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CardioVascular and Interventional Radiology

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19.04.2018 | Case Report

Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation)

verfasst von: Thomas Kroencke, Marcus Murnauer, Frank Alexander Jordan, Vera Blodow, Hannes Ruhnke, Tina Schaller, Bruno Märkl

Erschienen in: CardioVascular and Interventional Radiology | Ausgabe 8/2018

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Abstract

In a 50-year-old male with an incidentally discovered hepatocellular carcinoma, a congenital extrahepatic portosystemic shunt with the absence of the portal vein (Abernethy syndrome) was diagnosed by imaging. This study aims to discuss the variant anatomy relevant to this splanchnic vascular malformation, review its association with the development of liver neoplasms, and report the safety and efficacy of TARE followed by resection for a HCC arising in this rare condition.

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Titel: Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation)
verfasst von: Thomas Kroencke
Marcus Murnauer
Frank Alexander Jordan
Vera Blodow
Hannes Ruhnke
Tina Schaller
Bruno Märkl
Publikationsdatum: 19.04.2018
Verlag: Springer US
Erschienen in: CardioVascular and Interventional Radiology / Ausgabe 8/2018
Print ISSN: 0174-1551
Elektronische ISSN: 1432-086X
DOI: https://doi.org/10.1007/s00270-018-1965-5

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Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation)

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