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Pediatric Cardiology

Erschienen in:

01.08.2015 | Review Article

Perioperative Care of Children with Eisenmenger Syndrome Undergoing Non-cardiac Surgery

verfasst von: Bibhuti B. Das

Erschienen in: Pediatric Cardiology | Ausgabe 6/2015

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Abstract

The Eisenmenger syndrome (ES) is a severe form of pulmonary arterial hypertension and arises in congenital heart disease with a systemic-to-pulmonary shunt. Patients with ES have multisystem involvement as a result of chronic hypoxemia with hematologic, skeletal, renal, and neurologic systems, causing significant morbidity and mortality. In contrast to pulmonary arterial hypertension, survival prospects are far superior in patients with ES and a growing number of ES patients are surviving into adulthood. As a result, many face the prospect of incidental surgery. To date, there is no guideline for the perioperative care of ES patients in children and limited data available for adult patients. This review provides an overview of appropriate measures for the safe perioperative care of patients, based on an understanding of the pathophysiological changes that occur in ES.

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Titel: Perioperative Care of Children with Eisenmenger Syndrome Undergoing Non-cardiac Surgery
verfasst von: Bibhuti B. Das
Publikationsdatum: 01.08.2015
Verlag: Springer US
Erschienen in: Pediatric Cardiology / Ausgabe 6/2015
Print ISSN: 0172-0643
Elektronische ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-015-1184-7

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