, Ali Sobh, Marwa H Elnagdy

African guidelines for diagnosis and management of polyarticular juvenile idiopathic arthritis: PAFLAR initiative

  • Open Access
  • Research

Mohammed Hassan Abu-Zaid, Angela Nyangore Migowa, Hanna Lishan Kassa, Wassila Messadi, Yassmine Taha, Yaninga Halwani Fuseini, Madeleine Ngandeu, Yasser El Miedany, Michael Hofer, Wafa Hamdi, Temesgen Teferi Libe, Ali Sobh, Waleed Hassan, Yasmine Makhlouf, Ayodele Faleye, Soad Hashed, Samah Ismail Nasef, Chafia Dahou Makhloufi, Elisa Palalane, Hanene Lassoued Ferjani, Ahmed Seri, Doaa Mosad Mosa, Ourida Gacem, Francis Fredrick Furia, Samy Slimani, Christiaan Scott, Djohra Hadef

Clinical insights into heterogeneity of rheumatoid factor negative polyarticular juvenile idiopathic arthritis across the world

  • Open Access
  • Research article

Roberta Naddei, Marco Burrone, Francesca Ridella, Yosef Uziel, Maria Trachana, Pavla Dolezalova, Ingrida Rumba-Rozenfelde, Nicolino Ruperto, Angelo Ravelli, Alessandro Consolaro

Red blood cell distribution width predicts coronary artery lesions in Kawasaki disease: insights from a Japanese cohort

  • Open Access
  • Research article

Yamato Hanawa, Wataru Murasaki, Hiroyuki Namba, Kimihiko Oishi

Monozygotic twins discordant for juvenile dermatomyositis: clinical, serological and gene expression studies

  • Open Access
  • Research

Lauren M. Pachman, Amer Khojah, Gabrielle Morgan, Wilfredo Marin, Judith James, Sabah Kadri, Kai Lee Yap

Epidemiology and comorbidity of juvenile idiopathic arthritis in Poland– a nationwide study

  • Open Access
  • Research article

Zbigniew Żuber, Krzysztof Podwójcic, Mateusz Szeląg, Magdalena Krajewska-Włodarczyk, Krzysztof Batko, Michał Orleański, Jakub Sowiński, Maria Świderek, Agata Śmiglewska, Michał Maluchnik, Marek Brzosko, Brygida Kwiatkowska, Marcin Stajszczyk, Bogdan Batko

Perspectives and experiences of parents of children with juvenile dermatomyositis: a semi-structured interview study

  • Open Access
  • Research article

Amy Helen Kelly, Ayano Kelly, Davinder Singh-Grewal, Jeffrey Chaitow, Allison Jaure

Serositis as an indicator of poor prognosis in pediatric systemic lupus erythematosus

  • Open Access
  • Research

Wei-Chen Kao, Ya-Chiao Hu, Jyh-Hong Lee, Li-Chieh Wang, Yu-Tsan Lin, Yao-Hsu Yang, Bor-Luen Chiang, Hsin-Hui Yu

Non-organic back pain signs in children with amplified musculoskeletal pain involving the back

  • Open Access
  • Research

David D. Sherry, Mackenzie McGill, Sabrina Gmuca

Characterizing lupus in African American children in Southern United States

  • Open Access
  • Brief Report

Taylor B. Winstead, Spencer Hagwood, Cynthia Karlson, Anita Dhanrajani

Bacterial infection in patients with juvenile systemic lupus erythematosus and fever

  • Open Access
  • Research

José Fernando Gómez-Urrego, Nathalie Yepes-Madrid, Mónica Alexandra Gil-Artunduaga, María del Pilar Gómez-Mora, Luis Fernando Mejía-Rivera, Robinson Pacheco-López, Juan Pablo Rojas-Hernández

Unmet needs and research gaps in Still’s disease across ages: proceedings from a pediatric and adult joint expert panel

  • Open Access
  • Meeting Report

Claudia Bracaglia, Francesca Minoia, Sebastiaan J. Vastert, Christoph Kessel, Lorenzo Dagna, Angelo Ravelli, Fabrizio De Benedetti

Endocrine dysfunction in patients with juvenile idiopathic arthritis

  • Open Access
  • Research article

Sayan Mukherjee, Abilash Krishnan Vijayakumaran, Mukesh Kumar Maurya, Nishant Gautam Kamble, Ankush PM, Puneet Kumar, Wahid Ali, Mala Kumar, Saurabh Kumar, Pankti Mehta, T. G. Sundaram, Urmila Dhakad

Incidence and reasons for biologic and targeted synthetic DMARD switching in juvenile idiopathic arthritis: a real- life stratified analysis

  • Open Access
  • Research

Daniel Clemente, Leticia Leon, Juan Carlos Nieto-Gonzalez, Alina Lucica Boteanu, Laura Trives Folguera, Antía Asunción García-Fernández, Helena Amar Muñoz, Aliuska Palomeque, Juan Carlos López Robledillo, Lydia Abasolo

Influenza vaccination in patients with juvenile idiopathic arthritis under different treatments: safety and immune response

  • Open Access
  • Research

Adam Gyori, Arnold Nagy, Gabor Ottoffy, Tamas Decsi, Diana Simon, Timea Berki, Timea Dergez, David Kuti, Bernadett Mosdosi

Imaging assessment of calcinosis in juvenile dermatomyositis: a narrative review

  • Open Access
  • Review

Belina Y. Yi, Jessica Perfetto, Evin Rothschild, Kelly Rouster-Stevens, Amanda Robinson, Kathryn Cook, Delaney D. Ding, Andrea Eagle Child, Ovgu Kul Cinar, Barbara Limbach, Charalampia Papadopoulou, Lesley Ann Saketkoo, Adam Schiffenbauer, Heinrike Schmeling, Antonia Valenzuela, Susan Shenoi, Dawn M. Wahezi

Digital health tools in juvenile idiopathic arthritis: a systematic literature review

  • Open Access
  • Research article

Jordi Anton, María Montoro, Estíbaliz Loza, Teresa Otón, Susan Ramirez, Diego Benavent

Developing consensus outcome measures in juvenile systemic sclerosis: a global survey of pediatric rheumatologists and literature review

  • Open Access
  • Research

Natalia Vasquez-Canizares, Clare E. Pain, Francesco Zulian, Amra Adrovic Yildiz, Simone Appenzeller, Edoardo Marrani, Emanuela Del Giudice, Antonella Petaccia, Francesca Tirelli, Gabriele Simonini, Mustafa Çakan, Marco Cattalini, Paulo Rogerio Julio, Kathryn Torok, Raju Khubchandani, Ozgur Kasapcopur, Lauren Robinson, Eslam Al-Abadi, Aybuke Gunalp, Meiping Lu, Hanna Lythgoe, Amanda Robinson, Betul Sozeri, Susan Shenoi, Emily Willis, Katherine Clarke, Rongjun Zheng, Biagio Castaldi, Valentina Leone, Valerio Maniscalco, Lucy Stead, Lusine Ambartsumyan, Franziska Rosser, Phuoc Duong, Aurelia Minuti, Suzanne C. Li, Marinka Twilt

FDG-PET/CT as a useful tool for disease activity assessment in large vessel vasculitis in childhood

  • Open Access
  • Letter to the Editor

Tobias Krickau, Armin Atzinger, Joerg Juengert, Juergen Rech, Oliver Rompel, André Hoerning

Effect of additional intravenous immunoglobulin for infliximab-refractory Kawasaki disease: a cohort study

  • Open Access
  • Research article

Satoki Hatano, Hiro Nakao, Hiroshi Masuda, Hiroshi Ono, Mitsuru Kubota, Akira Ishiguro

Chronic non-bacterial osteomyelitis in children- five-year standardized follow-up of a prospective observational cohort in the pre-biological era

  • Open Access
  • Research

Christine Hofmann, Annette Holl-Wieden, Christiane Reiser, Meinrad Beer, Peter Raab, Henner Morbach, Hermann J. Girschick

International multidisciplinary consensus on the definition and clinical approach for monogenic inflammatory immune dysregulation disorders

  • Open Access
  • Research

Hend M. Alkwai, Ibrahim A. Almaghlouth, Leonardo Oliveira Mendonça, Shuayb Elkhalifa, Hassan Abolhassani, Suliman Aljumaah, Hamoud Al-Mousa, Mohammed F. Alosaimi, Alhanouf AlSaleem, Tadej Avcin, Winnie KY Chan, Graciela Espada, Marie-Louise Frémond, Ahmet Gül, Djohra Hadef, Nasim Movahedi, Helmut Wittkowski, Sulaiman M. Al-Mayouf

Application of the Scleroderma Clinical Trials Consortium Damage Index in patients with juvenile systemic sclerosis

  • Open Access
  • Research article

Caihui Zhang, Changyan Wang, Sihao Gao, Mingsheng Ma, Wei Wang, Tianyu Zhang, Yu Zhang, Xiaoyan Tang, Zhuo Li, Zhixing Sun, Lin Wang, Hongzhong Jin, Xiaofeng Zeng, Hongmei Song

Bayesian trial of adalimumab versus secukinumab for children with juvenile idiopathic arthritis associated uveitis or chronic anterior uveitis

  • Open Access
  • Research article

Athimalaipet V Ramanan, Andrew D Dick, Thomas Jaki, Gianmarco Caruso, David S Robertson, Ashley P Jones, Ben Hardwick, Sian Drake, Balini Balasubramaniam, Coziana Ciurtin, Ivan Foeldvari, Elke O Kreps, Alice Leahy, Kristina May, Pierre Quartier, Matthieu P Robert, Gabriele Simonini, Catherine Guly, Michael W Beresford

Diagnosis, management, and monitoring of interleukin-1 mediated diseases in Central and Eastern Europe: real-world data

  • Open Access
  • Research article

Marija Jelusic, Mario Sestan, Natasa Toplak, Constantin Tamas, Jelena Vojinovic, Zbigniew Zuber, Beata Wolska-Kusnierz, Mihaela Sparchez, Milos Jesenak, Skirmante Rusoniene, Valda Stanevica, Pavla Dolezalova, Liora Harel, Yosef Uziel, Marco Gattorno

Insights from the 2024 pediatric rheumatology basic/translational years in review

  • Open Access
  • Review

Jessica L. Turnier, Scott W. Canna

Nailfold videocapillaroscopy in patients with deficiency of adenosine deaminase 2 (DADA2): a case-control study

  • Open Access
  • Short Report

Pietro Francesco Bica, Caterina Matucci-Cerinic, Elvis Hysa, Andrea Cere, Silvia Rosina, Stefano Volpi, Roberta Caorsi, Alberto Sulli, Sabrina Paolino, Vanessa Smith, Maurizio Cutolo, Marco Gattorno

Management of childhood-onset systemic lupus erythematosus (cSLE) over the last two decades in Spain

  • Open Access
  • Review

Alina Boteanu, Juan José Bethencourt, Joan Calzada-Hernández, Daniel Clemente, Juan Carlos Nieto-González, Covadonga López, Laura Luque, Inmaculada Calvo

Two unique cases of eosinophilic granulomatosis with polyangiitis in childhood treated with anti-interleukin-5 therapy: infantile-onset and submandibular salivary gland involvement

  • Open Access
  • Case Report

Evangelia Constantine, Adam M. Bartholomeo, Inna Powers, Jerimiah L. Lysinger, Pia J. Hauk, Jordan Abbott, Heather H. de Keyser, Nicholas J. Gilman, Csaba Galambos, Angus Toland, Nicholas Willard, Jason Weinman, David Mong, Clara Lin, Jessica L. Bloom

Predictive factors of comorbid attention-deficit/hyperactivity disorder in early systemic autoimmune and auto-inflammatory disorders

  • Open Access
  • Brief Report

Briac Daniel, Eric Acquaviva, Brigitte Bader-Meunier, Alexandre Belot, Glory Dingulu, Cecile Dumaine, Albert Faye, Marie-Louise Frémond, Laura Lavialle, Ulrich Meinzer, Pierre Quartier, Caroline Vinit, Richard Delorme, Isabelle Melki, Pierre Ellul

Juvenile localized scleroderma: a large retrospective cohort study from a tertiary care center

  • Open Access
  • Research article

Bugra Han Egeli, Johnathan Dallas, Diana B. Reusch, Katharina S. Shaw, Stephen Gellis, Robert Sundel, Mary Beth Son, Ruth Ann Vleugels, Fatma Dedeoglu

Clinical characteristics and treatment of infantile Takayasu arteritis in the Chinese Han population: a single-center study

  • Open Access
  • Research

Jia Zhu, Min Kang, Yingjie Xu, Dan Zhang, Tong Yue, Ming Li, Min Wen, Feifei Wu, Gaixiu Su, Yang Yang, Wenquan Niu, Jianming Lai

Role of long non-coding RNAs and circular RNAs in kawasaki disease: a systematic review

  • Open Access
  • Research

Zahra Amirsardari, Mohammadmahdi Abbasi, Shana Ahadi, Aida Rezaee, Alireza Shalviri, Farnaz Shavandi, Reyhane Alidousti Shahraki, Mohammad Mahdavi, Mahshid Malakootian

Cytokines in saliva, serum, and temporomandibular joint synovial fluid in children with juvenile idiopathic arthritis: An explorative cross-sectional study

  • Open Access
  • Research

Paula Frid, Josefine M. Halbig, Per Alstergren, Johanna Rykke Berstad, Lena Cetrelli, Astrid Jullumstrø Feuerherm, Berit Flatø, Annika Rosen, Karen Rosendahl, Marite Rygg, Veronika Rypdal, Nils-Thomas Songstad, Berit Tømmerås, Ellen Nordal, Mohammed Al-Haroni

Pediatric immune-mediated necrotizing myopathy with anti-SRP antibodies targeting 19, 68, and 72 kda subunits

  • Open Access
  • Correspondence

Daigo Kato, Yoshitake Sato, Kanako Mitsunaga, Hiromi Aoyama, Naoko Okiyama, Ichizo Nishino, Minako Tomiita, Yuzaburo Inoue

Correction: Developing consensus outcome measures in juvenile systemic sclerosis: a global survey of pediatric rheumatologists and literature review

  • Open Access
  • Correction

Natalia Vasquez-Canizares, Clare E. Pain, Francesco Zulian, Amra Adrovic Yildiz, Simone Appenzeller, Edoardo Marrani, Emanuela Del Giudice, Antonella Petaccia, Francesca Tirelli, Gabriele Simonini, Mustafa Çakan, Marco Cattalini, Paulo Rogerio Julio, Kathryn Torok, Raju Khubchandani, Ozgur Kasapcopur, Lauren Robinson, Eslam Al‑Abadi, Aybuke Gunalp, Meiping Lu, Hanna Lythgoe, Amanda Robinson, Betul Sozeri, Susan Shenoi, Emily Willis, Katherine Clarke, Rongjun Zheng, Biagio Castaldi, Valentina Leone, Valerio Maniscalco, Lucy Stead, Lusine Ambartsumyan, Franziska Rosser, Phuoc Duong, Aurelia Minuti, Suzanne C. Li, Marinka Twilt

Exploring physical activity patterns in adolescents with hypermobility spectrum disorder or hypermobile Ehlers-Danlos Syndrome

  • Open Access
  • Research

Elke Schubert-Hjalmarsson, Jonatan Fridolfsson, Daniel Arvidsson, Mats Börjesson, Mari Lundberg

Immune checkpoint inhibitors and the pediatric rheumatologist: a pediatric needs assessment

  • Open Access
  • Research

John Storwick, Carrie Ye, Shahin Jamal, Nancy Maltez, Mercedes Chan

Identifying the characteristics of and developing a predictive model for differentiating cancer-related musculoskeletal symptoms from juvenile idiopathic arthritis

  • Open Access
  • Research

Khwanjira Archawanantakul, Soamarat Vilaiyuk, Samart Pakakasama, Butsabong Lerkvaleekul

Utility of patient-reported outcomes for pulmonary symptoms and sleep disturbance and impairment in children with systemic juvenile idiopathic arthritis

  • Open Access
  • Research

Kim Nguyen, Shima Yasin, Ndate Fall, Alexei A. Grom, Hermine I. Brunner, Christopher Towe, Grant S. Schulert

Juvenile dermatomyositis in Oman: clinical patterns and disease trajectory from a National cohort

  • Open Access
  • Brief Report

Reem Abdwani, Mahadev J. Mal, Eman Al Masroori, Ruqaiya Al Jashmi, Safiya Al Abrawi, Ibrahim Al-Zakwani

High rheumatoid factor does not diminish efficacy of TNF inhibitors in seropositive JIA

  • Open Access
  • Brief Report

Boris Hügle, Gerd Horneff, Johannes-Peter Haas

Disease activity at two consecutive registry visits and subsequent medication escalation for patients with juvenile idiopathic arthritis in the CARRA registry

  • Open Access
  • Research

Melissa L. Mannion, Monica S. Aswani, K. Ria Hearld, Emily A. Smitherman, Livie Timmerman, Jeffrey R. Curtis, R. Aamir, K. Abulaban, A. Adams, C. Aguiar Lapsia, H. Ahmed, S. Akoghlanian, A. AlBijadi, E. Allenspach, M. Alpizar, G. Amarilyo, M. Amoruso, S. Angeles-Han, S. Ardoin, S. Armendariz, N. Aviran Dagan, I. Balboni, S. Balevic, S. Ballinger, S. Baluta, L. Barillas-Arias, L. Barillas-Arias, M. Basiaga, K. Baszis, M. Becker, A. Begezda, E. Beil, H. Bell-Brunson, H. Benham, S. Benseler, L. BermudezSantiago, W. Bernal, T. Bigley, C. Bingham, B. Binstadt, C. Black, B. Blackmon, M. Blakley, J. Bohnsack, A. Boneparth, H. Bradfield, J. Bridges, E. Brooks, M. Brothers, D. Brown, H. Brunner, L. Buckley, Mary Buckley, Meredith Buckley, H. Bukulmez, D. Bullock, A. Cancino, S. Canna, L. Cannon, S. Canny, V. Cartwright, E. Chalom, Johanna Chang, Joyce Chang, M. Chang, A. Chang-Hoftman, A. Chen, P. Chiraseveenuprapund, K. Ciaglia, M. Cidon, D. Co, E. Cohen, R. Connor, K. Cook, A. Cooper, J. Cooper, K. Corbin, C. Correll, R. Cron, M. Curry, A. Dagci, A. Dalrymple, E. Datyner, T. Davis, D. De Ranieri, J. Dean, C. DeCoste, F. Dedeoglu, M. DeGuzman, N. Delnay, E. L. DeSantis, R. Devine, M. Dhalla, A. Dhanrajani, D. Dissanayake, B. Dizon, J. Drew, K. Driest, Q. Du, E. Duncan, K. Dunnock, D. Durkee, J. Dvergsten, A. Eberhard, K. Ede, B. Edelheit, C. Edens, M. Elder, Y. Elzaki, C. Failing, D. Fair, L. Favier, B. Feldman, J. Fennell, I. Ferguson, P. Ferguson, C. Figueroa, E. Flanagan, L. Fogel, E. Fox, M. Fox, L. Franklin, R. Fuhlbrigge, J. Fuller, T. Futch-West, S. Gagne, M. Geiszler, D. Gerstbacher, M. Gilbert, A. C. Gironella, D. Glaser, I. Goh, S. Gorry, N. Goswami, B. Gottlieb, T. Graham, S. Grevich, T. Griffin, A. Grim, A. Grom, M. Guevara, L. Guzman, T. Hahn, O. Halyabar, E. Hammelev, T. Hammond, S. Haro, J. Harris, O. Harry, J. Hausmann, A. Hay, K. Hays, K. Hayward, L. Henderson, M. Henrickson, A. Hersh, L. Hiraki, M. Hiskey, P. Hobday, C. Hoffart, M. J. Holland, M. Hollander, S. Hong, D. Horton, J. Hsu, A. Huber, J. Huggins, J. Hui-Yuen, M. Ibarra, A. Imlay, L. Imundo, C. Inman, A. Jackson, K. James, G. Janow, Y. Jiang, L. Johnson, N. Johnson, J. Jones, D. Kafisheh, K. Kaidar, S. Kasinathan, R. Kaur, E. Kessler, B. Kienzle, S. Kim, Y. Kimura, D. Kingsbury, M. Kitcharoensakkul, J. Klauss, K. Klein, M. Klein-Gitelman, A. Knight, L. Kovalick, D. Krajewski, C. Kremer, T. LaFlam, B. Lang, S. Lapidus, B. Lapin, A. Lasky, E. Lawson, R. Laxer, A. Lee, Patricia Lee, Pui Lee, T. Lee, E. Leisinger, L. Lentini, M. Lerman, Y. Levinsky, D. Levy, S. Li, S. Lieberman, L. Lim, E. Limenis, C. Lin, N. Ling, G. Lionetti, R. Livny, M. Lo, A. Long, M. Lopez-Peña, D. Lovell, S. Lvovich, A. Lytch, M. Ma, A. Machado, J. MacMahon, J. Madison, M. Mannion, C. Manos, L. Mansfield, B. Marston, K. Marzan, T. Mason, S. Matossian, L. McAllister, K. McBrearty, D. McCurdy, K. McDaniels, J. McDonald, L. McIntosh, E. Meidan, E. Mellins, Z. Mian, P. Miettunen, M. Miller, D. Milojevic, R. Mitacek, R. Modica, S. Mohan, K. Moore, T. Moore, L. Moorthy, J. Moreno, E. Morgan, A. Moyer, B. Murante, A. Murphy, E. Muscal, O. Mwizerwa, A. Najafi, K. Nanda, L. Nassi, S. Nativ, M. Natter, J. Neely, L. Newhall, A. Nguyen, P. Nigrovic, J. Nocton, B. Nolan, A. Nowakowski, K. Nowicki, R. Oakes, E. Oberle, S. Ogbonnaya-Whittesley, E. Ogbu, M. Oliver, R. Olveda, K. Onel, A. Orandi, J. Padam, N. Pan, J. Pandya, S. Panupattanapong, A. Pappo Toledano, J. Patel, P. Patel, A. Patrick, S. Patrizi, S. Paul, J. Perfetto, M. Perron, M. Peskin, C. Pinotti, L. Ponder, R. Pooni, S. Prahalad, M. Quinlan-Waters, J. Rafko, H. Rahimi, S. Ramsey, R. Randell, L. Ray, Ann Reed, Annelle Reed, H. Reid, D. Reiff, I. Reyhan, B. Richard, M. Riebschleger, E. Rife, M. Riskalla, A. Robinson, L. Robinson, L. Rodgers, M. Rodriquez, D. Rogers, T. Ronis, A. Rosado, M. Rosenkranz, N. Rosenwasser, H. Rothermel, D. Rothman, E. Rothschild, K. Rouster - Stevens, T. Rubinstein, N. Ruth, S. Sabbagh, R. Sadun, L. Santiago, V. Saper, A. Sarkissian, L. Scalzi, J. Schahn, K. Schikler, A. Schlefman, B. Schlichting, H. Schmeling, E. Schmitt, G. Schulert, C. Schutt, C. Seper, B. Shaham, R. Sheets, A. Shehab, S. Shenoi, M. Sherman, J. Shirley, M. Shishov, N. Singer, V. Sivaraman, E. Sloan, C. Smith, J. Smith, E. Smitherman, J. Soep, M. B. Son, C. Spencer, L. Spiegel, J. Spitznagle, H. Srinivasalu, H. Stapp, A. Stephens, Y. Sterba Rakovchik, S. Stern, B. Stevens, R. Stevenson, C. Stingl, M. Stoll, E. Stringer, S. Sule, J. Sullivan, R. Sundel, M. Sutter, C. Swaffar, N. Swayne, T. Symington, G. Syverson, A. M. Szymanski, S. Taber, R. Tal, A. Tambralli, A. Taneja, T. Tanner, S. Tarvin, A. Taxter, M. Tesher, T. Thakurdeen, A. Theisen, G. Thieroff, B. Thomas, L. Thomas, N. Thomas, L. Timmerman, T. Ting, C. Todd, D. Toib, K. Torok, H. Tory, M. Toth, E. Treemarcki, S. Tse, T. Tse, C. Tsin, J. Twachtman-Bassett, M. Twilt, T. Valcarcel, R. Valdovinos, A. Vallee, H. Van Mater, S. Vandenbergen, C. Varghese, N. Vasquez, P. Vega-Fernandez, J. Verbsky, R. Verstegen, E. von Scheven, S. Vora, L. Wagner-Weiner, D. Wahezi, S. Wakefield, B. Walker, S. Wallgren, H. Walters, M. Waterfield, J. Weiss, P. Weiss, E. Wershba, V. Westheuser, K. Widrick, C. Williams, S. Wong, S. Wooldridge, L. Woolnough, T. Wright, E. Wu, A. Yalcindag, R. Yeung, K. Yomogida, A. Zeft, Y. J. Zhang, Y. D. Zhao, Z. Zheng, A. Zhu, C. Zic

Mevalonate kinase deficiency: genetic and clinical characteristics of a Chinese pediatric cohort

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Chenchen Guan, Wenjie Wang, Qinhua Zhou, Jinqiao Sun, Lipin Liu, Luyao Liu, Bijun Sun, Jia Hou, Xiaochuan Wang

The utility of miR-16, miR-146a and miR-155 in serum and urine for juvenile idiopathic arthritis diagnostics and monitoring

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Ausra Snipaitiene, Kristina Snipaitiene, Andzelika Slegeryte, Benita Buragaite-Staponkiene, Asta Baranauskaite, Sonata Jarmalaite, Lina Jankauskaite

Risk prediction models for renal injury in children with IgA vasculitis: a systematic review and meta-analysis

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Jianrong Liao, Xuqiong Tan, Fengbi Jiang, Lin Zhu, Ping Zhou

Expanding the phenotypic and genetic spectrum of ORAS with novel homozygous variant in OTULIN gene: a case series and literature review

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Alhanouf AlSaleem, Abdulrahman Assiri, Rayyan Alfadda, Suliman Al-Jumaah, Sulaiman M. Al-Mayouf

A tale of two regions: comparing clinical features and outcomes in pediatric enthesitis-related arthritis

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Fatma Gül Demirkan, Vafa Guliyeva, Özlem Akgün, Hanene Lassoued Ferjani, Dorra Ben Nessib, Kawther Maatallah, Dhia Kaffel, Wafa Hamdi, Nuray Aktay Ayaz

Feasibility of applying infrared thermal imaging for home monitoring of arthritis in children

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Stephen Wong, Nivrutti Bhide, Erin Balay-Dustrude, Erin Sullivan, Joshua Scheck, Ian Muse, Kevin Cain, Debosmita Biswas, Savannah C. Partridge, Yongdong Zhao

Preliminary validation of a web-based MRI scoring system for children with chronic nonbacterial osteomyelitis (ChRonic nonbacterial Osteomyelitis Magnetic Resonance Imaging Scoring: CROMRIS)

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Farzana Nuruzzaman, T. Shawn Sato, Jennifer Stimec, Ramesh S. Iyer, Andrew Carbert, Joel Paschke, Lauren Potts, Meinrad Beer, Ming Huang, Johanna Monsalve, Anh-Vu Ngo, Mahesh Thapa, Xiaoyue Zhang, Walter P. Maksymowych, Polly J. Ferguson, Yongdong Zhao

Development and validation of a Pediatric Internationally agreed UltraSound Hip synovitis protocol (PIUS-hip), by the PReS imaging working party

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Daniel Windschall, Ralf Trauzeddel, Silvia Magni-Manzoni, Hatice Adiguzel-Dundar, Sven Hardt, Manuela Krumrey-Langkammerer, Lampros Fotis, Rainer Berendes, Sebastian Schua, Maria Haller, Ferhat Demir, Betul Sözeri, Faekah Gohar

Myocardial dysfunction is linked to endothelial dysfunction in JIA patients: a study of novel aortic circumferential strain

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Eman Shafik Shafie, Fatma ElZahraa Mostafa, Mohamad Samir AbdelWanis, Mira M. Gales, Antoine Fakhry AbdelMassih, Rana Essam

A roadmap for navigating child health research data sharing across Canada and beyond – building on UCAN CAN-DU

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Brittany Gerber, Gillian R. Currie, Alexander Mosoiu, Alexander Bernier, Francois P. Bernier, Kym M. Boycott, Guillermo Fiebelkorn, Kristien Hens, Bartha M. Knoppers, Claire LeBlanc, Stephen W. Scherer, David Shaw, Chris Viney, Carl Virtanen, Susanne M. Benseler, Rae S. M. Yeung, Deborah A. Marshall

Neurological involvement in children with familial Mediterranean fever: a systematic review

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Saverio La Bella, Antonio Corsello, Deniz Bayraktar, Armando Di Ludovico, Giovanna Scorrano, Marta Rinaldi, Yagmur Bayindir, Seza Ozen, Gregorio Paolo Milani, Marco Gattorno, Roberta Caorsi

Evaluating the causal effect of circulating proteome on the risk of Juvenile idiopathic arthritis: an omics pipeline study

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Xinglin Wu, Qiang Luo, Xiwen Luo, Dawei Liu, Fengming Li, Chenxi Ma, Xuemei Tang

Children’s experiences of a support program during their first year with juvenile idiopathic arthritis

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Karina Mördrup, Cecilia Bartholdson, Eva Broström, Johanna Granhagen Jungner

Childhood-onset Takayasu arteritis: clinical presentation, challenges and disease course

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L. Peremans, M. Twilt, A. Fifi-Mah, N. Johnson, D. Mosher, A. Wade, L. Hamiwka

Serum elafin levels in patients with IgA vasculitis: a prospective case-control study

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Cengiz Zeybek, Ahmet Bolat, Bedriye Nuray Alpman, Tuğba İpek Karaoğlu, Nimet Öner, Vildan Güngörer

New avenues in childhood vasculitis

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Hulya Ercan Emreol, Cagri Yildirim-Toruner, Marija Jelusic, Marinka Twilt, Seza Ozen

Still’s disease: bridging the gap between guidelines and clinical practice

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Çisem Yıldız, Batuhan Küçükali, Sevcan A. Bakkaloğlu

Neutrophil activation in juvenile dermatomyositis: associations with muscle function and disease progression

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Jia Shi, Yang Wu, Aviya L. Levy, Ting Wang, Abhinav Janappareddi, Payton Hermanson, Jorge A. Gonzalez Chapa, Qian Wang, Susan Shenoi, Christian Lood

Musculoskeletal manifestations in children with inflammatory bowel disease: a multicenter cohort study (GASTROREUM study)

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Adele Civino, Federico Diomeda, Romina Gallizzi, Marco Gattorno, Silvia Magni-Manzoni, Davide Montin, Gabriele Simonini, Giovanni Conti, Emanuela Del Giudice, Giovanni Filocamo, Fortunata Civitelli, Angela Miniaci, Serena Pastore, Francesco La Torre, Bianca Lattanzi, Angela Mauro, Lorenzo Mambelli, Patrizia Barone, Alma Nunzia Olivieri, Gianluca Vergine, Maria Cristina Maggio, Ilenia Floretta, Simona Campus, Luca Cantarini, Emanuela Sacco, Michela Cappella, Serena Arrigo, Giusyda Tarantino, Manuela Taurisano, Silvia Greco, Rossella Greco, Fabrizio De Benedetti, Francesca Bovis, Angelo Ravelli, Pierandrea Elefante, Alessandra Spagnolo, Francesco Chiarelli, Edoardo Marrani, Chiara Longo, Riccardo Lubrano, Giulia Loiacono, Cecilia Lugarà, Federica D’Amico, Arianna Petrillo, Rosaria Celano, Maria Francesca Gicchino, Francesca Cavataio, Alessandro De Fanti, Valeria Dell’Omo, Elisabetta Cortis, Federica Ferrari, Francesca Ardenti Morini, Francesca Soscia, Maria Pastore, Ilaria Battagliere, Eleonora Prete, Andrea Taddio

Referral letters to pediatric rheumatology: referral content and impact on triage – an observational study

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Alexandra Rydz, Fangfang Fu, Zhe Lu, Mark Drew, Dax Rumsey, Yan Yuan, Mercedes Chan

Exploring pediatric onset Still’s disease patient journey and parental perceptions in Türkiye through a survey

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Mehmet Yildiz, Elif Kilic Konte, Nergis Akay, Hatice Kubra Zora, Umit Gul, Kubra Ucak, Ece Aslan, Berkant Ersoy, Nihal Sahin, Elif Celikel, Boran Saracoglu, Sara Sebnem Kilic, Banu Celikel Acar, Ozgur Kasapcopur

Influenza vaccine uptake in juvenile idiopathic arthritis during the COVID-19 pandemic: a multi-centre cross-sectional study by PRES vaccination working party

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Despoina Maritsi, Noa Alpert, Masa Bizjak, Amit Ziv, Barbora Balaziova, Mehmet Yildiz, Alenka Gagro, Mario Sestan, Aygul Khabirova, Betul Sozeri, Sengul Caglayan, Marija Jelusic, Violetta Opoka-Winiarska, Mikhail Kostik, Claudia Bracaglia, Francesca Minoia, Tomas Dallos, Ozgur Kasapcopur, Natasa Toplak, Yosef Uziel, Panagiota Tsagkli, Merav Heshin-Bekenstein

Efficacy and safety of telitacicept in children with IgA vasculitis and IgA vasculitis nephritis: a single-center retrospective study

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Xueqing Ma, Yonghua He, Panpan Shao, Ling Guo, Wenpei Liang, Jianhua Zhou, Huiqing Yuan, Liru Qiu

Long-term safety of canakinumab in patients with systemic juvenile idiopathic arthritis: 5-year results from the Childhood Arthritis and Rheumatology Research Alliance (CARRA) registry

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Colleen Correll, Alis Burciu, Amita Bansal, Anne Dennos, Deepak Narayanswamy, Elodie Aubrun, Laura E. Schanberg, Li Yuhan, Rahel Schneider, Stephen Balevic, Yukiko Kimura, Timothy Beukelman, R. Aamir, A. Adams, C. Aguiar Lapsia, H. Ahmed, S. Akoghlanian, A. AlBijadi, E. Allenspach, G. Amarilyo, M. Amoruso, S. Angeles-Han, S. Ardoin, S. Armendariz, N. Aviran Dagan, I. Balboni, S. Balevic, S. Ballinger, S. Baluta, M. Basiaga, K. Baszis, M. Becker, E. Beil, H. Bell-Brunson, H. Benham, L. Bermudez-Santiago, W. Bernal, T. Bigley, C. Bingham, B. Binstadt, C. Black, B. Blackmon, M. Blakley, J. Bohnsack, A. Boneparth, J. Bridges, E. Brooks, M. Brothers, D. Brown, H. Brunner, L. Buckley, M. Buckley, M. Buckley, H. Bukulmez, D. Bullock, A. Cancino, S. Canna, L. Cannon, S. Canny, V. Cartwright, E. Chalom, M. Chang, Johanna Chang, Joyce Chang, A. Chang-Hoftman, A. Chen, K. Ciaglia, M. Cidon, D. Co, E. Cohen, R. Connor, K. Cook, A. Cooper, J. Cooper, K. Corbin, C. Correll, S. Cranley, R. Cron, M. Curry, A. Dagci, L. Dallas, A. Dalrymple, E. Datyner, T. Davis, D. De Ranieri, J. Dean, C. DeCoste, F. Dedeoglu, M. DeGuzman, N. Delnay, E. L. DeSantis, R. Devine, M. Dhalla, A. Dhanrajani, D. Dissanayake, B. Dizon, J. Drew, K. Driest, Q. Du, E. Duncan, K. Dunnock, D. Durkee, J. Dvergsten, A. Eberhard, K. Ede, B. Edelheit, C. Edens, M. Elder, Y. Elzaki, C. Failing, D. Fair, L. Favier, B. Feldman, J. Fennell, P. Ferguson, I. Ferguson, C. Figueroa, E. Flanagan, L. Fogel, E. Fox, M. Fox, L. Franklin, R. Fuhlbrigge, J. Fuller, T. Futch-West, M. Geiszler, D. Gerstbacher, M. Gilbert, A. C. Gironella, D. Glaser, I. Goh, S. Gorry, N. Goswami, B. Gottlieb, T. Graham, S. Grevich, T. Griffin, A. Grim, A. Grom, M. Guevara, L. Guzman, T. Hahn, O. Halyabar, E. Hammelev, S. Haro, J. Harris, O. Harry, A. Hay, K. Hays, K. Hayward, L. Henderson, M. Henrickson, A. Hersh, L. Hiraki, M. Hiskey, P. Hobday, C. Hoffart, M. J. Holland, M. Hollander, S. Hong, D. Horton, J. Hsu, A. Huber, J. Huggins, J. Hui-Yuen, M. Ibarra, L. Imundo, C. Inman, A. Jackson, K. James, G. Janow, S. Jared, Y. Jiang, L. Johnson, N. Johnson, J. Jones, D. Kafisheh, K. Kaidar, S. Kasinathan, E. Kessler, M. Khanam, B. Kienzle, S. Kim, Y. Kimura, D. Kingsbury, M. Kitcharoensakkul, J. Klauss, K. Klein, M. Klein-Gitelman, A. Knight, L. Kovalick, D. Krajewski, C. Kremer, C. Lacy, T. LaFlam, B. Lang, S. Lapidus, B. Lapin, A. Lasky, E. Lawson, R. Laxer, Patricia Lee, Pui Lee, T. Lee, L. Lentini, M. Lerman, Y. Levinsky, D. Levy, S. Li, S. Lieberman, L. Lim, E. Limenis, C. Lin, N. Ling, G. Lionetti, R. Livny, M. Lo, D. Lovell, S. Lvovich, A. Lytch, A. Machado, J. Madison, M. Mannion, C. Manos, B. Marston, K. Marzan, T. Mason, S. Matossian, L. McAllister, K. McBrearty, D. McCurdy, K. McDaniels, J. McDonald, L. McIntosh, Z. Mian, P. Miettunen, D. Milojevic, R. Mitacek, R. Modica, S. Mohan, T. Moore, K. Moore, L. Moorthy, E. Morgan, A. Moyer, B. Murante, A. Murphy, E. T. Murray, E. Muscal, O. Mwizerwa, A. Najafi, L. Nassi, S. Nativ, M. Natter, J. Neely, A. Nguyen, P. Nigrovic, J. Nocton, B. Nolan, A. Nowakowski, R. Oakes, E. Oberle, E. Ogbu, M. Oliver, K. Onel, A. Orandi, J. Padam, N. Pan, J. Pandya, S. Panupattanapong, A. Pappo Toledano, J. Patel, P. Patel, A. Patrick, S. Paul, J. Perfetto, C. Pinotti, L. Ponder, R. Pooni, S. Prahalad, M. Quinlan-Waters, J. Rafko, H. Rahimi, R. Randell, L. Ray, Ann Reed, Annelle Reed, H. Reid, I. Reyhan, B. Richard, M. Riebschleger, E. Rife, M. Riskalla, A. Robinson, L. Robinson, L. Rodgers, M. Rodriquez, D. Rogers, T. Ronis, A. Rosado, M. Rosenkranz, N. Rosenwasser, H. Rothermel, D. Rothman, K. Rouster-Stevens, T. Rubinstein, N. Ruth, S. Sabbagh, R. Sadun, L. Santiago, V. Saper, A. Sarkissian, L. Scalzi, J. Schahn, K. Schikler, A. Schlefman, H. Schmeling, E. Schmitt, G. Schulert, C. Schutt, C. Seper, R. Sheets, A. Shehab, S. Shenoi, M. Sherman, J. Shirley, M. Shishov, N. Singer, V. Sivaraman, E. Sloan, J. Smith, E. Smitherman, J. Soep, M. B. Son, C. Spencer, L. Spiegel, H. Srinivasalu, H. Stapp, A. Stephens, Y. Sterba Rakovchik, S. Stern, B. Stevens, R. Stevenson, M. Stoll, E. Stringer, S. Sule, J. Sullivan, M. Sutter, C. Swaffar, G. Syverson, A. M. Szymanski, S. Taber, R. Tal, A. Tambralli, A. Taneja, T. Tanner, S. Tarvin, A. Taxter, M. Tesher, A. Theisen, G. Thieroff, B. Thomas, L. Thomas, N. Thomas, L. Timmerman, T. Ting, C. Todd, D. Toib, K. Torok, H. Tory, M. Toth, E. Treemarcki, T. Tse, S. Tse, C. Tsin, J. Twachtman-Bassett, M. Twilt, T. Valcarcel, R. Valdovinos, A. Vallee, H. Van Mater, C. Varghese, N. Vasquez, P. Vega-Fernandez, J. Verbsky, R. Verstegen, E. von Scheven, S. Vora, L. Wagner-Weiner, D. Wahezi, S. Wakefield, B. Walker, S. Wallgren, H. Walters, M. Waterfield, P. Weiser, P. Weiss, J. Weiss, E. Wershba, K. Widrick, C. Williams, S. Wong, S. Wooldridge, L. Woolnough, T. Wright, E. Wu, A. Yalcindag, R. Yeung, A. Zeft, Y. J. Zhang, Y. D. Zhao, Z. Zheng, A. Zhu, C. Zic

Clinical profile and long-term outcomes of pediatric-onset Takayasu’s arteritis: data from a mexican national referral center

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Dilcia Paola Pagoaga-Vásquez, Gabriela Melendez-Ramírez, Emilia Josefina Patiño-Bahena, Alfonso Buendia-Hernández, Edgar Samuel Ramírez-Marroquín, Juan Eberto Calderon-Colmenero, Solange Gabriela Koretzky, Guering Eid-Lit, María Elena Soto

C-reactive protein to high density lipoprotein cholesterol ratio for predicting coronary artery lesions, and intravenous immunoglobulin resistance in Kawasaki disease

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Ling Li, Xue Xu, Yiming Guo, Yuhan Yan, Meng Li, Haizhao Zhao, Minmin Wang, Qingyu Kong, Cuifen Zhao

Incidence and risk factors of herpes zoster infection in pediatric systemic lupus erythematosus

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Adrienne Katrin M. Guiang-Valerio, Ma. Theresa M. Collante, Christine B. Bernal

Discordant phenotype caused by TREX1 variant in siblings with Aicardi-Goutières syndrome

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Rou Liu, Stefanie Kretschmer, Paulina Switala, Mohamed Attia, Min Ae Lee-Kirsch, Christine Wolf

Cervical spine arthritis as initial manifestation in Juvenile Idiopathic Arthritis: a multicenter retrospective study

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Estefania Quesada-Masachs, Jaime de Inocencio, Juan Carlos Nieto González, Indalecio Monteagudo Sáez, Sara Murias Loza, Marta Medrano San Ildefonso, Joan Calzada Hernández, Inmaculada Calvo Penadés, Rocío Galindo Zabala, Mireia Lopez Corbeto, Jordi Antón

Reproductive health knowledge and preferences in adolescent rheumatology patients: a convergent mixed methods study

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Acela C. Rosado, Josheili Llavona-Ortiz, Lisabeth V. Scalzi, Cynthia H. Chuang, Timothy Hahn, Catherine A. Bingham, Cuoghi Edens, Darilyn Rivera-Collazo, Kimberly Hays

Machine learning for screening and predicting the risk of developing uveitis in juvenile idiopathic arthritis

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Li Li, Junmei Zhang, Jianghong Deng, Weiying Kuang, Xiaohua Tan, Chao Li, Shipeng Li, Caifeng Li

Heart rate variability (HRV) in juvenile fibromyalgia: a preliminary study

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Federico Diomeda, Brigitte Dell’Anna, Rossella Greco, Giulia Loiacono, Roberta Zupo, Fabio Castellana, Adele Civino

Juvenile dermatomyositis: new insights into pathogenesis and clinical applications

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Pauline PL Chan Ng, Aris E. Syntakas, Lucy R. Wedderburn

Mental health screening in pediatric rheumatology: a feasibility study

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Sarah James, Laura Lolacher, Karen Hodge, Janine Slavec, Anna Draper, Nick McPhate, Kristin Houghton, Jaime Guzman, Lori Tucker

Predictors of relapse after withdrawing biotherapies in children with inactive juvenile idiopathic arthritis: a retrospective cohort study of the JIR cohort

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Vincent Jallot, Isabelle Koné-Paut, Sébastien Cavelot, Caroline Galeotti, Linda Rossi-Semerano, Véronique Hentgen, Perrine Dusser

Analysis of genes involved in immune response in children with HLH – case series

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Ewelina Gowin, Witold Szaflarski, Danuta Januszkiewicz-Lewandowska

Comparison of clinical practices during the transitional and young adult phases between patients with oligoarticular/polyarticular juvenile idiopathic arthritis and those with rheumatoid arthritis in Japan

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Sho Mori, Kosuke Shabana, Toshihiro Matsui, Tomo Nozawa, Yuko Sugita, Minako Tomiita, Yasuo Nakagishi, Yuichi Yamasaki, Hiroaki Umebayashi, Masato Yashiro, Naomi Iwata, Junko Yasumura, Hiroyuki Wakiguchi, Takeshi Yamamoto, Shunichiro Takezaki, Yuka Okura, Tadafumi Yokoyama, Masaki Shimizu, Masahiro Hirayama, Shigeto Tohma, Nami Okamoto, Masaaki Mori

Neutrophil lymphocyte ratio as a marker of skin disease activity in older children with juvenile dermatomyositis

  • Open Access
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Shreya Swaminathan, Nidhi Naik, Susan Shenoi, Sarah Vandenbergen, Jessica L. Turnier, Zilan Zheng, Jessica Neely, James S. Andrews, Christian Lood

Association of Mediterranean diet adherence with familial Mediterranean fever severity in a Lebanese cohort

  • Open Access
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Razane Hammoud, Remie El Helou, Dalal Sabbagh, Nour Fakih, Zeinab Safieddine, Layal Malli, Jana Jabbour, José-Noel Ibrahim

Anakinra for infants under six months with Kawasaki disease and coronary artery lesions: a multicenter case series and literature review

  • Open Access
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Giulia Inguscio, Stefano Romano, Marianna Fabi, Livia Gargiullo, Alessandra Marchesi, Maria Cristina Maggio, Maria Vincenza Mastrolia, Giovanni Battista Calabri, Gabriele Simonini, Teresa Giani

Novel risk scoring system for predicting intravenous immunoglobulin resistance and coronary artery aneurysm in Thai children with Kawasaki disease

  • Open Access
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Poomrapee Tantikittipisut, Ankavipar Saprungruang, Roongroj Manatpreeprem, Parichat Khaosut

Adoption of new treatment options in non-systemic juvenile idiopathic arthritis (JIA) in clinical practice

  • Open Access
  • Research

Hedda C. Lamers, Erika Van Nieuwenhove, Sebastiaan J. Vastert, Marc H. A. Jansen, Annet van Royen-Kerkhof, Joost F. Swart, Sytze de Roock

Symptom course of PFAPA syndrome

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Mathilde Labouret, Inès Elhani, Sébastien Cavelot, Glory Dingulu, Maurine Jouret, Ai Tien Nguyen, Adrien Subervie, Anne-Sophie Tavernier, Caroline Vinit, Véronique Hentgen

Clinical outcomes of giant coronary aneurysms in South Asian children with Kawasaki disease

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  • Research

Kumar Abhinav, Nisanth Selvam, Raman Krishna Kumar, Aishee Bhattacharya, Manu Pradeep, Suma Balan

Evaluation of the real-world safety of Canakinumab in the treatment of systemic juvenile idiopathic arthritis in children aged 0–16: a comprehensive analysis based on FAERS data

  • Open Access
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Peng Xiao, Bingqi Wei, Guilong Zhang, Xinyue Zhang, Hejia Wan, Yifan Qi, Liu Chen, Yong Huang, Jianjia Liu

Presence and reactivities of antibodies directed to citrullinated peptides in a Swedish JIA cohort

  • Open Access
  • Research

Raya Saleh, Erik Sundberg, Monika Hansson, Linda Mathsson-Alm, Karl Skriner, Guy Serre, Karin Lundberg, Leonid Padyukov, Helena Erlandsson Harris

A comprehensive report of disease complications of juvenile idiopathic arthritis using a prospective cohort study

  • Open Access
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Jacob Anderson, Kaleo Ede, Nikita Goswami, Michael Shishov, Geoffrey Thiele, Vinay Vaidya, Elisa Wershba

Vaccination coverage, immune responses, and clinical characteristics in children with PFAPA syndrome: a monocentric prospective study

  • Open Access
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Emilie Sallansonnet, Renato Gualtieri, Henri Margot, Manel Mejbri, Klara Posfay-Barbe, Geraldine Blanchard-Rohner

Kompaktes Leitlinien-Wissen Pädiatrie (Link öffnet in neuem Fenster)

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Neu im Fachgebiet Pädiatrie

Atopische Dermatitis als erhebliche seelische Belastung

Bei Kindern und Jugendlichen, die an atopischer Dermatitis leiden, ist auch das Risiko für viele psychische Erkrankungen erhöht. Dafür sprechen Ergebnisse einer großen Kohortenstudie auf Basis von US-Patientenakten.     

Elektroschrott: Wie Praxen Altgeräte sicher entsorgen

Ob nun Sonogerät, Praxiscomputer oder gar TI-Konnektor: Einfach zum nächsten Wertstoffhof sollten Praxisteams ausgediente Elektrogeräte nicht bringen. Was bei der Entsorgung zu beachten ist. Und wie die Teams sicher sensible Daten auf PC-Festplatte, externem Datenspeicher und TI-Komponenten löschen.

Tipps: So können Praxen die Risiken für einen GOÄ-Streit minimieren

Für Streitigkeiten, die das GOÄ-Honorar betreffen, sind neuerdings nur noch Landgerichte zuständig. Das macht Prozesse teurer. Eine Praxisberaterin erläutert, wie Praxen vorbauen können, um solche Streitfälle und Gerichtsverfahren zu vermeiden.

Assistierte Geburt oder Kaiserschnitt – was ist für die Gehirnentwicklung sicherer?

Ob vaginal-operative Geburt oder Kaiserschnitt in der Austreibungsphase: Das neurologische Outcome der Kinder scheint laut aktuellen Daten vergleichbar zu sein. Für Vakuumentbindungen und Geburten mit mehrfachem Instrumenteneinsatz gilt das jedoch nur mit Einschränkung.

Update Pädiatrie

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