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Erschienen in: Pediatric Surgery International 7/2016

11.03.2016 | Case Report

Presentation and management of pulmonary sequestration with total visceral inflow and outflow

verfasst von: Christopher L. Sudduth, Sarah J. Hill, Mehul V. Raval

Erschienen in: Pediatric Surgery International | Ausgabe 7/2016

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Abstract

Two of the most common types of congenital thoracic malformations are congenital pulmonary airway malformations (CPAMs) and bronchopulmonary sequestrations (BPS). Here we present the first known case of a hybrid lesion, with coexisting features of an extralobar sequestration (ELS) and CPAM type 2, with arterial inflow from the celiac trunk and venous outflow to the portal vein. The clinical presentation, investigative imaging and timing of surgery are discussed.
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Metadaten
Titel
Presentation and management of pulmonary sequestration with total visceral inflow and outflow
verfasst von
Christopher L. Sudduth
Sarah J. Hill
Mehul V. Raval
Publikationsdatum
11.03.2016
Verlag
Springer Berlin Heidelberg
Erschienen in
Pediatric Surgery International / Ausgabe 7/2016
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-016-3882-5

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