Autoinflammatory diseases
B1 Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome (PFAPA) in a 17 years old girl – case report
Erato Atsali1, Dimitra Kassara2, Pelagia Katsimbri2, Sorina Boiu1, Dimitrios T. Boumpas2, Vana Papaevangelou1
1Pediatric Rheumatology Unit,3RD Department of Pediatrics, National and Kapodestrian University of Athens, Medical School, Athens, Greece; 2Joint Rheumatology Program,4TH Department of Medicine, National and Kapodestrian University of Athens, Medical School, Athens, Greece
Correspondence: Erato Atsali
Disease outcome
B2 Case of paraneoplastic arthritis in child
Olena A. Oshlyanska, Ludmila I. Omelchenko, Tatiana A. Ljudvik
Department of connective tissue disorders in children, State Institute of Pediatrics, Obstetrics and Gynecology, Academy of Medical Sciences of Ukraine, Kyiv, Ukraine
Correspondence: Olena A. Oshlyanska
Juvenile idiopathic arthritis (oligo, poly, psoriatic)
B3 A patient with three diagnoses? juvenile idiopathic arthritis, chronic recurrent multifocal osteomyelitis and atypical subacute Moraxella osloensis infection
Katerina Bouchalova1,2,3, Marcel Schüller1, Jana Franova1, Jarmila Skotakova4, Marie Macku1
1Pediatric Rheumatology Unit, Pediatric Department, University Hospital Brno, Brno, Czech Republic; 2Department of Pediatrics, Palacky University, Olomouc, Olomouc, Czech Republic; 3Institute of Molecular and Translational Medicine, Palacky University, Olomouc, Olomouc, Czech Republic; 4Pediatric Radiology Department, University Hospital Brno, Brno, Czech Republic
Correspondence: Katerina Bouchalova
B4 Foot and ankle pathologies in juvenile idiopathic arthritis: a narrative review
Antoni Fellas1, Fiona Hawke1, Derek Santos2, Andrea Coda1
1School of Health Sciences, Faculty of Health and Medicine, University of Newcastle, Newcastle, Australia; 2School of Health Sciences, Queen Margaret University, Edinburgh, United Kingdom
Correspondence: Antoni Fellas
B5 Characterization of TCELLS in PBMCS of JIA patients in pre and post medication phase of treatment
Anthi Kelempisioti1, Paula Keskitalo2, Virpi Glumoff1, Petri Kulmala1,2, Paula Vahasalo2
1Medical Immunology and Microbiology, University of Oulu, Oulu, Finland; 2Pediatrics, University of Oulu, Oulu, Finland
Correspondence: Anthi Kelempisioti
B6 A 10-year Saudi experience of using adalimumab in treating Juvenile Idiopathic Arthritis
Mohammed A. Mozaffar, Asraa K. Turkistani, Samaa O. Sangoof
Pediatric, King Abdulaziz University Hospital, Facult of Medicine, Jeddah, Saudi Arabia
Correspondence: Mohammed A. Mozaffar
B7 Gene-engineering biological therapy in children with juvenile idiopathic arthritis in Moscow
Vladislav Sevostyanov1, Elena Zholobova2
1Municipal Children’s Polyclinic № 122, Moscow, Russian Federation; 2I.M. Sechenov First Moscow State Medical University, Moscow, Russian Federation
Correspondence: Vladislav Sevostyanov
Juvenile dermatomyositis
B8 Whole-Body Magnetic Resonance Imaging (WBMRI) revealing an extensive muscle involvement in a child presenting with Gottron’s papules and moderate muscle weakness– case report
Evangelia Bountouvi1, konstantinos Theodoropoulos2, Erato Atsali1, Renata Moutsiou1, Christina Tsalapaki3, Pelagia Katsimbri4, Sorina Boiu1, Dimitrios T. Boumpas4, Vana Papaevangelou1
1Pediatric Rheumatology Unit,3RD Department of Pediatrics, National and Kapodistrian University of Athens, Medical School, Athens, Greece; 22nd Department of Dermatology and Venereology, National and Kapodistrian University of Athens, Medical School, Athens, Greece; 3Clinical Immunology-Rheumatology Unit, 2nd Department of Medicine and Laboratory, National and Kapodistrian University of Athens, Medical School, Athens, Greece; 4Joint Rheumatology Program,4TH Department of Medicine, National and Kapodistrian University of Athens, Medical School, Athens, Greece
Correspondence: Evangelia Bountouvi
Macrophage activation syndrome
B9 “Clinical presentation of macrophage activation syndrome in Mexican children with rheumatic diseases”
Talia Diaz, Sofia Osorio, Maria Teresa Braña, Yuridiana Ramirez, Luis Aparicio, Andres Rodriguez, Enrique Faugier, Rocio Maldonado
Pediatric Rheumatology, Hospital Infantil de Mexico Federico Gomez, Ciudad de Mexico, Mexico
Correspondence: Talia Diaz
Miscellaneous rheumatic diseases
B10 Erythema nodosum as symptom of systemic diseases
Maria Francesca Gicchino, Carmela Granato, Giulia Macchini, Daniela Capalbo, Alma Nunzia Olivieri
Department of Women, Child and General and Specialistic Surgery, Università della Campania Luigi Vanvitelli, Naples, Italy
Correspondence: Maria Francesca Gicchino
B11 Observations from clinical practice
Nathan Hasson
Paediatric Rheumatology, The Portland Hospital, London, United Kingdom
B12 First pediatric patient with neuromyelitis optica and Sjogren’s syndrome successfully treated with tocilizumab
Achille Marino1, Sona Narula2, Melissa Lerman3
1Rheumatology, Meyer Children’s Hospital, Florence, Italy; 2Neurology, The Children’s Hospital of Philadelphia, Philadelphia, PA, United States; 3Rheumatology, The Children’s Hospital of Philadelphia, Philadelphia, PA, United States
Correspondence: Achille Marino
B13 Pediatric mixed connective tissue disease: variability of clinical characteristics at disease onset in two patients
Maria Amelia Muñoz Calonge, Sara Maria Murias Loza, Rosa Maria Alcobendas, Agustin Remesal
Pediatric Rheumatology, Pediatrician, Madrid, Spain
Correspondence: Maria Amelia Muñoz Calonge
Symptoms at disease onset | Laboratory examinations | Capillaroscopy | Anti-RNP antibodies | Diagnosis | |
---|---|---|---|---|---|
Case 1 | Arthritis Arthralgia | ANA 1/2560 ESR 54 mm/h CRP 80.55 mg/dL RF 49.9 UI/mL Lymphopenia | Compatible with MCTD | Positive | MCTD |
Case 2 | Raynaud’s Disease | ANA 1/2560 Positive Anti-Ro antibodies C4 9 mg/dl ESR 28 mm/h Lymphopenia | Sclerodermiform-like | Positive | MCTD |
B14 Complex regional pain syndrome type I: therapeutic management and progosis factors
Esmeralda Núñez-Cuadros1, Rocio Galindo Zavala1, Gisela Díaz-Cordovés Rego1, Cristina Antúnez Fernández2, Yaiza García Molina2, Antonio L. Urda Cardona2
1Paediatric Rheumatology, Universitary Regional Malaga Hospital, MALAGA, Spain; 2Paediatrics, Universitary Regional Malaga Hospital, MALAGA, Spain
Correspondence: Esmeralda Núñez-Cuadros
B15 A rare cause of joint pain: synovial haemangioma
Nihal Sahin1, Habibe S. Durmus2, Ayse S. Pinarbasi3, Zubeyde Gunduz1, Muammer H. Poyrazoglu1, Zehra F. Karaman4, Turhan Oktem5, Mithat Oner6, Ruhan Dusunsel1
1Pediatric Rheumatology, Erciyes University Faculty of Medicine, Kayseri, Turkey; 2Pediatrics, Erciyes University Faculty of Medicine, Kayseri, Turkey; 3Pediatric Nephrology, Erciyes University Faculty of Medicine, Kayseri, Turkey; 4Radiology, Erciyes University Faculty of Medicine, Kayseri, Turkey; 5Pathology, Erciyes University Faculty of Medicine, Kayseri, Turkey; 6Ortopedics, Erciyes University Faculty of Medicine, Kayseri, Turkey
Correspondence: Nihal Sahin
B16 Bowel bypass syndrome after postnatal jejunoileal anastomosis
Gordana Susic1, Tamara Krstajic2, Dragana Vujovic2, Nedeljko Radlovic2,3, Zoran Lekovic2,3, Dusica Novakovic1, Gordana Milosevski Lomic2
1Institute of Rheumatology, Belgrade, Serbia; 2University Children’s hospital, Belgrade, Serbia; 3School of Medicine, University of Belgrade, Belgrade, Serbia
Correspondence: Gordana Susic
Psycho-social aspects and rehabilitation
B17 Nurse’s experiences of distraction during procedures in pediatric care
Karina Mördrup1, Gunilla Hesselstrand2
1Pediatric Rheumatology Unit, Karolinska University Hospital, Stockholm, Sweden; 2Pediatric Orthopedic Unit, Karolinska University Hospital, Stockholm, Sweden
Correspondence: Karina Mördrup
Spondyloarthritis (SpA) and enthesitis related arthritis (ERA)
B18 Simultaneous presentation of musculoskeletal and gastrointestinal symptoms in HLA-B27 positive and anti-TTG negative patient with typical celiac disease histology
Iva Sorić1, Lovro Lamot1,2, Mandica Vidovic1, Mirta Lamot1, Miroslav Harjacek1,2
1Clinical Hospital Center Sestre Milosrdnice, Zagreb, Croatia; 2Univeristy of Zagreb School of Medicine, Zagreb, Croatia
Correspondence: Iva Sorić
Systemic juvenile idiopathic arthritis (JIA)
B19 Reaching the limits despite extended immunomodulatory therapy in a patient with systemic JIA; a case report
Eva Adank, Elvira Cannizzaro Schneider
Department of Paediatric Rheumatology, Kinderspital Zürich, Zürich, Switzerland
Correspondence: Eva Adank
Systemic lupus erythematosus and antiphospholipid syndrome
B20 Growth in children with Juvenile Systemic Lupus erythematosus in the Sultanate of Oman
Eiman Abdalla1, Irfan Ullah1, L Jeyaseelan2, Reem Abdwani1
1Child health, Sultan Qaboos University Hospital, Muscat, Oman; 2Biostatistics, Sultan Qaboos University Hospital, Muscat, Oman
Correspondence: Eiman Abdalla
B21 Maternal and neonatal outcome of SLE pregnancies in Sultan Qaboos University Hospital
Reem Abdwani1, Laila AL Shaqsi2, Ibrahim Al Zakwani1
1Child Health, Sultan Qaboos University, Muscat, Oman; 2Child Health, Oman Medical Speciality Board, Muscat, Oman
Correspondence: Reem Abdwani
Characteristic,
n (%) unless specified otherwise
| All (N = 147) | Non-SLE (n = 91) | SLE (n = 56) |
P-value |
---|---|---|---|---|
Age, mean ± SD, years | 30 ± 5 | 29 ± 5 | 31 ± 5 | 0.145 |
Primigravida (1) | 35 (24%) | 24 (26%) | 11 (20%) | |
Multigravida (2–4) | 79 (54%) | 52 (57%) | 27 (48%) | 0.084 |
Grand multigravida (>5) | 33 (24%) | 15 (16%) | 18 (32%) | |
Abortions | 38 (26%) | 14 (15%) | 24 (43%) | <0.001 |
Gestational diabetes | 24 (17%) | 9 (10%) | 15 (28%) | 0.004 |
Polyhydramnios | 4 (2.7%) | 0 | 4 (7.1%) | 0.020 |
Pre-term labour | 13 (8.8%) | 1 (1.1%) | 12 (21%) | <0.001 |
IUGR | 12 (8.2%) | 0 | 12 (21%) | <0.001 |