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European Journal of Pediatrics

Erschienen in:

01.10.2010 | Short Report

Scimitar Syndrome associated with partial anomalous pulmonary venous draining into superior vena cava

verfasst von: Esen Demir, Memnune Aşkın, Levent Midyat, Figen Gülen, Zülal Ülger, Remziye Tanaç, Selen Bayraktaroğlu

Erschienen in: European Journal of Pediatrics | Ausgabe 10/2010

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Abstract

Scimitar syndrome is a rare congenital cardiopulmonary malformation characterized by hypoplasia of the right lung and drainage of the right pulmonary veins into the vena cava inferior. It may also be associated with cardiac dextroversion and anomalies of the tracheobronchial system, cardiovascular system, and diaphragm. Some cases are asymptomatic with others diagnosed in early-childhood period with pulmonary hypoplasia and other associated malformations. We present here a patient whose venous return of the middle and lower lobes of the right lung is into the superior vena cava, which is a very unusual finding for this disorder.

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Titel: Scimitar Syndrome associated with partial anomalous pulmonary venous draining into superior vena cava
verfasst von: Esen Demir
Memnune Aşkın
Levent Midyat
Figen Gülen
Zülal Ülger
Remziye Tanaç
Selen Bayraktaroğlu
Publikationsdatum: 01.10.2010
Verlag: Springer-Verlag
Erschienen in: European Journal of Pediatrics / Ausgabe 10/2010
Print ISSN: 0340-6199
Elektronische ISSN: 1432-1076
DOI: https://doi.org/10.1007/s00431-010-1153-3

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